(Q32086395)

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Frontiers in research on cystic fibrosis: understanding its molecular and chemical basis and relationship to the pathogenesis of the disease

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scholarly article

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

1 reference

Europe PubMed Central

Frontiers in research on cystic fibrosis: understanding its molecular and chemical basis and relationship to the pathogenesis of the disease (English)

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

cystic fibrosis

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author name string

Ko YH

1

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

Pedersen PL

2

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

language of work or name

1 reference

based on heuristic

inferred from title

publication date

1 October 1997

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

Journal of Bioenergetics and Biomembranes

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

29

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

5

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

417-427

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Europe PubMed Central

PubMed publication ID

6 July 2017

Strategies for correcting the delta F508 CFTR protein-folding defect

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Phosphorylation-regulated CI− channel in CHO cells stably expressing the cystic fibrosis gene

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Altered protein folding may be the molecular basis of most cases of cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Chloride Conductance Expressed by ΔF508 and Other Mutant CFTRs In Xenopus Oocytes

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Antibacterial peptides: key components needed in immunity

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

ATP-binding site of adenylate kinase: mechanistic implications of its homology with ras-encoded p21, F1-ATPase, and other nucleotide-binding proteins

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Modeling of nucleotide binding domains of ABC transporter proteins based on a F1-ATPase/recA topology: structural model of the nucleotide binding domains of the cystic fibrosis transmembrane conductance regulator (CFTR)

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Defensins. Natural peptide antibiotics of human neutrophils

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

ATP synthases. Structure, reaction center, mechanism, and regulation of one of nature's most unique machines

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The two nucleotide-binding domains of cystic fibrosis transmembrane conductance regulator (CFTR) have distinct functions in controlling channel activity

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Binding of Pseudomonas aeruginosa to respiratory epithelial cells from patients with various mutations in the cystic fibrosis transmembrane regulator

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

In vitro mutated beta subunits from the F1-ATPase of the thermophilic bacterium, PS3, containing glutamine in place of glutamic acid in positions 190 or 201 assembles with the alpha and gamma subunits to produce inactive complexes

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Expression and functional properties of the second predicted nucleotide binding fold of the cystic fibrosis transmembrane conductance regulator fused to glutathione-S-transferase.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Regulation by ATP and ADP of CFTR chloride channels that contain mutant nucleotide-binding domains

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Intracellular turnover of cystic fibrosis transmembrane conductance regulator. Inefficient processing and rapid degradation of wild-type and mutant proteins

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Defensins: antimicrobial and cytotoxic peptides of mammalian cells

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The common variant of cystic fibrosis transmembrane conductance regulator is recognized by hsp70 and degraded in a pre-Golgi nonlysosomal compartment

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis: a disease of altered protein folding

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The cystic fibrosis transmembrane conductance regulator. Effects of the most common cystic fibrosis-causing mutation on the secondary structure and stability of a synthetic peptide

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Distantly related sequences in the alpha- and beta-subunits of ATP synthase, myosin, kinases and other ATP-requiring enzymes and a common nucleotide binding fold

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Mitochondrial ATP synthase. Quaternary structure of the F1 moiety at 3.6 A determined by x-ray diffraction analysis

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The spectrum of cystic fibrosis mutations

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

NMR studies of the interactions of substrates with enzymes and their peptide fragments.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Membrane pores induced by magainin

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic Fibrosis Transmembrane Conductance Regulator: Nucleotide Binding to a Synthetic Peptide

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Mutant (delta F508) cystic fibrosis transmembrane conductance regulator Cl- channel is functional when retained in endoplasmic reticulum of mammalian cells.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peptides with affinity for membranes

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Regulation of CFTR channel gating

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Effects of the delta F508 mutation on the structure, function, and folding of the first nucleotide-binding domain of CFTR.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Nucleoside triphosphates are required to open the CFTR chloride channel.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peptides from frog skin

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Effects of pyrophosphate and nucleotide analogs suggest a role for ATP hydrolysis in cystic fibrosis transmembrane regulator channel gating.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Adenosine triphosphatase and nucleotide binding activity of isolated beta-subunit preparations from Escherichia coli F1F0-ATP synthase

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Structural model of the nucleotide-binding conserved component of periplasmic permeases

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Control of CFTR chloride conductance by ATP levels through non-hydrolytic binding

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The ATP-binding component of a prokaryotic traffic ATPase is exposed to the periplasmic (external) surface

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Structure of the recA protein–ADP complex

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Structure at 2.8 A resolution of F1-ATPase from bovine heart mitochondria

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis: molecular biology and therapeutic implications

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Structural and functional similarities between the nucleotide-binding domains of CFTR and GTP-binding proteins

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Role of mutant CFTR in hypersusceptibility of cystic fibrosis patients to lung infections.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The nucleotide binding folds of the cystic fibrosis transmembrane conductance regulator are extracellularly accessible

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The cystic fibrosis transmembrane conductance regulator. Nucleotide binding to a synthetic peptide segment from the second predicted nucleotide binding fold.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Phosphorylation by cAMP-dependent protein kinase causes a conformational change in the R domain of the cystic fibrosis transmembrane conductance regulator

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Tracheal antimicrobial peptide, a cysteine-rich peptide from mammalian tracheal mucosa: peptide isolation and cloning of a cDNA.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Generation of cAMP-Activated Chloride Currents by Expression of CFTR

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

ABC Transporters: From Microorganisms to Man

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis transmembrane conductance regulator mutations that disrupt nucleotide binding

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Coupling of ATP hydrolysis with channel gating by purified, reconstituted CFTR.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Neutrophils and host defense

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Structure-function analysis of the histidine permease and comparison with cystic fibrosis mutations

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Antimicrobial defensin peptides form voltage-dependent ion-permeable channels in planar lipid bilayer membranes

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Antimicrobial activity of synthetic magainin peptides and several analogues

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The cystic fibrosis mutation (delta F508) does not influence the chloride channel activity of CFTR.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Three-dimensional structure of adenyl kinase

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The relation between genotype and phenotype in cystic fibrosis--analysis of the most common mutation (delta F508).

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Primary structures of MCP-1 and MCP-2, natural peptide antibiotics of rabbit lung macrophages

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Functional roles of the nucleotide-binding folds in the activation of the cystic fibrosis transmembrane conductance regulator

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis, lung infections, and a human tracheal antimicrobial peptide (hTAP)

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Mapping of cystic fibrosis transmembrane conductance regulator membrane topology by glycosylation site insertion.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Rat liver ATP synthase. Relationship of the unique substructure of the F1 moiety to its nucleotide binding properties, enzymatic states, and crystalline form

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

ATP-dependent transport systems in bacteria and humans: relevance to cystic fibrosis and multidrug resistance

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Spectrum of mutations in cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Recombinant synthesis, purification, and nucleotide binding characteristics of the first nucleotide binding domain of the cystic fibrosis gene product

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The amino-terminal portion of CFTR forms a regulated Cl- channel.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Abnormal localization of cystic fibrosis transmembrane conductance regulator in primary cultures of cystic fibrosis airway epithelia

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Chemical ecology

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Protein kinase A (PKA) still activates CFTR chloride channel after mutagenesis of all 10 PKA consensus phosphorylation sites

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis transmembrane conductance regulator: the first nucleotide binding fold targets the membrane with retention of its ATP binding function.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The chemistry of poisons in amphibian skin

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Intrinsic anion channel activity of the recombinant first nucleotide binding fold domain of the cystic fibrosis transmembrane regulator protein

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The cystic fibrosis transmembrane conductance regulator. Overexpression, purification, and characterization of wild type and delta F508 mutant forms of the first nucleotide binding fold in fusion with the maltose-binding protein.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Regulation of CFTR Cl- conductance in secretion by cellular energy levels

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

E. coli F1-ATPase: site-directed mutagenesis of the beta-subunit.

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The protein kinase A-regulated cardiac Cl- channel resembles the cystic fibrosis transmembrane conductance regulator

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Sequence homologies between nucleotide binding regions of CFTR and G-proteins suggest structural and functional similarities

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Structural model of ATP-binding proteins associated with cystic fibrosis, multidrug resistance and bacterial transport

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Conformational maturation of CFTR but not its mutant counterpart (delta F508) occurs in the endoplasmic reticulum and requires ATP

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Two conformations of crystalline adenylate kinase

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Bee and wasp venoms

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Interaction of a Lytic Polypeptide, Melittin, with Lipid Membrane Systems

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/9511927

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1023/A:1022402105375

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

Dimensions Publication ID

0 references

PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

6 July 2017

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