(Q36851526)

16 August 2017

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title

Cytoskeleton as a potential target in the neuropathology of maple syrup urine disease: insight from animal studies (English)

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maple syrup urine disease

16 August 2017

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Pessoa-Pureur R

1

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PubMed ID

17574538

16 August 2017

Wajner M

series ordinal

2

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16 August 2017

14 June 2007

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Journal of Inherited Metabolic Disease

16 August 2017

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16 August 2017

30

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16 August 2017

5

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16 August 2017

664-672

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https://scigraph.springernature.com/pub.10.1007/s10545-007-0562-6

16 August 2017

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cites work

Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane depolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS10545-007-0562-6

The co-workers of actin filaments: from cell structures to signals

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS10545-007-0562-6

Water Apparent Diffusion Coefficient and T2 Changes in the Acute Stage of Maple Syrup Urine Disease: Evidence of Intramyelinic and Vasogenic‐Interstitial Edema

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1007%2FS10545-007-0562-6

Effect of propionic and methylmalonic acids on the in vitro phosphorylation of intermediate filaments from cerebral cortex of rats during development

21 January 2018

1 reference

12 December 2020

Rho proteins: linking signaling with membrane trafficking

1 reference

12 December 2020

Disruption of actin cytoskeleton in cultured rat astrocytes suppresses ATP- and bradykinin-induced [Ca(2+)](i) oscillations by reducing the coupling efficiency between Ca(2+) release, capacitative Ca(2+) entry, and store refilling.

1 reference

12 December 2020

Maple syrup urine disease: findings on CT and MR scans of the brain in 10 infants

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12 December 2020

Methylmalonic and propionic acids increase the in vitro incorporation of 32P into cytoskeletal proteins from cerebral cortex of young rats through NMDA glutamate receptors

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12 December 2020

Effect of leucine administration on creatine kinase activity in rat brain.

1 reference

12 December 2020

Glutamate and gamma-aminobutyric acid neurotransmitter systems in the acute phase of maple syrup urine disease and citrullinemia encephalopathies in newborn calves

1 reference

12 December 2020

Intermediate filaments: molecular structure, assembly mechanism, and integration into functionally distinct intracellular Scaffolds

1 reference

12 December 2020

Glutamate binding in the rat cerebral cortex during ontogeny

1 reference

12 December 2020

Morphological alterations and cell death provoked by the branched-chain alpha-amino acids accumulating in maple syrup urine disease in astrocytes from rat cerebral cortex

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12 December 2020

Molecular architecture of intermediate filaments

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12 December 2020

GABAA, NMDA and AMPA receptors: a developmentally regulated 'ménage à trois'.

1 reference

12 December 2020

Oxidative stress and 17-alpha- and 17-beta-estradiol modulate neurofilaments differently

1 reference

12 December 2020

Filamentous nerve cell inclusions in neurodegenerative diseases

1 reference

12 December 2020

alpha-Ketoisocaproic acid regulates phosphorylation of intermediate filaments in postnatal rat cortical slices through ionotropic glutamatergic receptors

1 reference

12 December 2020

Abnormal distribution of phosphorylated neurofilaments in neuronal degeneration induced by kainic acid

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12 December 2020

Neurofilament gene expression: a major determinant of axonal caliber

1 reference

12 December 2020

Inhibition of brain glutamic acid decarboxylase by phenylalanine, valine, and leucine derivatives: a suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria.

1 reference

12 December 2020

Evidence that oxidative stress is increased in plasma from patients with maple syrup urine disease.

1 reference

12 December 2020

Nucleotide exchange between cytosolic ATP and F-actin-bound ADP may be a major energy-utilizing process in unstimulated platelets

1 reference

12 December 2020

Transient expression of the NR2C subunit of the NMDA receptor in developing rat brain.

1 reference

12 December 2020

Axonal transport of neurofilaments in normal and disease states

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12 December 2020

A potential role for altered protein phosphorylation in the mediation of developmental neurotoxicity

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12 December 2020

Phosphorylation-dependent immunoreactivity of neurofilaments increases during axonal maturation and beta,beta'-iminodipropionitrile intoxication

1 reference

12 December 2020

Amyloid beta-peptide (1-42)-induced oxidative stress and neurotoxicity: implications for neurodegeneration in Alzheimer's disease brain. A review

1 reference

12 December 2020

Inhibition of mitochondrial pyruvate transport by phenylpyruvate and alpha-ketoisocaproate.

1 reference

12 December 2020

The relationship between mitochondrial shape and function and the cytoskeleton.

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12 December 2020

Neurofilaments in health and disease

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12 December 2020

Creatine and antioxidant treatment prevent the inhibition of creatine kinase activity and the morphological alterations of C6 glioma cells induced by the branched-chain alpha-keto acids accumulating in maple syrup urine disease

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12 December 2020

Actin-ATP hydrolysis is a major energy drain for neurons.

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12 December 2020

Inhibition of glutamate uptake into synaptic vesicles of rat brain by the metabolites accumulating in maple syrup urine disease

1 reference

12 December 2020

The regulation of neurofilament protein dynamics by phosphorylation: clues to neurofibrillary pathobiology

1 reference

12 December 2020

Phosphorylated neurofilaments in neuronal perikarya and dendrites in human brain following axonal damage

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12 December 2020

Glutamate induces rapid upregulation of astrocyte glutamate transport and cell-surface expression of GLAST.

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12 December 2020

Influence of alpha-ketoacids on the respiration of brain in vitro.

1 reference

12 December 2020

Effect of the branched-chain alpha-ketoacids accumulating in maple syrup urine disease on the high molecular weight neurofilament subunit (NF-H) in rat cerebral cortex

1 reference

12 December 2020

Morphological alterations and induction of oxidative stress in glial cells caused by the branched-chain alpha-keto acids accumulating in maple syrup urine disease.

1 reference

12 December 2020

Alpha-keto-beta-methylvaleric acid increases the in vitro phosphorylation of intermediate filaments in cerebral cortex of young rats through the gabaergic system

1 reference

12 December 2020

The role of glutamate receptor maturation in perinatal seizures and brain injury

1 reference

12 December 2020

Neuropathological observations in maple syrup urine disease: branched-chain ketoaciduria

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12 December 2020

Effect of hyperphenylalaninemia chemically induced on in vitro incorporation of 32P into cytoskeletal proteins from cerebral cortex of developing rats

1 reference

12 December 2020

Induction of oxidative stress in rat brain by the metabolites accumulating in maple syrup urine disease.

1 reference

12 December 2020

Propionic acid induces cytoskeletal alterations in cultured astrocytes from rat cerebral cortex.

1 reference

12 December 2020

Alpha-ketoisocaproic acid increases phosphorylation of intermediate filament proteins from rat cerebral cortex by mechanisms involving Ca2+ and cAMP.

1 reference

12 December 2020

The axonal transport of mitochondria.

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12 December 2020

N-methyl-D-aspartate receptor excitotoxicity involves activation of polyamine synthesis: protection by alpha-difluoromethylornithine

1 reference

12 December 2020

Glutamate neurotoxicity and diseases of the nervous system

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12 December 2020

Alpha-ketoisocaproate increases the in vitro 32P incorporation into intermediate filaments in cerebral cortex of rats

1 reference

12 December 2020

Intermediate filaments mediate cytoskeletal crosstalk

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12 December 2020

Cytoskeletal assembly and ATP release regulate astrocytic calcium signaling.

1 reference

12 December 2020

Evidence that the branched-chain alpha-keto acids accumulating in maple syrup urine disease induce morphological alterations and death in cultured astrocytes from rat cerebral cortex

1 reference

12 December 2020

Propionic and L-methylmalonic acids induce oxidative stress in brain of young rats.

1 reference

12 December 2020

Abnormal dendritic development in maple syrup urine disease

1 reference

12 December 2020

Cyclin-dependent kinase 5 increases perikaryal neurofilament phosphorylation and inhibits neurofilament axonal transport in response to oxidative stress

1 reference

12 December 2020

Neurofilament functions in health and disease

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12 December 2020

Neurofilament phosphoforms: surrogate markers for axonal injury, degeneration and loss

1 reference

12 December 2020

Phosphorylation on carboxyl terminus domains of neurofilament proteins in retinal ganglion cell neurons in vivo: influences on regional neurofilament accumulation, interneurofilament spacing, and axon caliber

1 reference

12 December 2020

Dysmyelination in the brain of adolescents and young adults with maple syrup urine disease

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12 December 2020

Early changes in Huntington's disease patient brains involve alterations in cytoskeletal and synaptic elements

1 reference

12 December 2020

Cyclic AMP-dependent protein kinase mediates ocular dominance shifts in cat visual cortex

1 reference

12 December 2020

The actin cytoskeleton: a key regulator of apoptosis and ageing?

1 reference

12 December 2020

Reduction of glutamate uptake into cerebral cortex of developing rats by the branched-chain alpha-keto acids accumulating in maple syrup urine disease

1 reference

12 December 2020

Stimulation of lipid peroxidation in vitro in rat brain by the metabolites accumulating in maple syrup urine disease

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12 December 2020

Cytoskeletal actin gates a Cl- channel in neocortical astrocytes

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12 December 2020

Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease

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12 December 2020

Evidence that intracellular Ca2+ mediates the effect of alpha-ketoisocaproic acid on the phosphorylating system of cytoskeletal proteins from cerebral cortex of immature rats

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12 December 2020

Aberrant phosphorylation of neurofilaments accompanies transmitter-related changes in rat septal neurons following transection of the fimbria-fornix

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12 December 2020

Regional ontogeny of a unique glutamate recognition site in rat brain: an autoradiographic study

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12 December 2020

Neuronal intermediate filaments

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12 December 2020

Transient increased density of NMDA binding sites in the developing rat hippocampus

1 reference

12 December 2020

Neuronal metabolism of branched-chain amino acids: flux through the aminotransferase pathway in synaptosomes

1 reference

12 December 2020

Axonal cytoskeletal pathology in aged and diabetic human sympathetic autonomic ganglia.

1 reference

12 December 2020

A novel neuronal messenger molecule in brain: the free radical, nitric oxide

1 reference

12 December 2020

Regulation of microtubules in cell migration

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12 December 2020

alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats.

1 reference

12 December 2020

Reduction of large neutral amino acid levels in plasma and brain of hyperleucinemic rats.

1 reference

12 December 2020

Maple syrup urine disease encephalopathy: a follow-up study in the acute stage using diffusion-weighted MRI

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12 December 2020

Excitatory actions of gaba during development: the nature of the nurture

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12 December 2020

MAPLE SYRUP URINE DISEASE, WITH PARTICULAR REFERENCE TO DIETOTHERAPY

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12 December 2020

Regional regulation of microtubule dynamics in polarized, motile cells

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12 December 2020

Mechanism of actin polymerization in cellular ATP depletion

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12 December 2020

Age dependence of NMDA receptor involvement in epileptiform activity in rat hippocampal slices.

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12 December 2020

Long-term plasticity at GABAergic and glycinergic synapses: mechanisms and functional significance

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12 December 2020

Branched-chain alpha-keto acids accumulating in maple syrup urine disease induce reorganization of phosphorylated GFAP in C6-glioma cells

1 reference

12 December 2020

Phosphorylation-related immunoreactivity and the rate of transport of neurofilaments in chronic 2,5-hexanedione intoxication

1 reference

12 December 2020

10.1007/S10545-007-0562-6

Identifiers

DOI

1 reference

16 August 2017

1 reference

PubMed ID

17574538