(Q41734187)

8 October 2017

Dystrophin mutations predict cellular susceptibility to oxidative stress (English)

1 reference

8 October 2017

Disatnik MH

1

1 reference

PubMed ID

10797403

8 October 2017

Chamberlain JS

series ordinal

2

1 reference

PubMed ID

10797403

8 October 2017

Rando TA

series ordinal

3

1 reference

8 October 2017

1 May 2000

1 reference

8 October 2017

1 reference

8 October 2017

23

1 reference

8 October 2017

784-792

1 reference

8 October 2017

5

1 reference

The structural and functional diversity of dystrophin

8 October 2017

1 reference

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Apoptosis and necrosis: two distinct events induced, respectively, by mild and intense insults with N-methyl-D-aspartate or nitric oxide/superoxide in cortical cell cultures

21 January 2018

1 reference

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Nitric oxide synthase complexed with dystrophin and absent from skeletal muscle sarcolemma in Duchenne muscular dystrophy

21 January 2018

1 reference

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X chromosome-linked muscular dystrophy (mdx) in the mouse

21 January 2018

1 reference

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Association of the dystroglycan complex isolated from bovine brain synaptosomes with proteins involved in signal transduction.

21 January 2018

1 reference

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Neuronal nitric oxide synthase and dystrophin-deficient muscular dystrophy

21 January 2018

1 reference

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Selective loss of sarcolemmal nitric oxide synthase in Becker muscular dystrophy

21 January 2018

1 reference

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Overexpression of dystrophin in transgenic mdx mice eliminates dystrophic symptoms without toxicity

21 January 2018

1 reference

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Dp71 can restore the dystrophin-associated glycoprotein complex in muscle but fails to prevent dystrophy.

21 January 2018

1 reference

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Integrin-mediated muscle cell spreading. The role of protein kinase c in outside-in and inside-out signaling and evidence of integrin cross-talk

21 January 2018

1 reference

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Very mild muscular dystrophy associated with the deletion of 46% of dystrophin

21 January 2018

1 reference

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Regulation of antioxidant enzyme gene expression in response to oxidative stress and during differentiation of mouse skeletal muscle

21 January 2018

1 reference

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Gamma-sarcoglycan deficiency leads to muscle membrane defects and apoptosis independent of dystrophin

21 January 2018

1 reference

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Role of free radicals and catalytic metal ions in human disease: an overview

21 January 2018

1 reference

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Mutations in the integrin alpha7 gene cause congenital myopathy

21 January 2018

1 reference

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A PDZ-containing scaffold related to the dystrophin complex at the basolateral membrane of epithelial cells

21 January 2018

1 reference

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alpha1-syntrophin gene disruption results in the absence of neuronal-type nitric-oxide synthase at the sarcolemma but does not induce muscle degeneration

21 January 2018

1 reference

https://api.crossref.org/works/10.1002%2F%28SICI%291097-4598%28200005%2923%3A5%3C784%3A%3AAID-MUS17%3E3.0.CO%3B2-Y

Carbonyl assays for determination of oxidatively modified proteins.

21 January 2018

1 reference

https://api.crossref.org/works/10.1002%2F%28SICI%291097-4598%28200005%2923%3A5%3C784%3A%3AAID-MUS17%3E3.0.CO%3B2-Y

Frame-shift deletions in patients with Duchenne and Becker muscular dystrophy.

21 January 2018

1 reference

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Absence of integrin alpha 7 causes a novel form of muscular dystrophy

21 January 2018

1 reference

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How does dystrophin deficiency lead to muscle degeneration?--evidence from the mdx mouse

21 January 2018

1 reference

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The extracellular matrix as a cell survival factor

21 January 2018

1 reference

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An explanation for the phenotypic differences between patients bearing partial deletions of the DMD locus

21 January 2018

1 reference

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alpha-Dystroglycan is a laminin receptor involved in extracellular matrix assembly on myotubes and muscle cell viability.

21 January 2018

1 reference

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Oxidative stress and muscular dystrophy

21 January 2018

1 reference

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Dystrophin-associated proteins are greatly reduced in skeletal muscle from mdx mice

21 January 2018

1 reference

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Half the dystrophin gene is apparently enough for a mild clinical course: confirmation of its potential use for gene therapy.

21 January 2018

1 reference

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Expression of full-length and truncated dystrophin mini-genes in transgenic mdx mice

21 January 2018

1 reference

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Prevention of dystrophic pathology in mdx mice by a truncated dystrophin isoform.

21 January 2018

1 reference

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Primary mouse myoblast purification, characterization, and transplantation for cell-mediated gene therapy

21 January 2018

1 reference

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Muscular dystrophies and the dystrophin-glycoprotein complex

21 January 2018

1 reference

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Dystrophic muscle in mice chimeric for expression of alpha5 integrin

21 January 2018

1 reference

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Impaired metabolic modulation of alpha-adrenergic vasoconstriction in dystrophin-deficient skeletal muscle

21 January 2018

1 reference

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Ischemia/reperfusion injury in skeletal muscle

21 January 2018

1 reference

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Sparing of mdx extraocular muscles from dystrophic pathology is not attributable to normalized concentration or distribution of neuronal nitric oxide synthase

21 January 2018

1 reference

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Human dystrophin expression corrects the myopathic phenotype in transgenic mdx mice

21 January 2018

1 reference

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Bidirectional signaling between sarcoglycans and the integrin adhesion system in cultured L6 myocytes

21 January 2018

1 reference

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The alpha 5 beta 1 integrin supports survival of cells on fibronectin and up-regulates Bcl-2 expression

21 January 2018

1 reference

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Muscular dystrophy in mdx mice despite lack of neuronal nitric oxide synthase.

21 January 2018

1 reference

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mdx muscle pathology is independent of nNOS perturbation

21 January 2018

1 reference

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Evidence of oxidative stress in mdx mouse muscle: studies of the pre-necrotic state

21 January 2018

1 reference

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A dystrophin missense mutation showing persistence of dystrophin and dystrophin-associated proteins yet a severe phenotype

21 January 2018

1 reference

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Exogenous Dp71 restores the levels of dystrophin associated proteins but does not alleviate muscle damage in mdx mice

21 January 2018

1 reference

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Undetectable dystrophin can still result in a relatively benign phenotype of dystrophinopathy

21 January 2018

1 reference

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Oxyradical damage and mitochondrial enzyme activities in the mdx mouse

21 January 2018

1 reference

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Oxidative damage to muscle protein in Duchenne muscular dystrophy

21 January 2018

1 reference

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Oxidative stress as a potential pathogenic mechanism in an animal model of Duchenne muscular dystrophy

21 January 2018

1 reference

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Overexpression of copper/zinc superoxide dismutase: a novel cause of murine muscular dystrophy

21 January 2018

1 reference

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Muscle cells from mdx mice have an increased susceptibility to oxidative stress

21 January 2018

1 reference

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Copper/zinc superoxide dismutase: more is not necessarily better!

21 January 2018

1 reference

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Transmembrane signalling by integrins

21 January 2018

1 reference

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The molecular basis of muscular dystrophy in the mdx mouse: a point mutation

21 January 2018

1 reference

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Chemical biology of nitric oxide: Insights into regulatory, cytotoxic, and cytoprotective mechanisms of nitric oxide

21 January 2018

1 reference

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Characterization of translational frame exception patients in Duchenne/Becker muscular dystrophy

21 January 2018

1 reference

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10.1002/(SICI)1097-4598(200005)23:5<784::AID-MUS17>3.0.CO;2-Y

21 January 2018

Identifiers

DOI

1 reference

8 October 2017

1 reference

PubMed ID

10797403