(Q24644303)

2

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Peter D J Grootenhuis

3

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Bill Burton

4

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Dong Cao

5

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Tim Neuberger

6

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Amanda Turnbull

7

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Ashvani Singh

8

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John Joubran

9

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Anna Hazlewood

10

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Jinglan Zhou

11

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Jason McCartney

12

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Vijayalaksmi Arumugam

13

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Caroline Decker

14

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Jennifer Yang

15

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Chris Young

16

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Eric R Olson

17

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Jeffery J Wine

18

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Raymond A Frizzell

19

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Melissa Ashlock

20

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Paul Negulescu

Proceedings of the National Academy of Sciences of the United States of America

21

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language of work or name

English

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publication date

3 November 2009

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published in

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volume

106

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page(s)

18825-30

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issue

44

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cites work

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ATPase activity of the cystic fibrosis transmembrane conductance regulator

7 April 2017

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7 April 2017

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27 September 2017

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Regulation of normal and cystic fibrosis airway surface liquid volume by phasic shear stress

27 September 2017

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Rescue of DeltaF508-CFTR trafficking and gating in human cystic fibrosis airway primary cultures by small molecules

27 September 2017

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27 September 2017

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27 September 2017

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Activation of VPAC1 receptors by VIP and PACAP-27 in human bronchial epithelial cells induces CFTR-dependent chloride secretion

27 September 2017

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Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis

27 September 2017

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All-digital image capture and whole-field analysis of ciliary beat frequency

27 September 2017

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Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study

27 September 2017

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ENaC-CFTR interactions: the role of electrical coupling of ion fluxes explored in an epithelial cell model

27 September 2017

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Thiazolidinone CFTR inhibitor identified by high-throughput screening blocks cholera toxin-induced intestinal fluid secretion.

27 September 2017

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Cystic fibrosis gene mutations and pancreatitis risk: relation to epithelial ion transport and trypsin inhibitor gene mutations

27 September 2017

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Constitutive release of ATP and evidence for major contribution of ecto-nucleotide pyrophosphatase and nucleoside diphosphokinase to extracellular nucleotide concentrations

27 September 2017

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The first-nucleotide binding domain of the cystic-fibrosis transmembrane conductance regulator is important for inhibition of the epithelial Na+ channel.

27 September 2017

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Polyvariant mutant cystic fibrosis transmembrane conductance regulator genes. The polymorphic (Tg)m locus explains the partial penetrance of the T5 polymorphism as a disease mutation

27 September 2017

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Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis

27 September 2017

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In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis

27 September 2017

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Bicarbonate conductance and pH regulatory capability of cystic fibrosis transmembrane conductance regulator

27 September 2017

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Relative ion permeability of normal and cystic fibrosis nasal epithelium

27 September 2017

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Chloride impermeability in cystic fibrosis

27 September 2017

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Identification and regulation of the cystic fibrosis transmembrane conductance regulator-generated chloride channel

27 September 2017

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Defective function of the cystic fibrosis-causing missense mutation G551D is recovered by genistein

27 September 2017

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Cl- transport by cystic fibrosis transmembrane conductance regulator (CFTR) contributes to the inhibition of epithelial Na+ channels (ENaCs) in Xenopus oocytes co-expressing CFTR and ENaC.

30 May 2018

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Extraction of cilium beat parameters by the combined application of photoelectric measurements and computer simulation

30 May 2018

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Ability of adenovirus vectors containing different CFTR transcriptional cassettes to correct ion transport defects in CF cells.

30 May 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Altered fluid transport across airway epithelium in cystic fibrosis

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Mutations in CFTR associated with mild-disease-form Cl- channels with altered pore properties.

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Effect of cytosolic pH on epithelial Na+ channel in normal and cystic fibrosis sweat ducts

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Cystic fibrosis: a disease of vulnerability to airway surface dehydration.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Airway surface liquid volume regulates ENaC by altering the serine protease-protease inhibitor balance: a mechanism for sodium hyperabsorption in cystic fibrosis.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Hyposecretion, not hyperabsorption, is the basic defect of cystic fibrosis airway glands.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Phenylglycine and sulfonamide correctors of defective delta F508 and G551D cystic fibrosis transmembrane conductance regulator chloride-channel gating

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Effects of endothelin-1 on epithelial ion transport in human airways

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2773991

Lung disease associated with the IVS8 5T allele of the CFTR gene

28 November 2018

1 reference

12 December 2020

Increased bioelectric potential difference across respiratory epithelia in cystic fibrosis

1 reference

12 December 2020

Abnormal Ion Permeation Through Cystic Fibrosis Respiratory Epithelium

1 reference

12 December 2020

Correction of cAMP-stimulated fluid secretion in cystic fibrosis airway epithelia: efficiency of adenovirus-mediated gene transfer in vitro

1 reference

12 December 2020

1 reference

12 December 2020

Pulmonary disease severity in men with deltaF508 cystic fibrosis and residual chloride secretion

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.0904709106

1 reference

861018

ADS bibcode

2009PNAS..10618825V

0 references

861018

1 reference

1 reference

1 reference