(Q35209762)

7 August 2017

L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia (English)

1 reference

7 August 2017

C R Roe

1

1 reference

7 August 2017

D S Millington

2

1 reference

7 August 2017

D A Maltby

3

1 reference

7 August 2017

T P Bohan

4

1 reference

7 August 2017

C L Hoppel

5

1 reference

7 August 2017

language of work or name

English

0 references

publication date

1 June 1984

1 reference

Journal of Clinical Investigation

7 August 2017

1 reference

7 August 2017

73

1 reference

7 August 2017

1785-1788

1 reference

7 August 2017

6

1 reference

Relationship between acid-soluble carnitine and coenzyme A pools in vivo

7 August 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437091

Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437091

Carnitine metabolism and deficiency syndromes

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437091

Propionylcarnitine physiological variations in vivo

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437091

Carnitine metabolism in the fasting rat

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437091

Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=437091

Comparison of the carnitine acyltransferase activites from rat liver peroxisomes and microsomes

28 July 2018

1 reference

12 December 2020

Propionate inhibition of succinate:CoA ligase (GDP) and the citric acid cycle in mitochondria

1 reference

12 December 2020

Application of high resolution fast atom bombardment and constant B/E ratio linked scanning to the identification and analysis of acylcarnitines in metabolic disease

1 reference

12 December 2020

Glycine cleavage system in ketotic hyperglycinemia: a reduction of H-protein activity

1 reference

12 December 2020

L-carnitine therapy in propionicacidaemia

1 reference

12 December 2020

Hypocarnitinemia in disorders of organic acid metabolism

1 reference

12 December 2020

C6-C10-dicarboxylic aciduria: investigations of a patient with riboflavin responsive multiple acyl-CoA dehydrogenation defects

1 reference

12 December 2020

The specific inhibition of the pyruvate dehydrogenase complex from pig kidney by propionyl-CoA and isovaleryl-Co-A

1 reference

12 December 2020

Identifiers

DOI

10.1172/JCI111387

1 reference

7 August 2017

1 reference

7 August 2017

1 reference