(Q42993799)

12 November 2017

N-terminal domains of fibrillin 1 and fibrillin 2 direct the formation of homodimers: a possible first step in microfibril assembly (English)

1 reference

12 November 2017

T M Trask

1

1 reference

12 November 2017

T M Ritty

2

1 reference

12 November 2017

T Broekelmann

3

1 reference

12 November 2017

C Tisdale

4

1 reference

12 November 2017

R P Mecham

5

1 reference

12 November 2017

language of work or name

English

0 references

publication date

1 June 1999

1 reference

12 November 2017

9

1 reference

inferred from page(s)

published in

Biochemical Journal

1 reference

12 November 2017

340 ( Pt 3)

1 reference

12 November 2017

693-701

1 reference

Processing of the fibrillin-1 carboxyl-terminal domain.

12 November 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Identification and characterization of a new latent transforming growth factor-beta-binding protein, LTBP-4

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Morphology and biomechanics of the microfibrillar network of sea cucumber dermis

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Microfibrils provide non-linear elastic behaviour in the abdominal artery of the lobster Homarus americanus

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Solution structure of a pair of calcium-binding epidermal growth factor-like domains: implications for the Marfan syndrome and other genetic disorders

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Fibrillin-1: organization in microfibrils and structural properties

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Genomic organization of the sequence coding for fibrillin, the defective gene product in Marfan syndrome.

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Structure and expression of fibrillin-2, a novel microfibrillar component preferentially located in elastic matrices

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Developmental expression of fibrillin genes suggests heterogeneity of extracellular microfibrils

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

A mutation in FBN1 disrupts profibrillin processing and results in isolated skeletal features of the Marfan syndrome

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Fibrillin binds calcium and is coded by cDNAs that reveal a multidomain structure and alternatively spliced exons at the 5' end

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Elastin-Associated Microfibrils and Microfibrillar Proteins

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

The elastic fiber. I. The separation and partial characterization of its macromolecular components

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Fibrillin, a new 350-kD glycoprotein, is a component of extracellular microfibrils

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

TGF-beta 1 binding protein: a component of the large latent complex of TGF-beta 1 with multiple repeat sequences

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

An analysis by rotary shadowing of the structure of the mammalian vitreous humor and zonular apparatus

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Purification and partial characterization of fibrillin, a cysteine-rich structural component of connective tissue microfibrils

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Linkage of Marfan syndrome and a phenotypically related disorder to two different fibrillin genes

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Rotary shadowing of elastic system microfibrils in the ocular zonule, vitreous, and ligamentum nuchae

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Genetic linkage of the Marfan syndrome, ectopia lentis, and congenital contractural arachnodactyly to the fibrillin genes on chromosomes 15 and 5. The International Marfan Syndrome Collaborative Study

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Marfan syndrome caused by a recurrent de novo missense mutation in the fibrillin gene

26 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Vitreous humor of chicken contains two fibrillar systems: an analysis of their structure.

27 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1220300

Fibrillin: monomers and microfibrils

16 August 2018

1 reference

12 December 2020

The CTAB-DNA precipitation method: a common mini-scale preparation of template DNA from phagemids, phages or plasmids suitable for sequencing

1 reference

12 December 2020

Alignment of fibrillin molecules in elastic microfibrils is defined by transglutaminase-derived cross-links

1 reference

12 December 2020

Synthesis and assembly of fibrillin by fibroblasts and smooth muscle cells

1 reference

12 December 2020

Tenascin-C hexabrachion assembly is a sequential two-step process initiated by coiled-coil alpha-helices

1 reference

12 December 2020

The morphogenesis of elastic fibers

1 reference

12 December 2020

Recombinant pulmonary surfactant protein D. Post-translational modification and molecular assembly

1 reference

12 December 2020

Fibrillin immunoreactivity is associated with normal or fragmented elastic microfibrils at the dermal-epidermal junction in recessive dystrophic epidermolysis bullosa

1 reference

12 December 2020

10.1042/0264-6021:3400693

Identifiers

DOI

1 reference

12 November 2017

1 reference

12 November 2017

1 reference