(Q34220144)

31 July 2017

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title

Transgenic mouse model for familial amyotrophic lateral sclerosis with superoxide dismutase-1 mutation (English)

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amyotrophic lateral sclerosis

31 July 2017

main subject

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author name string

N Shibata

series ordinal

1

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31 July 2017

publication date

1 March 2001

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31 July 2017

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31 July 2017

volume

21

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31 July 2017

issue

1

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31 July 2017

page(s)

82-92

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Superoxide dismutase-1 mutation-related neurotoxicity in familial amyotrophic lateral sclerosis

31 July 2017

cites work

1 reference

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An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

21 January 2018

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ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

21 January 2018

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Transgenic mice expressing an altered murine superoxide dismutase gene provide an animal model of amyotrophic lateral sclerosis

21 January 2018

1 reference

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Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

21 January 2018

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Neuropathological changes in two lines of mice carrying a transgene for mutant human Cu,Zn SOD, and in mice overexpressing wild type human SOD: a model of familial amyotrophic lateral sclerosis (FALS).

21 January 2018

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The Golgi apparatus of spinal cord motor neurons in transgenic mice expressing mutant Cu,Zn superoxide dismutase becomes fragmented in early, preclinical stages of the disease

21 January 2018

1 reference

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Familial amyotrophic lateral sclerosis with widespread vacuolation and hyaline inclusions.

21 January 2018

1 reference

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Enhanced oxygen radical production in a transgenic mouse model of familial amyotrophic lateral sclerosis.

21 January 2018

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Benefit of vitamin E, riluzole, and gabapentin in a transgenic model of familial amyotrophic lateral sclerosis

21 January 2018

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Neuroprotective effects of creatine in a transgenic animal model of amyotrophic lateral sclerosis.

21 January 2018

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Therapeutic benefits of putrescine-modified catalase in a transgenic mouse model of familial amyotrophic lateral sclerosis

21 January 2018

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Elevated free nitrotyrosine levels, but not protein-bound nitrotyrosine or hydroxyl radicals, throughout amyotrophic lateral sclerosis (ALS)-like disease implicate tyrosine nitration as an aberrant in vivo property of one familial ALS-linked superox

21 January 2018

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Nonoxidative protein glycation is implicated in familial amyotrophic lateral sclerosis with superoxide dismutase-1 mutation

21 January 2018

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Increased 3-nitrotyrosine and oxidative damage in mice with a human copper/zinc superoxide dismutase mutation.

21 January 2018

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Nitration of the low molecular weight neurofilament is equivalent in sporadic amyotrophic lateral sclerosis and control cervical spinal cord

21 January 2018

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Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by a familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant

21 January 2018

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Selective loss of glial glutamate transporter GLT‐1 in amyotrophic lateral sclerosis

21 January 2018

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Knockout of glutamate transporters reveals a major role for astroglial transport in excitotoxicity and clearance of glutamate

21 January 2018

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Intracellular calcium parallels motoneuron degeneration in SOD-1 mutant mice.

21 January 2018

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Protective effect of neurofilament heavy gene overexpression in motor neuron disease induced by mutant superoxide dismutase

21 January 2018

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Parvalbumin and calbindin D-28k in the human motor system and in motor neuron disease.

21 January 2018

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Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

21 January 2018

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Formation of granular cytoplasmic aggregates in COS7 cells expressing mutant Cu/Zn superoxide dismutase associated with familial amyotrophic lateral sclerosis.

21 January 2018

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Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis

21 January 2018

1 reference

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Intense superoxide dismutase-1 immunoreactivity in intracytoplasmic hyaline inclusions of familial amyotrophic lateral sclerosis with posterior column involvement.

21 January 2018

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Inhibition of ICE slows ALS in mice

21 January 2018

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10.1046/J.1440-1789.2001.00361.X

21 January 2018

Identifiers

DOI

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31 July 2017

1 reference