(Q24299371)

respiratory chain complex IV assembly

GOA release 2020-03-11

1 reference

GOA release 2020-03-11

author

Pierre Rustin

3

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Jan-Willem Taanman

4

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author name string

Siôn L Williams

1

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Isabelle Valnot

Journal of Biological Chemistry

2

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language of work or name

English

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publication date

27 February 2004

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published in

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volume

279

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issue

9

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page(s)

7462-9

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cites work

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SURF1, encoding a factor involved in the biogenesis of cytochrome c oxidase, is mutated in Leigh syndrome

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Constitutive knockout of Surf1 is associated with high embryonic lethality, mitochondrial disease and cytochrome c oxidase deficiency in mice

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Shy1p is necessary for full expression of mitochondrial COX1 in the yeast model of Leigh's syndrome

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COX15 codes for a mitochondrial protein essential for the assembly of yeast cytochrome oxidase

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Mutations in COX10 result in a defect in mitochondrial heme A biosynthesis and account for multiple, early-onset clinical phenotypes associated with isolated COX deficiency

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Cleavage of Structural Proteins during the Assembly of the Head of Bacteriophage T4

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21 January 2018

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7 January 2021

Mitochondrial copper metabolism in yeast: interaction between Sco1p and Cox2p

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7 January 2021

Expression of mtDNA and nDNA encoded respiratory chain proteins in chemically and genetically-derived Rho0 human fibroblasts: a comparison of subunit proteins in normal fibroblasts treated with ethidium bromide and fibroblasts from a patient with mt

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7 January 2021

Detergent-solubilized bovine cytochrome c oxidase: dimerization depends on the amphiphilic environment

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7 January 2021

Immunological phenotyping of fibroblast cultures from patients with a mitochondrial respiratory chain deficit

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7 January 2021

SCO1 and SCO2 act as high copy suppressors of a mitochondrial copper recruitment defect in Saccharomyces cerevisiae

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7 January 2021

Characterization of YpmQ, an accessory protein required for the expression of cytochrome c oxidase in Bacillus subtilis

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7 January 2021

A human SCO2 mutation helps define the role of Sco1p in the cytochrome oxidase assembly pathway

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7 January 2021

Molecular mechanisms in mitochondrial DNA depletion syndrome

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7 January 2021