(Q34304294)

1 August 2017

The Z type variation of human alpha 1-antitrypsin causes a protein folding defect (English)

1 reference

1 August 2017

0 references

Yu MH

1

1 reference

PubMed ID

7664092

1 August 2017

Lee KN

series ordinal

2

1 reference

PubMed ID

7664092

1 August 2017

Kim J

series ordinal

3

1 reference

1 August 2017

1 May 1995

1 reference

Nature structural biology

1 August 2017

1 reference

1 August 2017

2

1 reference

1 August 2017

363-367

1 reference

1 August 2017

5

1 reference

The alpha 1-antitrypsin gene and its deficiency states

1 August 2017

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

The mechanism of Z alpha 1-antitrypsin accumulation in the liver

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Association of folding intermediates of glycoproteins with calnexin during protein maturation

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Altered protein folding may be the molecular basis of most cases of cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Cell-free formation of protease-resistant prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Mobile reactive centre of serpins and the control of thrombosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Implications of the three-dimensional structure of alpha 1-antitrypsin for structure and function of serpins

21 January 2018

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Human alpha 1-proteinase inhibitor. Crystal structure analysis of two crystal modifications, molecular model and preliminary analysis of the implications for function

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

What do dysfunctional serpins tell us about molecular mobility and disease?

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Effect of the Z mutation on the physical and inhibitory properties of alpha 1-antitrypsin

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Electrophoretic analysis of the unfolding of proteins by urea

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Kinetic study of protein unfolding and refolding using urea gradient electrophoresis

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Single amino acid mutations block a late step in the folding of beta-lactamase from Staphylococcus aureus

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Structural and functional characterization of the abnormal Z alpha 1-antitrypsin isolated from human liver

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Z-type alpha 1-antitrypsin is less competent than M1-type alpha 1-antitrypsin as an inhibitor of neutrophil elastase

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Biological implications of a 3 A structure of dimeric antithrombin

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

The intact and cleaved human antithrombin III complex as a model for serpin-proteinase interactions

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Role of N-linked oligosaccharide recognition, glucose trimming, and calnexin in glycoprotein folding and quality control

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

A lag in intracellular degradation of mutant alpha 1-antitrypsin correlates with the liver disease phenotype in homozygous PiZZ alpha 1-antitrypsin deficiency

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Effects of the delta F508 mutation on the structure, function, and folding of the first nucleotide-binding domain of CFTR.

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Structural clues to prion replication

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Rapid and efficient site-specific mutagenesis without phenotypic selection

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

Spectroscopic Determination of Tryptophan and Tyrosine in Proteins*

31 March 2020

1 reference

https://api.crossref.org/works/10.1038%2FNSB0595-363

31 March 2020

Identifiers

DOI

10.1038/NSB0595-363

1 reference

1 August 2017

1 reference

PubMed ID

7664092