(Q35117567)

6 August 2017

title

Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups (English)

1 reference

6 August 2017

C R Roe

1

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6 August 2017

C L Hoppel

2

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6 August 2017

T E Stacey

3

1 reference

6 August 2017

R A Chalmers

4

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6 August 2017

B M Tracey

5

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6 August 2017

D S Millington

6

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6 August 2017

language of work or name

English

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publication date

1 November 1983

1 reference

Archives of Disease in Childhood

6 August 2017

published in

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6 August 2017

volume

58

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6 August 2017

issue

11

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6 August 2017

page(s)

916-920

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Treatment of inborn errors of urea synthesis: activation of alternative pathways of waste nitrogen synthesis and excretion

6 August 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Urinary excretion of acetylcarnitine during human diabetic and fasting ketosis

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Propionylcarnitine physiological variations in vivo

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Short-chain organic acidemia and Reye's syndrome

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

The synthesis of hippurate from benzoate and glycine by rat liver mitochondria. Submitochondrial localization and kinetics

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Identification of D-threo-alpha-methylisocitrate as stereochemically specific substrate for bovine heart aconitase and inhibitor of TPN-linked isocitrate dehydrogenase

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Carnitine metabolism in the fasting rat

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Effect of 2-Methylcitrate on Citrate Metabolism: Implications for the Management of Patients with Propionic acidemia and Methylmalonic aciduria

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Carnitine metabolism in normal-weight and obese human subjects during fasting

9 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1628370

Propionate inhibition of succinate:CoA ligase (GDP) and the citric acid cycle in mitochondria

27 September 2018

1 reference

12 December 2020

The specific inhibition of the pyruvate dehydrogenase complex from pig kidney by propionyl-CoA and isovaleryl-Co-A

1 reference

12 December 2020

Glycine cleavage system in ketotic hyperglycinemia: a reduction of H-protein activity

1 reference

12 December 2020

L-carnitine therapy in propionicacidaemia

1 reference

12 December 2020

Hypocarnitinemia in disorders of organic acid metabolism

1 reference

12 December 2020

C6-C10-dicarboxylic aciduria: investigations of a patient with riboflavin responsive multiple acyl-CoA dehydrogenation defects

1 reference

12 December 2020

Disposition of sodium benzoate in newborn infants with hyperammonemia

1 reference

12 December 2020

Identifiers

DOI

10.1136/ADC.58.11.916

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6 August 2017

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6 August 2017

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