(Q22253419)

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Crystal structure of human branched-chain alpha-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease

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Crystal structure of human branched-chain alpha-ketoacid dehydrogenase and the molecular basis of multienzyme complex deficiency in maple syrup urine disease (English)

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crystal structure

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maple syrup urine disease

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inferred from title

author name string

A AEvarsson

1

author given names

A

author last names

AEvarsson

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28 March 2023

J L Chuang

2

author given names

J L

author last names

Chuang

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28 March 2023

R M Wynn

3

author given names

R M

author last names

Wynn

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28 March 2023

S Turley

4

author given names

S

author last names

Turley

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28 March 2023

D T Chuang

5

author given names

D T

author last names

Chuang

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28 March 2023

W G Hol

6

author given names

W G

author last names

Hol

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28 March 2023

language of work or name

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publication date

15 March 2000

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8

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277-91

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3

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Regulation of mammalian pyruvate and branched-chain alpha-keto acid dehydrogenase complexes by phosphorylation-dephosphorylation

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Atomic structure of the cubic core of the pyruvate dehydrogenase multienzyme complex

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Roles of amino acid residues surrounding phosphorylation site 1 of branched-chain alpha-ketoacid dehydrogenase (BCKDH) in catalysis and phosphorylation site recognition by BCKDH kinase.

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1 reference

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10.1016/S0969-2126(00)00105-2

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