(Q34856408)

4 August 2017

1 reference

title

Cytopathies involving mitochondrial complex II. (English)

1 reference

4 August 2017

Brian A C Ackrell

1

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4 August 2017

publication date

1 October 2002

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Molecular Aspects of Medicine

4 August 2017

published in

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4 August 2017

volume

23

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4 August 2017

issue

5

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4 August 2017

page(s)

369-384

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Progress in understanding structure-function relationships in respiratory chain complex II.

4 August 2017

cites work

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Genetics and molecular biology of Huntington's disease

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7 January 2021

Gene mutations in the succinate dehydrogenase subunit SDHB cause susceptibility to familial pheochromocytoma and to familial paraganglioma

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7 January 2021

Germline SDHD mutation in familial phaeochromocytoma

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7 January 2021

Promoter analysis of the human succinate dehydrogenase iron-protein gene--both nuclear respiratory factors NRF-1 and NRF-2 are required

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7 January 2021

Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin

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7 January 2021

Novel mutations in the SDHD gene in pedigrees with familial carotid body paraganglioma and sensorineural hearing loss

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7 January 2021

Mutations in SDHD, a mitochondrial complex II gene, in hereditary paraganglioma

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7 January 2021

Phenotypic dichotomy in mitochondrial complex II genetic disorders.

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7 January 2021

Neurochemical and histologic characterization of striatal excitotoxic lesions produced by the mitochondrial toxin 3-nitropropionic acid

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7 January 2021

Late-onset optic atrophy, ataxia, and myopathy associated with a mutation of a complex II gene

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7 January 2021

Mutation of a nuclear succinate dehydrogenase gene results in mitochondrial respiratory chain deficiency

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7 January 2021

Clinical, biochemical and molecular genetic correlations in Friedreich's ataxia

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7 January 2021

Partial inhibition of brain succinate dehydrogenase by 3-nitropropionic acid is sufficient to initiate striatal degeneration in rat.

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7 January 2021

Oxidative damage and metabolic dysfunction in Huntington's disease: selective vulnerability of the basal ganglia.

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7 January 2021

Inhibition of mitochondrial complex II induces a long-term potentiation of NMDA-mediated synaptic excitation in the striatum requiring endogenous dopamine.

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7 January 2021

Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

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7 January 2021

Mitochondrial reactive oxygen species trigger hypoxia-induced transcription

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7 January 2021

Reactive oxygen species generated at mitochondrial complex III stabilize hypoxia-inducible factor-1alpha during hypoxia: a mechanism of O2 sensing

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7 January 2021

Disabled early recruitment of antioxidant defenses in Friedreich's ataxia

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7 January 2021

CCC1 suppresses mitochondrial damage in the yeast model of Friedreich's ataxia by limiting mitochondrial iron accumulation

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7 January 2021

Characterization of the iron-sulfur centers in succinate dehydrogenase

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7 January 2021

Inactivation of the Friedreich ataxia mouse gene leads to early embryonic lethality without iron accumulation

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7 January 2021

Multiple defects of the respiratory chain including complex II in a family with myopathy and encephalopathy

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https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Rapid suppression of free radical formation by nerve growth factor involves the mitogen-activated protein kinase pathway

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https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Low iron concentration and aconitase deficiency in a yeast frataxin homologue deficient strain

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

The R22X mutation of the SDHD gene in hereditary paraganglioma abolishes the enzymatic activity of complex II in the mitochondrial respiratory chain and activates the hypoxia pathway

1 reference

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7 January 2021

Inhibition of succinate dehydrogenase by malonic acid produces an "excitotoxic" lesion in rat striatum

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7 January 2021

Mitochondrial defect in Huntington's disease caudate nucleus

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7 January 2021

Succinate: quinone oxidoreductases. Variations on a conserved theme

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

A structural model for the membrane-integral domain of succinate: quinone oxidoreductases.

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Transmembrane topology and axial ligands to hemes in the cytochrome b subunit of Bacillus subtilis succinate:menaquinone reductase.

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

An Escherichia coli mutant quinol:fumarate reductase contains an EPR-detectable semiquinone stabilized at the proximal quinone-binding site

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Mitochondrial myopathy with succinate dehydrogenase and aconitase deficiency. Abnormalities of several iron-sulfur proteins

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Biosynthesis and membrane binding of succinate dehydrogenase in Bacillus subtilis

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Cytochrome b in human complex II (succinate-ubiquinone oxidoreductase): cDNA cloning of the components in liver mitochondria and chromosome assignment of the genes for the large (SDHC) and small (SDHD) subunits to 1q21 and 11q23

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

The phylogenetic distribution of frataxin indicates a role in iron-sulfur cluster protein assembly

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

HIFalpha targeted for VHL-mediated destruction by proline hydroxylation: implications for O2 sensing

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7 January 2021

Structure of the Escherichia coli fumarate reductase respiratory complex

1 reference

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7 January 2021

Evidence for impairment of energy metabolism in vivo in Huntington's disease using localized 1H NMR spectroscopy

1 reference

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7 January 2021

The mitochondrial proteins Atm1p and Nfs1p are essential for biogenesis of cytosolic Fe/S proteins

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

IscA, an alternate scaffold for Fe-S cluster biosynthesis

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Structure of fumarate reductase from Wolinella succinogenes at 2.2 A resolution

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

A mitochondrial ferredoxin is essential for biogenesis of cellular iron-sulfur proteins

1 reference

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7 January 2021

The gene for the iron sulfur protein of succinate dehydrogenase (SDH-IP) maps to human chromosome 1p35-36.1.

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Structural and mechanistic mapping of a unique fumarate reductase

1 reference

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7 January 2021

Yeast mitochondrial protein, Nfs1p, coordinately regulates iron-sulfur cluster proteins, cellular iron uptake, and iron distribution

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Regulation of the 75-kDa subunit of mitochondrial complex I by iron

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Antioxidant treatment improves in vivo cardiac and skeletal muscle bioenergetics in patients with Friedreich's ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Effects of dietary iron deficiency of iron-sulfur proteins and bioenergetic functions of skeletal muscle mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Retention of heme in axial ligand mutants of succinate-ubiquinone xxidoreductase (complex II) from Escherichia coli

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Structure of L-aspartate oxidase: implications for the succinate dehydrogenase/fumarate reductase oxidoreductase family

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Biogenesis of iron-sulfur proteins in eukaryotes: a novel task of mitochondria that is inherited from bacteria

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Dominant isolated renal magnesium loss is caused by misrouting of the Na(+),K(+)-ATPase gamma-subunit

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Abortive assembly of succinate-ubiquinone reductase (complex II) in a ferrochelatase-deficient mutant of Escherichia coli

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Iron-sulfur cluster assembly: characterization of IscA and evidence for a specific and functional complex with ferredoxin

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Ataxia with isolated vitamin E deficiency is caused by mutations in the alpha-tocopherol transfer protein

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

The Quinone-binding sites of the Saccharomyces cerevisiae succinate-ubiquinone oxidoreductase

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Compound heterozygous mutations in the flavoprotein gene of the respiratory chain complex II in a patient with Leigh syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Brain-derived neurotrophic factor inhibits apoptosis and dopamine-induced free radical production in striatal neurons but does not prevent cell death

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

The yeast frataxin homologue mediates mitochondrial iron efflux. Evidence for a mitochondrial iron cycle

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Single muscle fibre analyses in 2 brothers with succinate dehydrogenase deficiency.

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Kearns-Sayre syndrome and complex II deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

The investigation of respiratory chain disorders in heart using endomyocardial biopsies

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Frataxin deficiency enhances apoptosis in cells differentiating into neuroectoderm

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Evidence for a conserved system for iron metabolism in the mitochondria of Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

The C-terminus of the succinate dehydrogenase IP peptide of Saccharomyces cerevisiae is significant for assembly of complex II

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

A defect in the cytochrome b large subunit in complex II causes both superoxide anion overproduction and abnormal energy metabolism in Caenorhabditis elegans

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Identification of quinone-binding and heme-ligating residues of the smallest membrane-anchoring subunit (QPs3) of bovine heart mitochondrial succinate:ubiquinone reductase.

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Frataxin expression rescues mitochondrial dysfunctions in FRDA cells

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Nearly all hereditary paragangliomas in the Netherlands are caused by two founder mutations in the SDHD gene

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Combinatorial mRNA regulation: iron regulatory proteins and iso-iron-responsive elements (Iso-IREs).

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Transfer of sulfur from IscS to IscU during Fe/S cluster assembly

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

On the possible interelations of the reactivity of soluble succinate dehydrogenase with ferricyanide, reconstitution activity, and the hipip iron sulfur center

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Jac1, a mitochondrial J-type chaperone, is involved in the biogenesis of Fe/S clusters in Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Resolution and reconstitution of succinate-ubiquinone reductase from Escherichia coli.

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

NifS-directed assembly of a transient [2Fe-2S] cluster within the NifU protein

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

Cysteine desulfurase activity indicates a role for NIFS in metallocluster biosynthesis

1 reference

https://api.crossref.org/works/10.1016%2FS0098-2997%2802%2900012-2

7 January 2021

10.1016/S0098-2997(02)00012-2

Identifiers

DOI

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4 August 2017

1 reference