(Q28533968)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

title

N-acetyl-L-cysteine prevents stress-induced desmin aggregation in cellular models of desminopathy (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

0 references

1 reference

Bertrand-David Segard

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

author name string

Florence Delort

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

Virginie Bailleux

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

Stéphanie Simon

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

Emilie Leccia

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

Blandine Gausseres

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

Fatma Briki

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

Patrick Vicart

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

Sabrina Batonnet-Pichon

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

language of work or name

English

0 references

publication date

1 October 2013

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

volume

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

issue

10

1 reference

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27 February 2020

page(s)

e76361

1 reference

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Creative Commons Attribution 4.0 International

27 February 2020

copyright license

start time

1 October 2013

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

describes a project that uses

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3788106/fullTextXML

inferred from PubMed Central ID database lookup

cites work

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Desmin is essential for the tensile strength and integrity of myofibrils but not for myogenic commitment, differentiation, and fusion of skeletal muscle

19 March 2017

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Oxidative stress and successful antioxidant treatment in models of RYR1-related myopathy

29 September 2017

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Subcellular localization of SREBP1 depends on its interaction with the C-terminal region of wild-type and disease related A-type lamins

29 September 2017

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Desmin mutations in the terminal consensus motif prevent synemin-desmin heteropolymer filament assembly.

29 September 2017

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Disease mutations in the "head" domain of the extra-sarcomeric protein desmin distinctly alter its assembly and network-forming properties

29 September 2017

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Protective effect of geranylgeranylacetone via enhancement of HSPB8 induction in desmin-related cardiomyopathy

29 September 2017

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Tensile properties of single desmin intermediate filaments

29 September 2017

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Association of alphaB-crystallin, a small heat shock protein, with actin: role in modulating actin filament dynamics in vivo

29 September 2017

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29 September 2017

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Cell signaling pathways to alphaB-crystallin following stresses of the cytoskeleton

29 September 2017

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Variable pathogenic potentials of mutations located in the desmin alpha-helical domain.

29 September 2017

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Severe muscle disease-causing desmin mutations interfere with in vitro filament assembly at distinct stages

29 September 2017

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Expression of stress-related genes in a cadmium-resistant A549 human cell line

29 September 2017

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The biology of desmin filaments: how do mutations affect their structure, assembly, and organisation?

29 September 2017

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29 September 2017

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29 September 2017

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29 September 2017

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Desmin mutation responsible for idiopathic dilated cardiomyopathy

29 September 2017

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Expression of the 25-kDa heat-shock protein (HSP27) correlates with resistance to the toxicity of cadmium chloride, mercuric chloride, cis-platinum(II)-diammine dichloride, or sodium arsenite in mouse embryonic stem cells transfected with sense or a

29 September 2017

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29 September 2017

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29 September 2017

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Distinct chaperone mechanisms can delay the formation of aggresomes by the myopathy-causing R120G alphaB-crystallin mutant

2 June 2018

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2 June 2018

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2 June 2018

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2 June 2018

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2 June 2018

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Disease severity in dominant Emery Dreifuss is increased by mutations in both emerin and desmin proteins.

21 January 2018

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A missense mutation in desmin tail domain linked to human dilated cardiomyopathy promotes cleavage of the head domain and abolishes its Z-disc localization.

21 January 2018

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21 January 2018

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Hsp27-2D-gel electrophoresis is a diagnostic tool to differentiate primary desminopathies from myofibrillar myopathies

21 January 2018

1 reference

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H2O2 activation of HSP25/27 protects desmin from calpain proteolysis in rat ventricular myocytes.

21 January 2018

1 reference

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Cyclic stretch reveals a mechanical role for intermediate filaments in a desminopathic cell model

21 January 2018

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Nuclear envelope disorganization in fibroblasts from lipodystrophic patients with heterozygous R482Q/W mutations in the lamin A/C gene

21 January 2018

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Severe myopathy mutations modify the nanomechanics of desmin intermediate filaments

27 November 2018

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12 December 2020

Biomechanical characterization of a desminopathy in primary human myoblasts

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12 December 2020

Desmin Is Oxidized and Nitrated in Affected Muscles in Myotilinopathies and Desminopathies

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12 December 2020

Glucocorticoid treatment induces expression of small heat shock proteins in human satellite cell populations: consequences for a desmin-related myopathy involving the R120G alpha B-crystallin mutation

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12 December 2020

Conspicuous involvement of desmin tail mutations in diverse cardiac and skeletal myopathies

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12 December 2020

Analysis of skeletal and cardiac muscle from desmin knock-out and normal mice by high resolution separation of myosin heavy-chain isoforms

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12 December 2020

Impact of disease mutations on the desmin filament assembly process

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12 December 2020

Mice expressing L345P mutant desmin exhibit morphological and functional changes of skeletal and cardiac mitochondria

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12 December 2020

Oxidative Stress in Desminopathies and Myotilinopathies: A Link between Oxidative Damage and Abnormal Protein Aggregation

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12 December 2020

10.1371/JOURNAL.PONE.0076361

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

0 references

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json

27 February 2020

PubMed publication ID

24098483

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24098483%20AND%20SRC:MED&resulttype=core&format=json