(Q34078150)

30 July 2017

1 reference

title

Mouse models of genetic diseases resulting from mutations in elastic fiber proteins (English)

1 reference

30 July 2017

H C Dietz

1

1 reference

PubMed ID

11068202

30 July 2017

R P Mecham

series ordinal

2

1 reference

30 July 2017

1 November 2000

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30 July 2017

1 reference

30 July 2017

19

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30 July 2017

481-488

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30 July 2017

6

1 reference

Structure of the mutant fibrillin-1 gene in the tight skin (TSK) mouse.

30 July 2017

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Functional domains on elastin and microfibril-associated glycoprotein involved in elastic fibre assembly

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

The elastin gene is disrupted by a translocation associated with supravalvular aortic stenosis

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

TGF-beta1 binding protein-like modules of fibrillin-1 and -2 mediate integrin-dependent cell adhesion

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Endothelial cell connecting filaments anchor endothelial cells to the subjacent elastic lamina in the developing aortic intima of the mouse

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

A human vascular disorder, supravalvular aortic stenosis, maps to chromosome 7.

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Differential response of mesoderm- and neural crest-derived smooth muscle to TGF-beta1: regulation of c-myb and alpha1 (I) procollagen genes

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Bovine latent transforming growth factor beta 1-binding protein 2: molecular cloning, identification of tissue isoforms, and immunolocalization to elastin-associated microfibrils

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Identification and characterization of an eight-cysteine repeat of the latent transforming growth factor-beta binding protein-1 that mediates bonding to the latent transforming growth factor-beta1.

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

The fine structure of elastic fibers

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Recombinant latent transforming growth factor beta-binding protein 2 assembles to fibroblast extracellular matrix and is susceptible to proteolytic processing and release.

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

TGF-beta 1 binding protein: a component of the large latent complex of TGF-beta 1 with multiple repeat sequences

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

The Tight skin mouse: demonstration of mutant fibrillin-1 production and assembly into abnormal microfibrils.

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Elastin is an essential determinant of arterial morphogenesis

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Novel arterial pathology in mice and humans hemizygous for elastin

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Interactions between growth factors and integrins: latent forms of transforming growth factor-beta are ligands for the integrin alphavbeta1

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Latent transforming growth factor-beta: structural features and mechanisms of activation

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

The integrin alpha v beta 6 binds and activates latent TGF beta 1: a mechanism for regulating pulmonary inflammation and fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Spontaneous occurrence of anti-fibrillin-1 autoantibodies in tight-skin mice

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Self Reactive Repertoire of Tight Skin Mouse: Immunochemical and Molecular Characterization of Anti-Topoisomerase I Autoantibodies

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Autosomal dominant supravalvular aortic stenosis: localization to chromosome 7

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Targetting of the gene encoding fibrillin-1 recapitulates the vascular aspect of Marfan syndrome.

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Pathogenetic sequence for aneurysm revealed in mice underexpressing fibrillin-1

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Cell adhesion and integrin binding to recombinant human fibrillin-1

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

The cutaneous microfibrillar apparatus contains latent transforming growth factor-beta binding protein-1 (LTBP-1) and is a repository for latent TGF-beta1

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Characterization of an in vitro model of elastic fiber assembly

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Elastogenic cells in the developing cardiovascular system. Smooth muscle, nonmuscle, and cardiac neural crest

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Characterization of mutated protein encoded by partially duplicated fibrillin-1 gene in tight skin (TSK) mice

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

A tandem duplication within the fibrillin 1 gene is associated with the mouse tight skin mutation

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Embryonic lineage of vascular smooth muscle cells determines responses to collagen matrices and integrin receptor expression.

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

Smooth muscle lineage diversity in the chick embryo. Two types of aortic smooth muscle cell differ in growth and receptor-mediated transcriptional responses to transforming growth factor-beta.

1 reference

https://api.crossref.org/works/10.1016%2FS0945-053X%2800%2900101-3

7 January 2021

10.1016/S0945-053X(00)00101-3

Identifiers

DOI

1 reference

30 July 2017

1 reference

PubMed ID

11068202