(Q34016471)

English

CFTR with a partially deleted R domain corrects the cystic fibrosis chloride transport defect in human airway epithelia in vitro and in mouse nasal mucosa in vivo

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scholarly article

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

CFTR with a partially deleted R domain corrects the cystic fibrosis chloride transport defect in human airway epithelia in vitro and in mouse nasal mucosa in vivo (English)

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

cystic fibrosis

0 references

author name string

Lynda S Ostedgaard

1

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Joseph Zabner

2

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Daniel W Vermeer

3

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Tatiana Rokhlina

4

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Philip H Karp

5

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Arlene A Stecenko

6

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Christoph Randak

7

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Michael J Welsh

8

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

language of work or name

0 references

publication date

19 February 2002

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Proceedings of the National Academy of Sciences of the United States of America

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

99

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

5

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

3093-3098

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

Adeno-associated virus type 6 (AAV6) vectors mediate efficient transduction of airway epithelial cells in mouse lungs compared to that of AAV2 vectors

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Non-specific activation of the epithelial sodium channel by the CFTR chloride channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Binding of adeno-associated virus type 5 to 2,3-linked sialic acid is required for gene transfer

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Regulation of the cystic fibrosis transmembrane conductance regulator Cl- channel by its R domain

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Gene therapy vectors based on adeno-associated virus: characteristics and applications to acquired and inherited diseases (review).

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Severed channels probe regulation of gating of cystic fibrosis transmembrane conductance regulator by its cytoplasmic domains

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Adeno-associated viral vectors as gene delivery vehicles

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

A functional R domain from cystic fibrosis transmembrane conductance regulator is predominantly unstructured in solution

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Adeno-associated virus type 5 (AAV5) but not AAV2 binds to the apical surfaces of airway epithelia and facilitates gene transfer

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Conformation, independent of charge, in the R domain affects cystic fibrosis transmembrane conductance regulator channel openings

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Gene transfer for cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Structure and function of the CFTR chloride channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Efficient expression of CFTR function with adeno-associated virus vectors that carry shortened CFTR genes

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Incorporation of adenovirus in calcium phosphate precipitates enhances gene transfer to airway epithelia in vitro and in vivo

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Membrane-associated heparan sulfate proteoglycan is a receptor for adeno-associated virus type 2 virions

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Function of the R domain in the cystic fibrosis transmembrane conductance regulator chloride channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Quantitative analysis of the packaging capacity of recombinant adeno-associated virus

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Human airway ion transport. Part one.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Regulation of the cystic fibrosis transmembrane conductance regulator Cl- channel by negative charge in the R domain.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

A mouse model for the delta F508 allele of cystic fibrosis.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Normalization of raised sodium absorption and raised calcium-mediated chloride secretion by adenovirus-mediated expression of cystic fibrosis transmembrane conductance regulator in primary human cystic fibrosis airway epithelial cells

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

The two nucleotide-binding domains of cystic fibrosis transmembrane conductance regulator (CFTR) have distinct functions in controlling channel activity

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Effect of deletion mutations on the function of CFTR chloride channels

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

5 July 2018

Expression of full-length and truncated dystrophin mini-genes in transgenic mdx mice

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.261714599

21 January 2018

Basolateral localization of fiber receptors limits adenovirus infection from the apical surface of airway epithelia.

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.261714599

21 January 2018

Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro.

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.261714599

21 January 2018

Stimulation of CFTR activity by its phosphorylated R domain.

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.261714599

21 January 2018

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.261714599

21 January 2018

Characterization of 19 disease-associated missense mutations in the regulatory domain of the cystic fibrosis transmembrane conductance regulator.

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.261714599

21 January 2018

Stimulatory and Inhibitory Functions of the R Domain on CFTR Chloride Channel.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

CFTR is a conductance regulator as well as a chloride channel

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

Control of CFTR channel gating by phosphorylation and nucleotide hydrolysis.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

CFTR activation: additive effects of stimulatory and inhibitory phosphorylation sites in the R domain.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

Expression of the cystic fibrosis transmembrane conductance regulator from a novel adeno-associated virus promoter.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=122478

29 October 2018

Gene therapy for cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Functional characterization of the CFTR R domain using CFTR/MDR1 hybrid and deletion constructs

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Effect of Deleting the R Domain on CFTR-Generated Chloride Channels

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Processing of CFTR bearing the P574H mutation differs from wild-type and deltaF508-CFTR

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Removal of multiple arginine-framed trafficking signals overcomes misprocessing of delta F508 CFTR present in most patients with cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Gene therapy for cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cystic fibrosis transmembrane conductance regulator Cl- channels with R domain deletions and translocations show phosphorylation-dependent and -independent activity

1 reference

https://pubmed.ncbi.nlm.nih.gov/11854474

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1073/PNAS.261714599

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

2002PNAS...99.3093O

0 references

PMC publication ID

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

30 July 2017

ResearchGate publication ID

0 references

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