(Q45855581)

17 December 2017

title

Metabolic profiles of dystrophin and utrophin expression in mouse models of Duchenne muscular dystrophy (English)

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17 December 2017

author name string

J L Griffin

1

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17 December 2017

E Sang

2

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17 December 2017

T Evens

3

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17 December 2017

K Davies

4

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17 December 2017

K Clarke

5

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17 December 2017

language of work or name

English

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publication date

1 October 2002

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17 December 2017

published in

FEBS Letters

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17 December 2017

volume

530

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17 December 2017

page(s)

109-116

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17 December 2017

issue

1-3

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17 December 2017

Population frequencies of inherited neuromuscular diseases—A world survey

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2802%2903437-3

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21 January 2018

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The complete sequence of dystrophin predicts a rod-shaped cytoskeletal protein

21 January 2018

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Primary structure of dystrophin-related protein

21 January 2018

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The structural and functional diversity of dystrophin

21 January 2018

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Utrophin binds laterally along actin filaments and can couple costameric actin with sarcolemma when overexpressed in dystrophin-deficient muscle

21 January 2018

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Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle.

21 January 2018

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Expression of full-length utrophin prevents muscular dystrophy in mdx mice

21 January 2018

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Muscular dystrophy--reason for optimism?

21 January 2018

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Metabolic profiling of genetic disorders: a multitissue (1)H nuclear magnetic resonance spectroscopic and pattern recognition study into dystrophic tissue

21 January 2018

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Abnormal lipid profile of dystrophic cardiac tissue as demonstrated by one- and two-dimensional magic-angle spinning (1)H NMR spectroscopy

21 January 2018

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Skeletal muscle-specific expression of a utrophin transgene rescues utrophin-dystrophin deficient mice.

21 January 2018

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Defective regulation of energy metabolism in mdx-mouse skeletal muscles

21 January 2018

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Regeneration and myogenic cell proliferation correlate with taurine levels in dystrophin- and MyoD-deficient muscles.

21 January 2018

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21 January 2018

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Rescue of skeletal muscles of gamma-sarcoglycan-deficient mice with adeno-associated virus-mediated gene transfer.

21 January 2018

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Adeno-associated virus vector carrying human minidystrophin genes effectively ameliorates muscular dystrophy in mdx mouse model

21 January 2018

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Aminoglycoside antibiotics restore dystrophin function to skeletal muscles of mdx mice

21 January 2018

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Molecular and functional analysis of the utrophin promoter

21 January 2018

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A second promoter provides an alternative target for therapeutic up-regulation of utrophin in Duchenne muscular dystrophy

21 January 2018

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Induction of utrophin gene expression by heregulin in skeletal muscle cells: role of the N-box motif and GA binding protein

21 January 2018

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21 January 2018

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Activation of calcineurin and stress activated protein kinase/p38-mitogen activated protein kinase in hearts of utrophin-dystrophin knockout mice

21 January 2018

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Diastolic dysfunction and altered energetics in the alphaMHC403/+ mouse model of familial hypertrophic cardiomyopathy

21 January 2018

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Metabolic shifts and myocyte hypertrophy in deflazacort treatment of mdx mouse cardiomyopathy

21 January 2018

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Nuclear magnetic resonance spectroscopy study of muscle growth, mdx dystrophy and glucocorticoid treatments: correlation with repair.

21 January 2018

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Investigation of skeletal muscle denervation and reinnervation using magnetic resonance spectroscopy

21 January 2018

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Metabonomics: a platform for studying drug toxicity and gene function

21 January 2018

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A functional genomics strategy that uses metabolome data to reveal the phenotype of silent mutations

21 January 2018

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Genetic suppression of phenotypes arising from mutations in dystrophin-related genes in Caenorhabditis elegans.

21 January 2018

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Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene

21 January 2018

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Cross-reactive protein in Duchenne muscle

21 January 2018

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Expression of truncated utrophin leads to major functional improvements in dystrophin-deficient muscles of mice

7 January 2021

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https://api.crossref.org/works/10.1016%2FS0014-5793%2802%2903437-3

Cellular energetics of dystrophic muscle

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2802%2903437-3

10.1016/S0014-5793(02)03437-3

7 January 2021

Identifiers

DOI

1 reference

17 December 2017

PubMed ID

12387876

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17 December 2017