(Q35067305)

6 August 2017

title

Filipin recognizes both GM1 and cholesterol in GM1 gangliosidosis mouse brain (English)

1 reference

6 August 2017

3

1 reference

6 August 2017

Julian R Arthur

1

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6 August 2017

Karie A Heinecke

series ordinal

2

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6 August 2017

publication date

20 April 2011

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Journal of Lipid Research

6 August 2017

published in

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6 August 2017

volume

52

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6 August 2017

issue

7

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6 August 2017

page(s)

1345-1351

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describes a project that uses

6 August 2017

ImageQuant

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3122916/fullTextXML

inferred from PubMed Central ID database lookup

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Cyclodextrin overcomes deficient lysosome-to-endoplasmic reticulum transport of cholesterol in Niemann-Pick type C cells

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Chronic cyclodextrin treatment of murine Niemann-Pick C disease ameliorates neuronal cholesterol and glycosphingolipid storage and disease progression

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8 July 2018

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8 July 2018

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A comparative study of cytoplasmic granules imaged by the real-time microscope, Nile Red and Filipin in fibroblasts from patients with lipid storage diseases

8 July 2018

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8 July 2018

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8 July 2018

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Glycosphingolipid accumulation inhibits cholesterol efflux via the ABCA1/apolipoprotein A-I pathway: 1-phenyl-2-decanoylamino-3-morpholino-1-propanol is a novel cholesterol efflux accelerator

8 July 2018

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8 July 2018

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8 July 2018

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Accumulation of glycosphingolipids in Niemann-Pick C disease disrupts endosomal transport

8 July 2018

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Alterations in the permeability of Neurospora crassa due to polyene antibiotics

8 July 2018

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8 July 2018

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8 July 2018

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Accumulation of cholera toxin and GM1 ganglioside in the early endosome of Niemann-Pick C1-deficient cells

8 July 2018

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Filipin-dependent inhibition of cholera toxin: evidence for toxin internalization and activation through caveolae-like domains

8 July 2018

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8 July 2018

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Fluorometric evidence for the binding of cholesterol to the filipin complex

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Studies on the biological properties of polyene antibiotics. Evidence for the direct interaction of filipin with cholesterol

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Abnormalities of cerebral lipids in GM1-gangliosidoses, infantile, juvenile, and chronic type

8 July 2018

1 reference

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An electrophoretic variant of beta-galactosidase with altered catalytic properties in a patient with GM1 gangliosidosis

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Early Diagnosis and Prevention of Genetic Disease

8 July 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Complete correction of enzymatic deficiency and neurochemistry in the GM1-gangliosidosis mouse brain by neonatal adeno-associated virus-mediated gene delivery

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Substrate reduction reduces gangliosides in postnatal cerebrum-brainstem and cerebellum in GM1 gangliosidosis mice.

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Differential subcellular localization of cholesterol, gangliosides, and glycosaminoglycans in murine models of mucopolysaccharide storage disorders

27 September 2018

1 reference

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Inheritance of lysosomal acid beta-galactosidase activity and gangliosides in crosses of DBA/2J and knockout mice.

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Gargoylism; a mucopolysaccharidosis.

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Cholesterol accumulation in NPC1-deficient neurons is ganglioside dependent

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Sphingolipid storage induces accumulation of intracellular cholesterol by stimulating SREBP-1 cleavage

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Filipin III: Configuration Assignment and Confirmation by Synthetic Correlation

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Quantified increases of cholesterol, total lipid and globotriaosylceramide in filipin-positive Niemann-Pick type C fibroblasts

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Jamming the endosomal system: lipid rafts and lysosomal storage diseases.

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Cholesterol modulates membrane traffic along the endocytic pathway in sphingolipid-storage diseases

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Increased levels of GM2 ganglioside in fibroblasts from a patient with juvenile Niemann-Pick disease type C.

27 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3122916

Filipin, an Antifungal Antibiotic: Isolation and Properties

27 September 2018

1 reference

Crossref

https://api.crossref.org/works/10.1194%2FJLR.M012633

GM1-ganglioside-mediated activation of the unfolded protein response causes neuronal death in a neurodegenerative gangliosidosis

21 January 2018

1 reference

12 December 2020

Filipin as a cholesterol probe. I. Morphology of filipin-cholesterol interaction in lipid model systems

1 reference

12 December 2020

Filipin as a fluorescent probe of lipoprotein-derived sterols on thin-layer chromatograms

1 reference

12 December 2020

Distinct alterations in phospholipid metabolism in brains of apolipoprotein E-deficient mice

1 reference

12 December 2020

N-butyldeoxygalactonojirimycin reduces neonatal brain ganglioside content in a mouse model of GM1 gangliosidosis

1 reference

12 December 2020

1 reference

12 December 2020

Oxidation products of cholesteryl linoleate are resistant to hydrolysis in macrophages, form complexes with proteins, and are present in human atherosclerotic lesions

1 reference

12 December 2020

Generalized CNS disease and massive GM1-ganglioside accumulation in mice defective in lysosomal acid beta-galactosidase

1 reference

12 December 2020

Lipid Composition of Whole Brain and Cerebellum in Hurler Syndrome (MPS IH) Mice

1 reference

12 December 2020

Identifiers

DOI

10.1194/JLR.M012633

1 reference

6 August 2017

1 reference

6 August 2017

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