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Cystic fibrosis
scientific article published on 01 January 1998
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instance of
scholarly article
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
review article
1 reference
stated in
Europe PubMed Central
title
Cystic fibrosis
(English)
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
main subject
cystic fibrosis
0 references
author
Pamela Zeitlin
series ordinal
2
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
author name string
B J Rosenstein
series ordinal
1
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
language of work or name
English
0 references
publication date
1 January 1998
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
published in
The Lancet
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
volume
351
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
issue
9098
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
page(s)
277-282
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
cites work
The cystic fibrosis transmembrane conductance regulator gene
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Identification of the cystic fibrosis gene: genetic analysis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
The diagnosis of cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Molecular diagnosis of cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Mutations in the cystic fibrosis gene in patients with congenital absence of the vas deferens
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Pulmonary Function and Clinical Observations in Men With Congenital Bilateral Absence of the Vas Deferens
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Neonatal screening for cystic fibrosis: a comparison of two strategies for case detection in 1.2 million babies
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
The changing epidemiology of cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
High-dose pancreatic-enzyme supplements and fibrosing colonopathy in children with cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Efficacy of aerosolized tobramycin in patients with cystic fibrosis.
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Prognosis in cystic fibrosis treated with continuous flucloxacillin from the neonatal period
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Lung transplantation
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Variable Severity of Pulmonary Disease in Adults with Identical Cystic Fibrosis Mutations
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Correlation between genotype and phenotype in patients with cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
A Cystic Fibrosis Mutation Associated with Mild Lung Disease
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
A cystic fibrosis transmembrane conductance regulator splice variant with partial penetrance associated with variable cystic fibrosis presentations
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Inhibition of epithelial Na+ currents by intracellular domains of the cystic fibrosis transmembrane conductance regulator
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Degradation of CFTR by the ubiquitin-proteasome pathway
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Chloride Conductance Expressed by ΔF508 and Other Mutant CFTRs In Xenopus Oocytes
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Aminoglycoside antibiotics restore CFTR function by overcoming premature stop mutations
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Correcting temperature-sensitive protein folding defects
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
A Short-Term Trial of Butyrate to Stimulate Fetal-Globin-Gene Expression in the β-Globin Disorders
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
In vivo activation of the cystic fibrosis transmembrane conductance regulator mutant deltaF508 in murine nasal epithelium
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
cAMP-independent activation of CFTR Cl channels by the tyrosine kinase inhibitor genistein
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Modulation of CFTR chloride channels by calyculin A and genistein
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
A1 receptor antagonist 8-cyclopentyl-1,3-dipropylxanthine selectively activates chloride efflux from human epithelial and mouse fibroblast cell lines expressing the cystic fibrosis transmembrane regulator delta F508 mutation
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Efficiency of gene transfer for restoration of normal airway epithelial function in cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Gender gap in cystic fibrosis mortality
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Diagnostic criteria for cystic fibrosis in men with congenital absence of the vas deferens
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Genetic and clinical features of patients with cystic fibrosis diagnosed after the age of 16 years
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Conventional and modified nasal potential-difference measurement in cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Sweat testing for the diagnosis of cystic fibrosis: practical considerations
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Diagnosing cystic fibrosis: blood, sweat, and tears
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
The effects of panresistant bacteria in cystic fibrosis patients on lung transplant outcome
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Heart-lung transplantation for patients under 10 with cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Antibiotic treatment of initial colonization with Pseudomonas aeruginosa postpones chronic infection and prevents deterioration of pulmonary function in cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Effect of high-dose ibuprofen in patients with cystic fibrosis.
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Pilot study to assess the effect of inhaled corticosteroids on lung function in patients with cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Pediatric lung transplantation at St. Louis Children's Hospital, 1990-1995
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Colonization of the respiratory tract with Pseudomonas cepacia in cystic fibrosis. Risk factors and outcomes
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Cystic fibrosis: a review of pulmonary infections and interventions
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Familial concordance of pancreatic function in cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Cystic fibrosis 3849+10kb C > T mutation associated with severe pulmonary disease and male fertility
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Clinical spectrum in homozygotes and compound heterozygotes inheriting cystic fibrosis mutation 3849 + 10kbC > T: significance for geneticists
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Genetic determinants of airways' colonisation with Pseudomonas aeruginosa in cystic fibrosis
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Relationship of genotype to early pulmonary function in infants with cystic fibrosis identified through neonatal screening.
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Resting energy expenditure, pulmonary inflammation, and genotype in the early course of cystic fibrosis.
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Determinants of mild clinical symptoms in cystic fibrosis patients. Residual chloride secretion measured in rectal biopsies in relation to the genotype
1 reference
stated in
Crossref
reference URL
https://api.crossref.org/works/10.1016%2FS0140-6736%2897%2909174-5
retrieved
7 January 2021
based on heuristic
inferred from DOI database lookup
Identifiers
DOI
10.1016/S0140-6736(97)09174-5
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
PubMed publication ID
9457113
1 reference
stated in
Europe PubMed Central
PubMed publication ID
9457113
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:9457113%20AND%20SRC:MED&resulttype=core&format=json
retrieved
9 November 2019
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