(Q34987828)

5 August 2017

title

Rescue of functional CFTR channels in cystic fibrosis: a dramatic multivalent effect using iminosugar cluster-based correctors (English)

1 reference

5 August 2017

0 references

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Frédéric Becq

10

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

author name string

Philippe Compain

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Camille Decroocq

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Julien de Sousa

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

David Rodríguez-Lucena

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Terry D Butters

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Johanna Bertrand

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Romain Clément

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Clément Boinot

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

Caroline Norez

11

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

publication date

13 September 2013

1 reference

5 August 2017

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

volume

14

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

13 June 2020

issue

15

1 reference

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13 June 2020

page(s)

2050-2058

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24038832%20AND%20SRC:MED&resulttype=core&format=json

Treatment of cystic fibrosis in the adult

13 June 2020

cites work

1 reference

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Comparison of the clinical manifestations of cystic fibrosis in black and white patients

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Phosphorylation-regulated CI− channel in CHO cells stably expressing the cystic fibrosis gene

21 January 2018

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Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

21 January 2018

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21 January 2018

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Rescue of functional delF508-CFTR channels in cystic fibrosis epithelial cells by the alpha-glucosidase inhibitor miglustat

21 January 2018

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Discovery of pyrrolo[2,3-b]pyrazines derivatives as submicromolar affinity activators of wild type, G551D, and F508del cystic fibrosis transmembrane conductance regulator chloride channels

21 January 2018

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A cystic fibrosis respiratory epithelial cell chronically treated by miglustat acquires a non-cystic fibrosis-like phenotype

21 January 2018

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Novel oral treatment of Gaucher's disease with N-butyldeoxynojirimycin (OGT 918) to decrease substrate biosynthesis.

21 January 2018

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Sustained therapeutic effects of oral miglustat (Zavesca, N-butyldeoxynojirimycin, OGT 918) in type I Gaucher disease.

21 January 2018

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A randomized placebo-controlled trial of miglustat in cystic fibrosis based on nasal potential difference

21 January 2018

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Selection of the biological activity of DNJ neoglycoconjugates through click length variation of the side chain

21 January 2018

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4-C-Me-DAB and 4-C-Me-LAB - enantiomeric alkyl-branched pyrrolidine iminosugars - are specific and potent α-glucosidase inhibitors; acetone as the sole protecting group

21 January 2018

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Glycosidase inhibition with fullerene iminosugar balls: a dramatic multivalent effect.

21 January 2018

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Functional Rescue of F508del-CFTR Using Small Molecule Correctors

21 January 2018

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Small-molecule correctors of defective DeltaF508-CFTR cellular processing identified by high-throughput screening.

21 January 2018

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A stepwise huisgen cycloaddition process: copper(I)-catalyzed regioselective "ligation" of azides and terminal alkynes

21 January 2018

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21 January 2018

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Modular synthesis of multivalent glycoarchitectures and their unique selectin binding behavior

21 January 2018

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Determination of CFTR chloride channel activity and pharmacology using radiotracer flux methods.

21 January 2018

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21 January 2018

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A counterintuitive approach to treat enzyme deficiencies: use of enzyme inhibitors for restoring mutant enzyme activity

21 January 2018

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Proteasome-dependent pharmacological rescue of cystic fibrosis transmembrane conductance regulator revealed by mutation of glycine 622.

21 January 2018

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Post-translational disruption of the delta F508 cystic fibrosis transmembrane conductance regulator (CFTR)-molecular chaperone complex with geldanamycin stabilizes delta F508 CFTR in the rabbit reticulocyte lysate.

21 January 2018

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Endoplasmic reticulum stress in the absence of calnexin

21 January 2018

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Compounds that correct F508del-CFTR trafficking can also correct other protein trafficking diseases: an in vitro study using cell lines.

21 January 2018

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A cystic fibrosis tracheal gland cell line, CF-KM4. Correction by adenovirus-mediated CFTR gene transfer

21 January 2018

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21 January 2018

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