(Q33887985)

29 July 2017

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title

Spinocerebellar ataxia type 1--modeling the pathogenesis of a polyglutamine neurodegenerative disorder in transgenic mice (English)

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29 July 2017

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spinocerebellar ataxia

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Clark HB

1

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29 July 2017

Orr HT

series ordinal

2

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29 July 2017

publication date

1 April 2000

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Journal of Neuropathology & Experimental Neurology

29 July 2017

published in

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29 July 2017

volume

59

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29 July 2017

issue

4

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29 July 2017

page(s)

265-270

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Letter: Hereditary ataxia and HL-A genotypes

29 July 2017

cites work

1 reference

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21 January 2018

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Evidence for a mechanism predisposing to intergenerational CAG repeat instability in spinocerebellar ataxia type I.

21 January 2018

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Intranuclear neuronal inclusions: a common pathogenic mechanism for glutamine-repeat neurodegenerative diseases?

21 January 2018

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Striatal dopamine nerve terminal markers but not nigral cellularity are reduced in spinocerebellar ataxia type 1.

21 January 2018

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An epidemiological study of mental health and socioeconomic conditions in Sumatera, Indonesia

21 January 2018

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Clinicopathology of spinocerebellar degeneration: its correlation to the unstable CAG repeat of the affected gene

21 January 2018

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The Purkinje cell in olivopontocerebellar atrophy. A Golgi and immunocytochemical study

21 January 2018

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Expression analysis of the ataxin-1 protein in tissues from normal and spinocerebellar ataxia type 1 individuals

21 January 2018

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Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures

21 January 2018

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Nuclear inclusions in spinocerebellar ataxia type 1.

21 January 2018

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Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain

21 January 2018

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Machado-Joseph disease gene product is a cytoplasmic protein widely expressed in brain

21 January 2018

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Spinocerebellar ataxia type 7 (SCA7): a neurodegenerative disorder with neuronal intranuclear inclusions

21 January 2018

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Nuclear inclusions of the androgen receptor protein in spinal and bulbar muscular atrophy

21 January 2018

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Intranuclear neuronal inclusions in Huntington's disease and dentatorubral and pallidoluysian atrophy: correlation between the density of inclusions and IT15 CAG triplet repeat length

21 January 2018

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Are neuronal intranuclear inclusions the common neuropathology of triplet-repeat disorders with polyglutamine-repeat expansions?

21 January 2018

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Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1.

21 January 2018

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Ataxin-1 nuclear localization and aggregation: role in polyglutamine-induced disease in SCA1 transgenic mice

21 January 2018

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Mutation of the Angelman ubiquitin ligase in mice causes increased cytoplasmic p53 and deficits of contextual learning and long-term potentiation.

21 January 2018

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A family of proteins structurally and functionally related to the E6-AP ubiquitin-protein ligase

21 January 2018

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Polyglutamine expansion down-regulates specific neuronal genes before pathologic changes in SCA1.

21 January 2018

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Mouse models of human CAG repeat disorders

21 January 2018

1 reference

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Clinical, neuropathologic, and genetic studies of a large spinocerebellar ataxia type 1 (SCA1) kindred

21 January 2018

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SCA1 transgenic mice: A model for neurodegeneration caused by an expanded CAG trinucleotide repeat

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FJNEN%2F59.4.265

21 January 2018

Identifiers

DOI

10.1093/JNEN/59.4.265

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29 July 2017

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