(Q36388415)

13 August 2017

Isovaleryl-CoA dehydrogenase: demonstration in rat liver mitochondria by ion exchange chromatography and isoelectric focusing (English)

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13 August 2017

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Noda C

1

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13 August 2017

Rhead WJ

series ordinal

2

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13 August 2017

Tanaka K

series ordinal

3

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13 August 2017

language of work or name

English

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publication date

1 May 1980

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Proceedings of the National Academy of Sciences of the United States of America

13 August 2017

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13 August 2017

77

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13 August 2017

5

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13 August 2017

2646-2650

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On the mechanism of dehydrogenation of fatty acyl derivatives of coenzyme A. III. Palmityl coA dehydrogenase

13 August 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Enzymatic carboxylation of beta-hydroxyisovaleryl coenzyme A

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

On the mechanism of dehydrogenation of fatty acyl derivatives of coenzyme A. I. The general fatty acyl coenzyme A dehydrogenase

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Studies on the fatty acid oxidizing system of animal tissues. III. Butyryl coenzyme A dehydrogenase

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Demonstration of a specific mitochondrial isovaleryl-CoA dehydrogenase deficiency in fibroblasts from patients with isovaleric acidemia

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Isovaleric acidemia: a new genetic defect of leucine metabolism

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Demonstration of a new mammalian isoleucine catabolic pathway yielding an Rseries of metabolites

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Acyl coenzyme A dehydrogenases and electron-transferring flavoprotein from beef hart mitochondria

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Ethylmalonic-adipic aciduria. In vivo and in vitro studies indicating deficiency of activities of multiple acyl-CoA dehydrogenases

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Mammalian metabolism of glutaric acid

30 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Glutaric aciduria: Inherited deficiency of glutaryl-CoA dehydrogenase activity

28 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Acyl-CoA dehydrogenases and electron-transferring flavoprotein

28 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Studies on glutaryl-CoA dehydrogenase in leucocytes, fibroblasts and amniotic fluid cells. The normal enzyme and the mutant form in patients with glutaric aciduria

28 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Metabolism in rats in vivo of RS-2-methylbutyrate and n-butyrate labeled with stable isotopes at various positions. Mechanism of biosynthesis and degradation of ethylmalonyl semialdehyde and ethylmalonic acid

28 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

Isovaleric acidemia. Clinical features of a new genetic defect of leucine metabolism.

28 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=349459

The Electron-transferring Flavoprotein as a Common Intermediate in the Mitochondrial Oxidation of Butyryl Coenzyme A and Sarcosine

21 September 2018

1 reference

12 December 2020

The Isolation and Identification of N-Isovalerylglycine from Urine of Patients with Isovaleric Acidemia

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12 December 2020

A rapid and simple procedure to deplete rat-liver mitochondria of lysosomal activity

1 reference

12 December 2020

Possibility of inborn defect in isovalericacidaemia involving altered enzyme specificity rather than total inactivity

1 reference

12 December 2020

The purification and some properties of electron transfer flavoprotein and general fatty acyl coenzyme A dehydrogenase from pig liver mitochondria

1 reference

12 December 2020

Glutaric aciduria type II: Report on a previously undescribed metabolic disorder

1 reference

12 December 2020

Acyl-coenzyme A dehydrogenase from pig kidney. Purification and properties

1 reference

12 December 2020

Metabolism in rats in vivo of (2S)[3,3,3-2H3]isobutyrate. Identification of (2-pro-S)methyl group as the source of a proton in dehydrogenation

1 reference

12 December 2020

On the mechanism of dehydrogenation of fatty acyl derivatives of coenzyme A. VII. The nature of the green color of butyryl dehydrogenase

1 reference

12 December 2020

The specificity of triglyceride synthesis from diglycerides in chicken adipose tissue

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.77.5.2646

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13 August 2017

0 references

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13 August 2017

PubMed publication ID

6930657

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