(Q24531109)

English

Activities of branched-chain 2-oxo acid dehydrogenase and its components in skin fibroblasts from normal and classical-maple-syrup-urine-disease subjects

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scholarly article

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Activities of branched-chain 2-oxo acid dehydrogenase and its components in skin fibroblasts from normal and classical-maple-syrup-urine-disease subjects (English)

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author name string

D T Chuang

1

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W L Niu

2

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R P Cox

3

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language of work or name

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publication date

15 October 1981

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Biochemical Journal

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200

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1

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59-67

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Purification and characterization of branched chain alpha-keto acid dehydrogenase complex of bovine kidney

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

24 March 2017

ON THE NATURE OF ALLOSTERIC TRANSITIONS: A PLAUSIBLE MODEL

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

24 March 2017

A kinetic study of dihydrolipoyl transacetylase from bovine kidney

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

24 March 2017

Purification and characterization of branched chain alpha-ketoacid dehydrogenase from bovine liver mitochondria

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

24 March 2017

Partial purification and properties of branched-chain 2-oxo acid dehydrogenase of ox liver

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

24 March 2017

Pyruvate dehydrogenase complex activity in normal and deficient fibroblasts

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

27 September 2017

Maple syrup urine disease: branched-chain keto acid decarboxylation in fibroblasts as measured with amino acids and keto acids

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

27 September 2017

Substrate specificity and stabilization by thiamine pyrophosphate of rat liver branched chain α-ketoacid dehydrogenase

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

27 September 2017

Clonal growth in vitro of epithelial cells from normal human tissues

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

30 May 2018

Reversible ATP-induced inactivation of branched-chain 2-oxo acid dehydrogenase

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

30 May 2018

The effect of acylcarnitines on the oxidation of branched chain α-keto acids in mitochondria

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

30 May 2018

Role of pyruvate carboxylase in fatty acid synthesis: Alterations during preadipocyte differentiation

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1163502

30 May 2018

Intermittent branched-chain ketonuria. Variant of maple-syrup-urine disease

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The enzyme defect in maple syrup urine disease (branched chain ketoaciduria)

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Mammalian alpha-keto acid dehydrogenase complexes. VI. Nature of the multiple forms of pig heart lipoamide dehydrogenase

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Enzyme activity in classical and variant forms of maple syrup urine disease

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Rapid diagnosis of maple syrup urine disease (branched chain ketoaciduria) by micro-enzyme assay in leukocytes and fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Complementation Analysis of Maple Syrup Urine Disease in Heterokaryons derived from Cultured Human Fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Subcellular distribution and cofactor function of human branched chain alpha-ketoacid dehydrogenase in normal and mutant cultured skin fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Maple Syrup Urine Disease: Analysis of Branched Chain Ketoacid Decarboxylation in Cultured Fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Modulation of branched-chain alpha-keto acid decarboxylase activity in rat liver mitochondria by hypophysectomy

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Structure, assembly and function of mammalian alpha-keto acid dehydrogenase complexes

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Friedreich's ataxia: I. Normal pyruvate dehydrogenase complex activity in platelets

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Active and inactive forms of branched-chain 2-oxoacid dehydrogenase complex in rat heart and skeletal muscle

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Direct evidence for the inactivation of branched-chain oxo-acid dehydrogenase by enzyme phosphorylation

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Inactivation of rat liver and kidney branched chain 2‐oxoacid dehydrogenase complex by adenosine triphosphate

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Studies on the nature and reactions of protein-bound lipoic acid

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

alpha-Ketoglutaric dehydrogenase. VII. The role of thioctic acid

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

THE METABOLISM OF LEUCINE IN TISSUE CULTURE OF SKIN FIBROBLASTS OF MAPLE-SYRUP-URINE DISEASE

1 reference

https://pubmed.ncbi.nlm.nih.gov/6895847

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1042/BJ2000059

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