(Q34699604)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

title

Pyruvate dehydrogenase complex deficiency caused by ubiquitination and proteasome-mediated degradation of the E1 subunit (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

main subject

protein ubiquitination

1 reference

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

author name string

Li Zhong

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

Arun Srivastava

series ordinal

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

Peter W Stacpoole

series ordinal

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

language of work or name

English

0 references

publication date

8 October 2007

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

Journal of Biological Chemistry

8 January 2020

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

volume

283

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

issue

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

8 January 2020

page(s)

237-243

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17923481%20AND%20SRC:MED&resulttype=core&format=json

Clinical and genetic spectrum of pyruvate dehydrogenase deficiency: dihydrolipoamide acetyltransferase (E2) deficiency

8 January 2020

cites work

1 reference

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Pyruvate dehydrogenase phosphatase deficiency: identification of the first mutation in two brothers and restoration of activity by protein complementation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Pyruvate dehydrogenase E3 binding protein (protein X) deficiency

21 January 2018

1 reference

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Down-regulation of expression of rat pyruvate dehydrogenase E1alpha gene by self-complementary adeno-associated virus-mediated small interfering RNA delivery

21 January 2018

1 reference

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Endosomal localization and receptor dynamics determine tyrosine phosphorylation of hepatocyte growth factor-regulated tyrosine kinase substrate

21 January 2018

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Narrative review: protein degradation and human diseases: the ubiquitin connection

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Ubiquitin-binding proteins: similar, but different.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Strength in numbers: preventing rereplication via multiple mechanisms in eukaryotic cells

21 January 2018

1 reference

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Tyrphostins I: synthesis and biological activity of protein tyrosine kinase inhibitors

21 January 2018

1 reference

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A novel RING-type ubiquitin ligase breast cancer-associated gene 2 correlates with outcome in invasive breast cancer

21 January 2018

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Blocking of EGF-dependent cell proliferation by EGF receptor kinase inhibitors

21 January 2018

1 reference

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The proteasome inhibitor MG132 protects against acute pancreatitis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Back to the future with ubiquitin

21 January 2018

1 reference

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Proteasome inhibition enhances AAV-mediated transgene expression in human synoviocytes in vitro and in vivo.

21 January 2018

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Rapid degradation of Bim by the ubiquitin-proteasome pathway mediates short-term ischemic tolerance in cultured neurons

21 January 2018

1 reference

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Rapid turnover of GATA-2 via ubiquitin-proteasome protein degradation pathway

21 January 2018

1 reference

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Protein-tyrosine phosphatases and cancer

21 January 2018

1 reference

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Acquisition of inhibitor-sensitive protein kinases through protein design

21 January 2018

1 reference

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A dual role of EGFR protein tyrosine kinase signaling in ubiquitination of AAV2 capsids and viral second-strand DNA synthesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Gene silencing: trans-histone regulatory pathway in chromatin

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Protein tyrosine kinase-substrate interactions

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Role of ubiquitination in IGF-1 receptor signaling and degradation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Demonstration of an unstable variant of pyruvate dehydrogenase protein (E1) in cultured fibroblasts from a patient with congenital lactic acidemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Dichloroacetate stabilizes the mutant E1alpha subunit in pyruvate dehydrogenase deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200

Differential effect of DCA treatment on the pyruvate dehydrogenase complex in patients with severe PDHC deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M704748200