(Q34234577)

31 July 2017

Galactocerebrosidase-deficient oligodendrocytes maintain stable central myelin by exogenous replacement of the missing enzyme in mice (English)

1 reference

31 July 2017

1 reference

Yoichi Kondo

1

1 reference

31 July 2017

David A Wenger

series ordinal

2

1 reference

31 July 2017

Vittorio Gallo

series ordinal

3

1 reference

31 July 2017

Ian D Duncan

series ordinal

4

1 reference

31 July 2017

language of work or name

English

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publication date

13 December 2005

1 reference

31 July 2017

6

1 reference

Proceedings of the National Academy of Sciences of the United States of America

inferred from page(s)

published in

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31 July 2017

102

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31 July 2017

18670-18675

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31 July 2017

51

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Overcoming the blood-brain barrier with high-dose enzyme replacement therapy in murine mucopolysaccharidosis VII.

31 July 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Enzyme replacement therapy results in substantial improvements in early clinical phenotype in a mouse model of globoid cell leukodystrophy

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Transplantation of umbilical-cord blood in babies with infantile Krabbe's disease

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Immunohistochemical distribution of cation-dependent mannose 6-phosphate receptors in the mouse central nervous system: comparison with that of cation-independent mannose 6-phophate receptors

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Enzyme replacement and enhancement therapies for lysosomal diseases

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Insulin-like growth factor-II/Mannose-6-phosphate receptor in the spinal cord and dorsal root ganglia of the adult rat.

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Retrovirus-mediated gene transfer and galactocerebrosidase uptake into twitcher glial cells results in appropriate localization and phenotype correction

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Molecular cloning and expression of cDNA for murine galactocerebrosidase and mutation analysis of the twitcher mouse, a model of Krabbe's disease

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

The twitcher mouse: a model for Krabbe disease and for experimental therapies

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

The future for treatment by bone marrow transplantation for adrenoleukodystrophy, metachromatic leukodystrophy, globoid cell leukodystrophy and Hurler syndrome

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Globoid cell leucodystrophy (Krabbe's disease): deficiency of galactocerebroside beta-galactosidase

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

The twitcher mouse: accumulation of galactosylsphingosine and pathology of the sciatic nerve.

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Chromosomal mapping of mouse myelin basic protein gene and structure and transcription of the partially deleted gene in shiverer mutant mice.

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Structure and function of the mannose 6-phosphate/insulinlike growth factor II receptors

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

Fetal and adult human oligodendrocyte progenitor cell isolates myelinate the congenitally dysmyelinated brain

28 July 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Towards the reconstruction of central nervous system white matter using neural precursor cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Expression of the green fluorescent protein in the oligodendrocyte lineage: a transgenic mouse for developmental and physiological studies.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Apoptotic positive cells in Krabbe brain and induction of apoptosis in rat C6 glial cells by psychosine

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

An apoptotic depletion of oligodendrocytes in the twitcher, a murine model of globoid cell leukodystrophy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Increased NG2(+) glial cell proliferation and oligodendrocyte generation in the hypomyelinating mutant shiverer

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Effects of implantation site of dead stem cells in rats with stroke damage

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Improved myelination in nerve grafts from the leucodystrophic twitcher into trembler mice: evidence for enzyme replacement.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Hematopoietic cell transplantation ameliorates clinical phenotype and progression of the CNS pathology in the mouse model of late onset Krabbe disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

The twitcher mouse: normal pattern of early myelination in the spinal cord.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Localization of receptors for endocytosis of lysosomal enzymes on different brain cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

AAV-mediated expression of galactocerebrosidase in brain results in attenuated symptoms and extended life span in murine models of globoid cell leukodystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Developmentally regulated mannose 6-phosphate receptor-mediated transport of a lysosomal enzyme across the blood-brain barrier

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Migration activity of microglia and macrophages into rat brain.

21 January 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

STUDIES IN GLOBOID (KRABBE) LEUKODYSTROPHY. 3. SIGNIFICANCE OF EXPERIMENTALLY-PRODUCED GLOBOID-LIKE ELEMENTS IN RAT WHITE MATTER AND SPLEEN

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1317926

The murine mutation osteopetrosis is in the coding region of the macrophage colony stimulating factor gene

28 October 2018

1 reference

https://api.crossref.org/works/10.1073%2FPNAS.0506473102

Hematopoietic stem-cell transplantation in globoid-cell leukodystrophy

21 January 2018

1 reference

12 December 2020

Enzyme replacement in Tay-Sachs disease

1 reference

12 December 2020

Hereditary leucodystrophy in the mouse: the new mutant twitcher

1 reference

12 December 2020

The Twitcher mouse: an enzymatically authentic model of human globoid cell leukodystrophy (Krabbe disease)

1 reference

12 December 2020

Direct transfer of a lysosomal enzyme from lymphoid cells to deficient fibroblasts

1 reference

12 December 2020

Enzyme replacement in grafted nerve of twitcher mouse

1 reference

12 December 2020

Direct enzyme transfer from lymphocytes is specific

1 reference

12 December 2020

Proliferative capacity of oligodendrocytes in the demyelinating twitcher spinal cord

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.0506473102

1 reference

31 July 2017

0 references

1 reference

31 July 2017

1 reference