(Q35915766)

11 August 2017

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title

A cure for traffic jams: small molecule chaperones in the endoplasmic reticulum (English)

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11 August 2017

main subject

endoplasmic reticulum

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molecular chaperones

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author name string

Karin Römisch

series ordinal

1

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11 August 2017

publication date

1 November 2004

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11 August 2017

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11 August 2017

volume

5

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11 August 2017

issue

11

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11 August 2017

page(s)

815-820

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Quality control in the endoplasmic reticulum protein factory

11 August 2017

cites work

1 reference

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Pharmacological chaperones rescue cell-surface expression and function of misfolded V2 vasopressin receptor mutants

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A contradictory treatment for lysosomal storage disorders: inhibitors enhance mutant enzyme activity

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Aberrant retention of tyrosinase in the endoplasmic reticulum mediates accelerated degradation of the enzyme and contributes to the dedifferentiated phenotype of amelanotic melanoma cells

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The molecular mechanism of stabilization of proteins by TMAO and its ability to counteract the effects of urea

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Trehalose-enzyme interactions result in structure stabilization and activity inhibition. The role of viscosity

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21 January 2018

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Structural control of endoplasmic reticulum-associated degradation: effect of chemical chaperones on 3-hydroxy-3-methylglutaryl-CoA reductase

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Chemical chaperones mediate increased secretion of mutant alpha 1-antitrypsin (alpha 1-AT) Z: A potential pharmacological strategy for prevention of liver injury and emphysema in alpha 1-AT deficiency

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21 January 2018

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21 January 2018

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21 January 2018

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Improvement in cardiac function in the cardiac variant of Fabry's disease with galactose-infusion therapy

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Do molecular chaperones have to be proteins?

21 January 2018

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Molecular chaperones in the yeast endoplasmic reticulum maintain the solubility of proteins for retrotranslocation and degradation

21 January 2018

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6-mer peptide selectively anneals to a pathogenic serpin conformation and blocks polymerization. Implications for the prevention of Z alpha(1)-antitrypsin-related cirrhosis

21 January 2018

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Mutants of neuroserpin that cause dementia accumulate as polymers within the endoplasmic reticulum

21 January 2018

1 reference

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Regulation of protein secretion through controlled aggregation in the endoplasmic reticulum

21 January 2018

1 reference

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Correction of Defective Protein Kinesis of Human P-glycoprotein Mutants by Substrates and Modulators

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1600-0854.2004.00231.X

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1600-0854.2004.00231.X

10.1111/J.1600-0854.2004.00231.X

21 January 2018

Identifiers

DOI

1 reference

11 August 2017

1 reference