(Q34202007)

31 July 2017

1 reference

title

Pathogenesis of prion diseases: a progress report (English)

1 reference

31 July 2017

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Aguzzi A

1

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PubMed ID

11279534

31 July 2017

Heppner FL

series ordinal

2

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31 July 2017

1 October 2000

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Cell Death & Differentiation

31 July 2017

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31 July 2017

7

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31 July 2017

10

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31 July 2017

889-902

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https://scigraph.springernature.com/pub.10.1038/sj.cdd.4400737

31 July 2017

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cites work

Novel proteinaceous infectious particles cause scrapie

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Scrapie and cellular PrP isoforms are encoded by the same chromosomal gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Identification of scrapie prion protein-specific mRNA in scrapie-infected and uninfected brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Mice devoid of PrP are resistant to scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

No propagation of prions in mice devoid of PrP.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

21 January 2018

Between cows and monkeys

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Self-replication and scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Experimental transmission of a Kuru-like syndrome to chimpanzees

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Creutzfeldt-Jakob Disease (Spongiform Encephalopathy): Transmission to the Chimpanzee

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Creutzfeldt-Jakob Disease: Focus among Libyan Jews in Israel

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Mutation of the prion protein in Libyan Jews with Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Bovine spongiform encephalopathy and early onset variant Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Interactions between wild-type and mutant prion proteins modulate neurodegeneration in transgenic mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

A single amino acid alteration (101L) introduced into murine PrP dramatically alters incubation time of transmissible spongiform encephalopathy

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

NMR structure of the mouse prion protein domain PrP(121-231)

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

NMR characterization of the full-length recombinant murine prion protein, mPrP(23-231).

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Recombinant full-length murine prion protein, mPrP(23-231): purification and spectroscopic characterization.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Prion protein NMR structure and familial human spongiform encephalopathies

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Seeding "one-dimensional crystallization" of amyloid: a pathogenic mechanism in Alzheimer's disease and scrapie?

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Species specificity in the cell-free conversion of prion protein to protease-resistant forms: a model for the scrapie species barrier

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Partial unfolding and refolding of scrapie-associated prion protein: evidence for a critical 16-kDa C-terminal domain.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Non-genetic propagation of strain-specific properties of scrapie prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

In situ formation of protease-resistant prion protein in transmissible spongiform encephalopathy-infected brain slices.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Selective neuronal targeting in prion disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

PrPc glycoform heterogeneity as a function of brain region: implications for selective targeting of neurons by prion strains

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Developmental expression of the prion protein gene in glial cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Cellular isoform of the scrapie agent protein participates in lymphocyte activation

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Immunologic and molecular biologic studies of prion proteins in bovine spongiform encephalopathy

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Prion protein selectively binds copper(II) ions

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Nearly ubiquitous tissue distribution of the scrapie agent precursor protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Identification of candidate proteins binding to prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

The human 37-kDa laminin receptor precursor interacts with the prion protein in eukaryotic cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Complementary hydropathy identifies a cellular prion protein receptor

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Complete genomic sequence and analysis of the prion protein gene region from three mammalian species.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Structure and polymorphism of the mouse prion protein gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Loss of cerebellar Purkinje cells in aged mice homozygous for a disrupted PrP gene.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Ataxia in prion protein (PrP)-deficient mice is associated with upregulation of the novel PrP-like protein doppel

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Expression of amino-terminally truncated PrP in the mouse leading to ataxia and specific cerebellar lesions.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

NEUROBIOLOGY:PrP's Double Causes Trouble

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Spongiform encephalopathies. Breech-birth prions

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Analysis of interaction sites in homo- and heteromeric complexes containing Bcl-2 family members and the cellular prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Cloning the chromosomal breakpoint of t(14;18) human lymphomas: clustering around JH on chromosome 14 and near a transcriptional unit on 18.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Prions prevent neuronal cell-line death.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Transgenic mice expressing hamster prion protein produce species-specific scrapie infectivity and amyloid plaques.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Transgenetic studies implicate interactions between homologous PrP isoforms in scrapie prion replication.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Eight prion strains have PrP(Sc) molecules with different conformations

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Identification of a gene which controls the incubation period of some strains of scrapie agent in mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Linkage of the scrapie-associated fibril protein (PrP) gene and Sinc using congenic mice and restriction fragment length polymorphism analysis

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Neuropathological findings in cattle with clinically suspect but histologically unconfirmed bovine spongiform encephalopathy (BSE).

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

The spectrum of transmissible spongiform encephalopathies

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

From slow virus to prion: a review of transmissible spongiform encephalopathies

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Diagnosis of Creutzfeldt-Jakob disease and related human spongiform encephalopathies

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

A new variant of Creutzfeldt-Jakob disease in the UK.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Sträussler-Scheinker's syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Sleepless in Bologna: transmission of fatal familial insomnia

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Is the neuropathology of new variant Creutzfeldt-Jakob disease and kuru similar?

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Transmissible spongiform encephalopathies in humans.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

A transmembrane form of the prion protein in neurodegenerative disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Transmissible and genetic prion diseases share a common pathway of neurodegeneration

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Normal host prion protein (PrPC) is required for scrapie spread within the central nervous system

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

PrP-expressing tissue required for transfer of scrapie infectivity from spleen to brain.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Impaired prion replication in spleens of mice lacking functional follicular dendritic cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Sequential appearance and accumulation of pathognomonic markers in the central nervous system of hamsters orally infected with scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Scrapie-associated prion protein accumulates in astrocytes during scrapie infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

MRI assessment of the blood-brain barrier in a hamster model of scrapie.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Astrocyte-specific expression of hamster prion protein (PrP) renders PrP knockout mice susceptible to hamster scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Microglia: a sensor for pathological events in the CNS

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Role of microglia and host prion protein in neurotoxicity of a prion protein fragment.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Inhibition of protease-resistant prion protein formation by porphyrins and phthalocyanines

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Porphyrin and phthalocyanine antiscrapie compounds.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

[URE3] as an altered URE2 protein: evidence for a prion analog in Saccharomyces cerevisiae

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

De novo generation of a PrPSc-like conformation in living cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

The same prion strain causes vCJD and BSE

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

21 January 2018

A suspicious signature

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

Diagnosis of new variant Creutzfeldt-Jakob disease by tonsil biopsy

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

PrP expression in B lymphocytes is not required for prion neuroinvasion

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

BSE and prions: uncertainties about the agent

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Insertion in prion protein gene in familial Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Diagnosis of Gerstmann-Sträussler syndrome in familial dementia with prion protein gene analysis

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

The cellular prion protein (PrP) selectively binds to Bcl-2 in the yeast two-hybrid system

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Linkage of prion protein and scrapie incubation time genes

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Prion protein mutation in family first reported by Gerstmann, Sträussler, and Scheinker

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Creutzfeldt-Jakob disease after administration of human growth hormone

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

The role of the spleen in the neuroinvasion of scrapie in mice

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

A crucial role for B cells in neuroinvasive scrapie.

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Abnormal isoform of prion protein accumulates in follicular dendritic cells in mice with Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Pathogenesis of Mouse Scrapie: Evidence for Spread of Infection from Central to Peripheral Nervous System

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Increased blood-brain barrier permeability in scrapie-infected mice.

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Prophylactic potential of pentosan polysulphate in transmissible spongiform encephalopathies

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Reversion of prion protein conformational changes by synthetic b-sheet breaker peptides

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Rnq1: an epigenetic modifier of protein function in yeast

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Creating a protein-based element of inheritance

1 reference

https://api.crossref.org/works/10.1038%2FSJ.CDD.4400737

7 January 2021

Identifiers

DOI

10.1038/SJ.CDD.4400737

1 reference

31 July 2017

1 reference

PubMed ID

11279534