(Q40466156)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15669681%20AND%20SRC:MED&resulttype=core&format=json

7 January 2020

title

Correlation between enzyme activity and substrate storage in a cell culture model system for Gaucher disease (English)

1 reference

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7 January 2020

1 reference

3

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7 January 2020

author name string

U H Schueler

1

1 reference

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7 January 2020

T Kolter

2

1 reference

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7 January 2020

G C Zirzow

4

1 reference

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7 January 2020

K Sandhoff

5

1 reference

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7 January 2020

R O Brady

6

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7 January 2020

publication date

1 January 2004

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15669681%20AND%20SRC:MED&resulttype=core&format=json

Journal of Inherited Metabolic Disease

7 January 2020

published in

1 reference

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7 January 2020

volume

27

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7 January 2020

issue

5

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7 January 2020

page(s)

649-658

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https://scigraph.springernature.com/pub.10.1023/b:boli.0000042959.44318.7c

7 January 2020

exact match

0 references

cites work

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Altered ganglioside biosynthesis in mouse cell cultures following transformation with chemical carcinogens and x-irradiation

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Macrophages exposed in vitro to conduritol B epoxide resemble Gaucher cells

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METABOLISM OF GLUCOCEREBROSIDES. II. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN GAUCHER'S DISEASE.

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Chemical chaperones increase the cellular activity of N370S beta -glucosidase: a therapeutic strategy for Gaucher disease

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12 December 2020

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12 December 2020

beta-Glucosidase inhibition in murine peritoneal macrophages by conduritol-B-epoxide: an in vitro model of the Gaucher cell

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Sphingolipids—Their Metabolic Pathways and the Pathobiochemistry of Neurodegenerative Diseases

1 reference

Crossref

https://api.crossref.org/works/10.1023%2FB%3ABOLI.0000042959.44318.7C

7 January 2021