(Q35910029)

11 August 2017

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title

Fibrillin microfibrils: multipurpose extracellular networks in organismal physiology (English)

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11 August 2017

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Francesco Ramirez

1

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11 August 2017

Lynn Y Sakai

series ordinal

2

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11 August 2017

Harry C Dietz

series ordinal

3

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11 August 2017

Daniel B Rifkin

series ordinal

4

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11 August 2017

publication date

1 October 2004

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11 August 2017

published in

Physiological Genomics

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11 August 2017

volume

19

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11 August 2017

issue

2

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11 August 2017

page(s)

151-154

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Making sense of latent TGFbeta activation

11 August 2017

cites work

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https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Regulation of limb patterning by extracellular microfibrils

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Fine tuning of growth factor signals depends on fibrillin microfibril networks

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

The elastin gene is disrupted by a translocation associated with supravalvular aortic stenosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Latent transforming growth factor beta-binding protein 1 interacts with fibrillin and is a microfibril-associated protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Evidence for a critical contribution of haploinsufficiency in the complex pathogenesis of Marfan syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Elastin is an essential determinant of arterial morphogenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Novel arterial pathology in mice and humans hemizygous for elastin

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Elastic fiber homeostasis requires lysyl oxidase-like 1 protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Homozygosity for a missense mutation in fibulin-5 (FBLN5) results in a severe form of cutis laxa

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Inactivation of the lysyl oxidase gene Lox leads to aortic aneurysms, cardiovascular dysfunction, and perinatal death in mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Fibulin-5/DANCE is essential for elastogenesis in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Dysregulation of TGF-beta activation contributes to pathogenesis in Marfan syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Pathogenetic sequence for aneurysm revealed in mice underexpressing fibrillin-1

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Targetting of the gene encoding fibrillin-1 recapitulates the vascular aspect of Marfan syndrome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Cell signaling events: a view from the matrix

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

Fibulin-5 is an elastin-binding protein essential for elastic fibre development in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FPHYSIOLGENOMICS.00092.2004

10.1152/PHYSIOLGENOMICS.00092.2004

21 January 2018

Identifiers

DOI

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11 August 2017

1 reference