(Q34415166)

2 August 2017

title

Doxycycline attenuates and delays toxicity of the oculopharyngeal muscular dystrophy mutation in transgenic mice (English)

1 reference

oculopharyngeal muscular dystrophy

2 August 2017

0 references

1 reference

1 reference

Janet E Davies

1

1 reference

2 August 2017

Lin Wang

2

1 reference

2 August 2017

Lourdes Garcia-Oroz

3

1 reference

2 August 2017

Lynnette J Cook

4

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2 August 2017

Coralie Vacher

5

1 reference

2 August 2017

Dominic G O'Donovan

6

1 reference

2 August 2017

David C Rubinsztein

7

1 reference

2 August 2017

language of work or name

English

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publication date

1 May 2005

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2 August 2017

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2 August 2017

volume

11

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2 August 2017

issue

6

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2 August 2017

page(s)

672-677

1 reference

https://scigraph.springernature.com/pub.10.1038/nm1242

2 August 2017

exact match

0 references

cites work

Short GCG expansions in the PABP2 gene cause oculopharyngeal muscular dystrophy

1 reference

Nuclear inclusions in oculopharyngeal muscular dystrophy consist of poly(A) binding protein 2 aggregates which sequester poly(A) RNA

21 January 2018

1 reference

A molecular pathogenesis for transcription factor associated poly-alanine tract expansions

21 January 2018

1 reference

Involvement of the ubiquitin-proteasome pathway and molecular chaperones in oculopharyngeal muscular dystrophy

21 January 2018

1 reference

Mammalian, yeast, bacterial, and chemical chaperones reduce aggregate formation and death in a cell model of oculopharyngeal muscular dystrophy

21 January 2018

1 reference

Congo red, doxycycline, and HSP70 overexpression reduce aggregate formation and cell death in cell models of oculopharyngeal muscular dystrophy

21 January 2018

1 reference

Anti-amyloidogenic activity of tetracyclines: studies in vitro.

21 January 2018

1 reference

Epidermal immunization by a needle-free powder delivery technology: Immunogenicity of influenza vaccine and protection in mice

21 January 2018

1 reference

Minocycline inhibits caspase-independent and -dependent mitochondrial cell death pathways in models of Huntington's disease

21 January 2018

1 reference

Myopathy phenotype in transgenic mice expressing mutated PABPN1 as a model of oculopharyngeal muscular dystrophy.

21 January 2018

1 reference

Oligomerization of polyalanine expanded PABPN1 facilitates nuclear protein aggregation that is associated with cell death

21 January 2018

1 reference

Heat shock protein 27 prevents cellular polyglutamine toxicity and suppresses the increase of reactive oxygen species caused by huntingtin

21 January 2018

1 reference

Minocycline inhibits cytochrome c release and delays progression of amyotrophic lateral sclerosis in mice

21 January 2018

1 reference

Inhibition of apoptosis improves outcome in a model of congenital muscular dystrophy

21 January 2018

1 reference

Minocycline and doxycycline are not beneficial in a model of Huntington's disease

21 January 2018

1 reference

Isolation of genomic and cDNA clones encoding bovine poly(A) binding protein II.

21 January 2018

1 reference

Behavioral and functional analysis of mouse phenotype: SHIRPA, a proposed protocol for comprehensive phenotype assessment

21 January 2018

1 reference

Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene

21 January 2018

1 reference

Morphological changes in muscle fibers in oculopharyngeal muscular dystrophy

21 January 2018

1 reference

inferred from DOI database lookup

7 January 2021

based on heuristic

Nuclear accumulation of expanded PABP2 gene product in oculopharyngeal muscular dystrophy

1 reference

inferred from DOI database lookup

7 January 2021

based on heuristic

Identifiers

DOI

10.1038/NM1242

1 reference

2 August 2017

1 reference