(Q35515879)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

title

ADAMTSL6β protein rescues fibrillin-1 microfibril disorder in a Marfan syndrome mouse model through the promotion of fibrillin-1 assembly (English)

1 reference

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11 February 2020

1 reference

5

1 reference

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11 February 2020

author name string

Masahiro Saito

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Misaki Kurokawa

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Masahito Oda

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Masamitsu Oshima

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Kazutaka Kosaka

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Kazuhisa Nakao

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Miho Ogawa

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Ri-ichiroh Manabe

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Naoto Suda

10

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Ganburged Ganjargal

11

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Yasunobu Hada

12

1 reference

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11 February 2020

Toshihide Noguchi

13

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Toshio Teranaka

14

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Kiyotoshi Sekiguchi

15

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Toshiyuki Yoneda

16

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

Takashi Tsuji

17

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

language of work or name

English

0 references

publication date

31 August 2011

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

Journal of Biological Chemistry

11 February 2020

published in

1 reference

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11 February 2020

volume

286

1 reference

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11 February 2020

issue

44

1 reference

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11 February 2020

page(s)

38602-38613

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

ADAMTSL-6 is a novel extracellular matrix protein that binds to fibrillin-1 and promotes fibrillin-1 fibril formation

11 February 2020

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Extracellular microfibrils: contextual platforms for TGFbeta and BMP signaling

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

A homozygous mutation in ADAMTSL4 causes autosomal-recessive isolated ectopia lentis

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Fibrillin assembly requires fibronectin.

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

ADAMTSL2 mutations in geleophysic dysplasia demonstrate a role for ADAMTS-like proteins in TGF-beta bioavailability regulation

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Biogenesis of extracellular microfibrils: Multimerization of the fibrillin-1 C terminus into bead-like structures enables self-assembly

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Transcriptome database KK-Periome for periodontal ligament development: expression profiles of the extracellular matrix genes

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Therapy of Marfan syndrome

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Mechanisms for asporin function and regulation in articular cartilage

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Fibrillin-rich microfibrils: Structural determinants of morphogenetic and homeostatic events

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Marfan syndrome: from molecular pathogenesis to clinical treatment

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Angiotensin II type 1 receptor blockade attenuates TGF-beta-induced failure of muscle regeneration in multiple myopathic states

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Establishment of immortalized dental follicle cells for generating periodontal ligament in vivo

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Nanostructure of fibrillin-1 reveals compact conformation of EGF arrays and mechanism for extensibility.

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Lentivirus vectors expressing short hairpin RNAs against the U3-overlapping region of HIV nef inhibit HIV replication and infectivity in primary macrophages

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Immunohistochemical characterization of elastic system fibers in rat molar periodontal ligament

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Cited2 modulates TGF-beta-mediated upregulation of MMP9

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Losartan, an AT1 antagonist, prevents aortic aneurysm in a mouse model of Marfan syndrome

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Fibrillins 1 and 2 perform partially overlapping functions during aortic development

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Recent progress towards a molecular understanding of Marfan syndrome

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

The prodomain of BMP-7 targets the BMP-7 complex to the extracellular matrix

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

TGF-beta-dependent pathogenesis of mitral valve prolapse in a mouse model of Marfan syndrome

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Evidence for a critical contribution of haploinsufficiency in the complex pathogenesis of Marfan syndrome

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Consequences of cysteine mutations in calcium-binding epidermal growth factor modules of fibrillin-1.

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Structure of the integrin binding fragment from fibrillin-1 gives new insights into microfibril organization

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Fine tuning of growth factor signals depends on fibrillin microfibril networks

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Transcriptional profiling and regulation of the extracellular matrix during muscle regeneration

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Dysregulation of TGF-beta activation contributes to pathogenesis in Marfan syndrome

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Transforming growth factor-beta signal transduction and progressive renal disease

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Extracellular matrix in vascular morphogenesis and disease: structure versus signal

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Latent transforming growth factor beta-binding protein 1 interacts with fibrillin and is a microfibril-associated protein

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Core-binding factor alpha 1 (Cbfa1) induces osteoblastic differentiation of C2C12 cells without interactions with Smad1 and Smad5.

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Punctin, a novel ADAMTS-like molecule, ADAMTSL-1, in extracellular matrix

12 July 2018

1 reference

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Pathogenetic sequence for aneurysm revealed in mice underexpressing fibrillin-1

12 July 2018

1 reference

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TGF-beta signalling from cell membrane to nucleus through SMAD proteins

12 July 2018

1 reference

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Fibrillin, a new 350-kD glycoprotein, is a component of extracellular microfibrils

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3207443

Severe periodontitis in Marfan's syndrome: a case report

12 July 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

Oxytalan fibres in the periodontal ligament of equine molar cheek teeth

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

The development of a bioengineered organ germ method.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

Characteristic phenotype of immortalized periodontal cells isolated from a Marfan syndrome type I patient.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

Influence of extended operation time and of occlusal force on determination of pulpal healing pattern in replanted mouse molars.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

Quantification of expression and methylation of the Igf2r imprinted gene in segmental trisomic mouse model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

Effects of fibrillin-1 degradation on microfibril ultrastructure.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

Fibrillin-1 microfibril deposition is dependent on fibronectin assembly

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M111.243451

Phenotypic alteration of vascular smooth muscle cells precedes elastolysis in a mouse model of Marfan syndrome

21 January 2018

1 reference

12 December 2020

Gene expression and accumulation of fibrillin-1, fibrillin-2, and tropoelastin in cultured periodontal fibroblasts

1 reference

12 December 2020

Cementum matrix formation in vivo by cultured dental follicle cells

1 reference

12 December 2020

Allelic variation in normal human FBN1 expression in a family with Marfan syndrome: a potential modifier of phenotype?

1 reference

12 December 2020

Light microscopic autoradiography for study of early changes in the distribution of water-soluble materials

1 reference

12 December 2020

Structure of periodontal tissues in health and disease

1 reference

12 December 2020

A very private TGF-beta receptor embrace

1 reference

12 December 2020

Identifiers

DOI

10.1074/JBC.M111.243451

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21880733%20AND%20SRC:MED&resulttype=core&format=json

11 February 2020

PubMed publication ID

21880733

1 reference