(Q28186254)

The cerebral proteopathies

published in

Molecular Neurobiology

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volume

21

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issue

1-2

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page(s)

83-95

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cites work

1 reference

12 December 2020

Structural neurology: are seeds at the root of neuronal degeneration?

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12 December 2020

Genetics of Alzheimer's disease

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12 December 2020

Induction of beta (A4)-amyloid in primates by injection of Alzheimer's disease brain homogenate. Comparison with transmission of spongiform encephalopathy

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12 December 2020

Unifying features of systemic and cerebral amyloidosis

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12 December 2020

Soluble pool of Abeta amyloid as a determinant of severity of neurodegeneration in Alzheimer's disease

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12 December 2020

A decamer duplication in the 3' region of the BRI gene originates an amyloid peptide that is associated with dementia in a Danish kindred

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12 December 2020

Anti-amyloid drugs: potential in the treatment of diseases associated with aging

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12 December 2020

Apolipoprotein E4 promotes incipient Alzheimer pathology in the elderly.

1 reference

12 December 2020

Correlative Memory Deficits, Abeta Elevation, and Amyloid Plaques in Transgenic Mice

1 reference

12 December 2020

High-level neuronal expression of abeta 1-42 in wild-type human amyloid protein precursor transgenic mice: synaptotoxicity without plaque formation

1 reference

12 December 2020

Common core structure of amyloid fibrils by synchrotron X-ray diffraction.

1 reference

12 December 2020

Familial Parkinson disease gene product, parkin, is a ubiquitin-protein ligase

1 reference

12 December 2020

Labeling of cerebral amyloid in vivo with a monoclonal antibody

1 reference

12 December 2020

Diffusible, nonfibrillar ligands derived from Abeta1-42 are potent central nervous system neurotoxins

1 reference

12 December 2020

Spontaneous generation of infectious nucleating amyloids in the transmissible and nontransmissible cerebral amyloidoses

1 reference

12 December 2020

Transgenic mice in the study of polyglutamine repeat expansion diseases

1 reference

12 December 2020

Aggresomes: a cellular response to misfolded proteins

1 reference

12 December 2020

Evidence for and against the transmissibility of Alzheimer disease

1 reference

12 December 2020

Creutzfeldt-Jakob disease and related transmissible spongiform encephalopathies

1 reference

12 December 2020

Origin of the name "amyloidosis". Proposal for its replacement

1 reference

12 December 2020

Soluble amyloid beta peptide concentration as a predictor of synaptic change in Alzheimer's disease

1 reference

12 December 2020

Expanded polyglutamine in the Machado-Joseph disease protein induces cell death in vitro and in vivo

1 reference

12 December 2020

Protein aggregation after transient cerebral ischemia.

1 reference

12 December 2020

Nonapoptotic neurodegeneration in a transgenic mouse model of Huntington's disease

1 reference

12 December 2020

Huntingtin acts in the nucleus to induce apoptosis but death does not correlate with the formation of intranuclear inclusions.

1 reference

12 December 2020

Advanced glycation endproducts are associated with Hirano bodies in Alzheimer's disease

1 reference

12 December 2020

Protein misfolding, evolution and disease

1 reference

12 December 2020

Amyloid deposition is delayed in mice with targeted deletion of the serum amyloid P component gene

1 reference

12 December 2020

Apolipoprotein E4 promotes the early deposition of Abeta42 and then Abeta40 in the elderly

1 reference

12 December 2020

Peripherally administered antibodies against amyloid beta-peptide enter the central nervous system and reduce pathology in a mouse model of Alzheimer disease

1 reference

12 December 2020

A beta amyloidogenesis: unique, or variation on a systemic theme?

1 reference

12 December 2020

Aggregates in neurodegenerative disease: crowds and power?

1 reference

12 December 2020

The mechanism of Z alpha 1-antitrypsin accumulation in the liver

1 reference

12 December 2020

Approaches to discovery and characterization of inhibitors of amyloid beta-peptide polymerization

1 reference

12 December 2020

Suppression of aggregate formation and apoptosis by transglutaminase inhibitors in cells expressing truncated DRPLA protein with an expanded polyglutamine stretch.

1 reference

12 December 2020

A stop-codon mutation in the BRI gene associated with familial British dementia

1 reference

12 December 2020

Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis

1 reference

12 December 2020

The mechanism of islet amyloid polypeptide toxicity is membrane disruption by intermediate-sized toxic amyloid particles.

1 reference

12 December 2020

Intranuclear neuronal inclusions in Huntington's disease and dentatorubral and pallidoluysian atrophy: correlation between the density of inclusions and IT15 CAG triplet repeat length

1 reference

12 December 2020

Familial dementia caused by polymerization of mutant neuroserpin

1 reference

12 December 2020

Elevated transglutaminase-induced bonds in PHF tau in Alzheimer's disease.

1 reference

12 December 2020

Blood buffy coat from Alzheimer's disease patients and their relatives does not transmit spongiform encephalopathy to hamsters.

1 reference

12 December 2020

ER stress response: getting the UPR hand on misfolded proteins

1 reference

12 December 2020

The alternative conformations of amyloidogenic proteins and their multi-step assembly pathways

1 reference

12 December 2020

Fractionation and characterization of oligomeric, protofibrillar and fibrillar forms of beta-amyloid peptide

1 reference

12 December 2020

Alzheimer's disease amyloid propagation by a template-dependent dock-lock mechanism

1 reference

12 December 2020

The pathogenesis of Alzheimer disease: an alternative to the amyloid hypothesis

1 reference

12 December 2020

Beta-secretase cleavage of Alzheimer's amyloid precursor protein by the transmembrane aspartic protease BACE

1 reference

12 December 2020

Seeding "one-dimensional crystallization" of amyloid: a pathogenic mechanism in Alzheimer's disease and scrapie?

1 reference

12 December 2020

Prion research: the next frontiers.

1 reference

12 December 2020

Beta-sheet breaker peptides inhibit fibrillogenesis in a rat brain model of amyloidosis: implications for Alzheimer's therapy

1 reference

12 December 2020

Identification of the major Abeta1-42-degrading catabolic pathway in brain parenchyma: suppression leads to biochemical and pathological deposition

1 reference

12 December 2020

Islet amyloid and type 2 diabetes mellitus

1 reference

12 December 2020

Inhibition of huntingtin fibrillogenesis by specific antibodies and small molecules: implications for Huntington's disease therapy

1 reference

12 December 2020

Immunization with amyloid-beta attenuates Alzheimer-disease-like pathology in the PDAPP mouse

1 reference

12 December 2020

Amyloid diseases: abnormal protein aggregation in neurodegeneration

1 reference

12 December 2020

Disaggregation of Alzheimer beta-amyloid by site-directed mAb.

1 reference

12 December 2020

1 reference

12 December 2020

Tissue transglutaminase: a possible role in neurodegenerative diseases

1 reference

12 December 2020

BACE2, a beta -secretase homolog, cleaves at the beta site and within the amyloid-beta region of the amyloid-beta precursor protein

1 reference

12 December 2020

In search of gamma-secretase: presenilin at the cutting edge

1 reference

12 December 2020

Search for a transmissible agent in Alzheimer's disease: studies of human buffy coat.

1 reference

12 December 2020

Mutations in RNA: a first example of molecular misreading in Alzheimer's disease

1 reference

12 December 2020

Progressive dementia and epilepsy in a young adult: unusual intraneuronal inclusions

1 reference

12 December 2020

Familial Presenile Dementia with Spastic Paralysis

1 reference

12 December 2020

Etiology and pathogenesis of prion diseases.

1 reference

12 December 2020

Evidence for seeding of beta -amyloid by intracerebral infusion of Alzheimer brain extracts in beta -amyloid precursor protein-transgenic mice.

1 reference

12 December 2020

Amyloid deposits and amyloidosis. The beta-fibrilloses (first of two parts).

1 reference

12 December 2020

Screening for pharmacologic inhibitors of amyloid fibril formation.

1 reference

12 December 2020

Islet amyloid: a long-recognized but underappreciated pathological feature of type 2 diabetes

1 reference

12 December 2020

Gene dose of apolipoprotein E type 4 allele and the risk of Alzheimer's disease in late onset families

1 reference

12 December 2020

Apolipoprotein E polymorphism and Alzheimer's disease.

1 reference

12 December 2020

Protein precipitation: a common etiology in neurodegenerative disorders?

1 reference

12 December 2020

The biophysics of sickle cell hydroxyurea therapy

1 reference

12 December 2020

Prion diseases and the BSE crisis

1 reference

12 December 2020

Conformational disease

1 reference

12 December 2020

Mitotic phosphoepitopes precede paired helical filaments in Alzheimer's disease

1 reference

12 December 2020

REVIEW: tau protein pathology in Alzheimer's disease and related disorders

1 reference

12 December 2020

Nucleated conformational conversion and the replication of conformational information by a prion determinant

1 reference

12 December 2020