(Q36851172)

16 August 2017

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title

Knockin animal models of inherited arrhythmogenic diseases: what have we learned from them? (English)

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16 August 2017

Kathy M Nilles

1

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16 August 2017

Barry London

series ordinal

2

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16 August 2017

publication date

16 June 2007

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Journal of Cardiovascular Electrophysiology

16 August 2017

published in

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16 August 2017

volume

18

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16 August 2017

issue

10

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16 August 2017

page(s)

1117-1125

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Gene disruption in mice: models of development and disease

16 August 2017

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Strain-specific patterns of autonomic nervous system activity and heart failure susceptibility in mice

21 January 2018

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21 January 2018

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Subdiaphragmatic murine electrophysiological studies: sequential determination of ventricular refractoriness and arrhythmia induction

21 January 2018

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The congenital long QT syndromes from genotype to phenotype: clinical implications

21 January 2018

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Inner ear defects induced by null mutation of the isk gene

21 January 2018

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Involvement of IsK-associated K+ channel in heart rate control of repolarization in a murine engineered model of Jervell and Lange-Nielsen syndrome

21 January 2018

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A new spontaneous mouse mutation in the Kcne1 gene

21 January 2018

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Replacement by homologous recombination of the minK gene with lacZ reveals restriction of minK expression to the mouse cardiac conduction system.

21 January 2018

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Cardiac gap junction channels: modulation of expression and channel properties

21 January 2018

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Connexin30.2 containing gap junction channels decelerate impulse propagation through the atrioventricular node

21 January 2018

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A cardiac sodium channel mutation cosegregates with a rare connexin40 genotype in familial atrial standstill

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21 January 2018

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21 January 2018

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Conduction slowing and sudden arrhythmic death in mice with cardiac-restricted inactivation of connexin43

21 January 2018

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Specific permeability and selective formation of gap junction channels in connexin-transfected HeLa cells

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Connexin31 cannot functionally replace connexin43 during cardiac morphogenesis in mice.

21 January 2018

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21 January 2018

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Abrupt rate accelerations or premature beats cause life-threatening arrhythmias in mice with long-QT3 syndrome.

21 January 2018

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Stimulation of protein kinase C inhibits bursting in disease-linked mutant human cardiac sodium channels

21 January 2018

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Effect of pacing and mexiletine on dispersion of repolarisation and arrhythmias in DeltaKPQ SCN5A (long QT3) mice

21 January 2018

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Long QT syndrome patients with mutations of the SCN5A and HERG genes have differential responses to Na+ channel blockade and to increases in heart rate. Implications for gene-specific therapy.

21 January 2018

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Genetic basis and molecular mechanism for idiopathic ventricular fibrillation

21 January 2018

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Cardiac conduction defects associate with mutations in SCN5A

21 January 2018

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Slowed conduction and ventricular tachycardia after targeted disruption of the cardiac sodium channel gene Scn5a

21 January 2018

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Mouse model of SCN5A-linked hereditary Lenègre's disease: age-related conduction slowing and myocardial fibrosis

21 January 2018

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A single Na(+) channel mutation causing both long-QT and Brugada syndromes

21 January 2018

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Overlap syndrome of cardiac sodium channel disease in mice carrying the equivalent mutation of human SCN5A-1795insD

21 January 2018

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Cardiac excitation-contraction coupling

21 January 2018

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Mutations in the cardiac ryanodine receptor gene (hRyR2) underlie catecholaminergic polymorphic ventricular tachycardia

21 January 2018

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Clinical and molecular characterization of patients with catecholaminergic polymorphic ventricular tachycardia.

21 January 2018

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Identification of mutations in the cardiac ryanodine receptor gene in families affected with arrhythmogenic right ventricular cardiomyopathy type 2 (ARVD2)

21 January 2018

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Genetics of arrhythmogenic right ventricular cardiomyopathy

21 January 2018

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Enhanced basal activity of a cardiac Ca2+ release channel (ryanodine receptor) mutant associated with ventricular tachycardia and sudden death

21 January 2018

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Enhanced store overload-induced Ca2+ release and channel sensitivity to luminal Ca2+ activation are common defects of RyR2 mutations linked to ventricular tachycardia and sudden death

21 January 2018

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Bidirectional ventricular tachycardia and fibrillation elicited in a knock-in mouse model carrier of a mutation in the cardiac ryanodine receptor.

21 January 2018

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FKBP12.6 deficiency and defective calcium release channel (ryanodine receptor) function linked to exercise-induced sudden cardiac death

21 January 2018

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Protection from cardiac arrhythmia through ryanodine receptor-stabilizing protein calstabin2.

21 January 2018

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Stabilization of cardiac ryanodine receptor prevents intracellular calcium leak and arrhythmias

21 January 2018

1 reference

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Screening for ryanodine receptor type 2 mutations in families with effort-induced polymorphic ventricular arrhythmias and sudden death: early diagnosis of asymptomatic carriers.

21 January 2018

1 reference

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Direct block of hERG potassium channels by the protein kinase C inhibitor bisindolylmaleimide I (GF109203X).

21 January 2018

1 reference

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Differential Ca2+ sensitivity of RyR2 mutations reveals distinct mechanisms of channel dysfunction in sudden cardiac death.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Mice with the R176Q cardiac ryanodine receptor mutation exhibit catecholamine-induced ventricular tachycardia and cardiomyopathy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Cre recombinase: the universal reagent for genome tailoring

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Conditional protein alleles using knockin mice and a chemical inducer of dimerization

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Improved methods for the generation of human gene knockout and knockin cell lines

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Ankyrins and human disease: what the electrophysiologist should know

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

A novel form of short QT syndrome (SQT3) is caused by a mutation in the KCNJ2 gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Architectural and functional asymmetry of the His-Purkinje system of the murine heart.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Atrial fibrillation in KCNE1-null mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

Evaluation of Approaches to Generation of Tissue-specific Knock-in Mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1540-8167.2007.00884.X

10.1111/J.1540-8167.2007.00884.X

21 January 2018

Identifiers

DOI

1 reference

16 August 2017

1 reference