(Q35001649)

5 August 2017

1 reference

title

Chemical chaperones: a pharmacological strategy for disorders of protein folding and trafficking (English)

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5 August 2017

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David H Perlmutter

1

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5 August 2017

language of work or name

English

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publication date

1 December 2002

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5 August 2017

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5 August 2017

volume

52

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5 August 2017

issue

6

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5 August 2017

page(s)

832-836

1 reference

https://scigraph.springernature.com/pub.10.1203/00006450-200212000-00004

5 August 2017

exact match

0 references

cites work

Perturbations in maturation of secretory proteins and their association with endoplasmic reticulum chaperones in a cell culture model for epithelial ischemia

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Increased thermal stability of collagen in the presence of sugars and polyols

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Glycerol reverses the misfolding phenotype of the most common cystic fibrosis mutation.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Degradation of CFTR by the ubiquitin-proteasome pathway

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Chemical chaperones correct the mutant phenotype of the delta F508 cystic fibrosis transmembrane conductance regulator protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Correcting temperature-sensitive protein folding defects

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Defective aquaporin-2 trafficking in nephrogenic diabetes insipidus and correction by chemical chaperones

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Misfolding of mutant aquaporin-2 water channels in nephrogenic diabetes insipidus

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Chemical chaperones mediate increased secretion of mutant alpha 1-antitrypsin (alpha 1-AT) Z: A potential pharmacological strategy for prevention of liver injury and emphysema in alpha 1-AT deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Trimethylamine N-oxide-induced cooperative folding of an intrinsically unfolded transcription-activating fragment of human glucocorticoid receptor.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Manipulating the amyloid-beta aggregation pathway with chemical chaperones.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Chemical chaperones regulate molecular chaperones in vitro and in cells under combined salt and heat stresses

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Long-term treatment of girls with ornithine transcarbamylase deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Reactivation of silenced, virally transduced genes by inhibitors of histone deacetylase

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Pharmacological chaperones rescue cell-surface expression and function of misfolded V2 vasopressin receptor mutants

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Correction of defective protein trafficking of a mutant HERG potassium channel in human long QT syndrome. Pharmacological and temperature effects

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Recovering antibody secretion using a hapten ligand as a chemical chaperone.

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Improvement in cardiac function in the cardiac variant of Fabry's disease with galactose-infusion therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Galactose stabilizes various missense mutants of alpha-galactosidase in Fabry disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

Correction of Defective Protein Kinesis of Human P-glycoprotein Mutants by Substrates and Modulators

21 January 2018

1 reference

https://api.crossref.org/works/10.1203%2F00006450-200212000-00004

10.1203/00006450-200212000-00004

21 January 2018

Identifiers

DOI

1 reference

Dimensions Publication ID

5 August 2017

1033865272

0 references

Fatcat ID

release_dies2zersbbcxp7mkyvk3jpwpm

1 reference

Fatcat

https://api.fatcat.wiki/v0/release/dies2zersbbcxp7mkyvk3jpwpm

mapped directly with Wikidata item

24 November 2022

based on heuristic

1 reference