(Q37856806)

24 August 2017

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title

Hyperammonemia in review: pathophysiology, diagnosis, and treatment (English)

1 reference

24 August 2017

0 references

1 reference

Ari Auron

1

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24 August 2017

Patrick D Brophy

series ordinal

2

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24 August 2017

language of work or name

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23 March 2011

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24 August 2017

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24 August 2017

volume

27

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24 August 2017

issue

2

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24 August 2017

page(s)

207-222

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Ammonia toxicity and its prevention in inherited defects of the urea cycle

24 August 2017

cites work

1 reference

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Renal ammoniagenesis in an early stage of metabolic acidosis in man.

21 January 2018

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Nutritional management of patients with urea cycle disorders

21 January 2018

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Neurological implications of urea cycle disorders

21 January 2018

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Neurologic damage and neurocognitive dysfunction in urea cycle disorders

21 January 2018

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Neurologic outcome in children with inborn errors of urea synthesis. Outcome of urea-cycle enzymopathies

21 January 2018

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Survival after treatment with phenylacetate and benzoate for urea-cycle disorders

21 January 2018

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Effects of hyperammonaemia on brain function

21 January 2018

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https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Peritoneal dialysis in neonates with inborn errors of metabolism: is it really out of date?

21 January 2018

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https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Current concepts in the pathogenesis of urea cycle disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Ornithine transcarbamylase deficiency: neuropathologic changes acquired in utero

21 January 2018

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Magnetic resonance spectroscopy shows increased brain glutamine in ornithine carbamoyl transferase deficiency

21 January 2018

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Role of glutamine in cerebral nitrogen metabolism and ammonia neurotoxicity

21 January 2018

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Organic osmolytes in hyponatremia and ammonia toxicity

21 January 2018

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Accumulation of large neutral amino acids in the brain of sparse-fur mice at hyperammonemic state

21 January 2018

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https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Role of NMDA receptors in acute liver failure and ammonia toxicity: therapeutical implications.

21 January 2018

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Differential vulnerability of central neurons of the rat to quinolinic acid

21 January 2018

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Effect of ammonia on astrocytic glutamate uptake/release mechanisms.

21 January 2018

1 reference

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Reduction in the MK-801 binding sites of the NMDA sub-type of glutamate receptor in a mouse model of congenital hyperammonemia: prevention by acetyl-L-carnitine

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Glutamatergic and gabaergic neurotransmission and neuronal circuits in hepatic encephalopathy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Brain serotonin2 and serotonin1A receptors are altered in the congenitally hyperammonemic sparse fur mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Anorexia and altered serotonin metabolism in a patient with argininosuccinic aciduria

21 January 2018

1 reference

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Progressive decrease of cerebral cytochrome C oxidase activity in sparse-fur mice: role of acetyl-L-carnitine in restoring the ammonia-induced cerebral energy depletion

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Mechanisms of ischemic neuroprotection by acetyl-L-carnitine

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Ammonium alters creatine transport and synthesis in a 3D culture of developing brain cells, resulting in secondary cerebral creatine deficiency.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

CNTF protects oligodendrocytes from ammonia toxicity: intracellular signaling pathways involved

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Oxidative stress and mitogen-activated protein kinase phosphorylation mediate ammonia-induced cell swelling and glutamate uptake inhibition in cultured astrocytes.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Gene expression profiling of astrocytes from hyperammonemic mice reveals altered pathways for water and potassium homeostasis in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Identifying the direct effects of ammonia on the brain.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Cross-sectional multicenter study of patients with urea cycle disorders in the United States

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Lysinuric protein intolerance. Basolateral transport defect in renal tubuli

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Carbamazepine-induced hyperammonemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Hyperammonemia in asterixis induced by carbamazepine: two case reports

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

The role of carnitine supplementation during valproic acid therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Valproate-induced hyperammonemic encephalopathy and normal liver functions: possible synergism with topiramate

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Valproate-induced hyperammonemic encephalopathy in the presence of topiramate

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Adjunctive topiramate enhances the risk of hypothermia associated with valproic acid therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Hyperammonemic encephalopathy after induction chemotherapy for acute lymphoblastic leukemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Hyperammonemia encephalopathy: an important cause of neurological deterioration following chemotherapy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Idiopathic hyperammonemia (IHA) after dose-dense induction chemotherapy for acute myeloid leukemia: Case report and review of the literature

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Risk of transient hyperammonemic encephalopathy in cancer patients who received continuous infusion of 5-fluorouracil with the complication of dehydration and infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Risk of hyperammonemic coma in the puerperium: two cases of women with diagnosed and undiagnosed deficiency of urea cycle enzymes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Ornithine transcarbamylase deficiency in pregnancy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Carbamyl phosphate synthase deficiency: diagnosed during pregnancy in a 41-year-old.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Relationship of renal ammonia production and potassium homeostasis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Hyperammonaemia with distal renal tubular acidosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Hyperammonemic encephalopathy caused by carnitine deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Acute encephalopathy of Bacillus cereus mimicking Reye syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Medical management and dialysis therapy for the infant with an inborn error of metabolism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Current strategies for the management of neonatal urea cycle disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Management and emergency treatments of neonates with a suspicion of inborn errors of metabolism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Biochemical efficacy of N-carbamylglutamate in neonatal severe hyperammonaemia due to propionic acidaemia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

The first use of N-carbamylglutamate in a patient with decompensated maple syrup urine disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

N-carbamylglutamate in emergency management of hyperammonemia in neonatal acute onset propionic and methylmalonic aciduria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

N-carbamylglutamate enhances ammonia detoxification in a patient with decompensated methylmalonic aciduria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Favourable long-term outcome after immediate treatment of neonatal hyperammonemia due to N-acetylglutamate synthase deficiency.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Inhibition of glutamine synthetase reduces ammonia-induced astrocyte swelling in rat

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Prenatal benzoate treatment in urea cycle defects

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Arginine, an indispensable amino acid for patients with inborn errors of urea synthesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Alternative pathway therapy for urea cycle disorders: twenty years later

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Continuous venovenous haemodialysis (CVVHD) and continuous peritoneal dialysis (CPD) in the acute management of 21 children with inborn errors of metabolism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Extracorporeal dialysis in neonatal hyperammonemia: modalities and prognostic indicators.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Acute hemodialysis for hyperammonemia in small neonates

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Clearance of amino acids by hemodialysis in argininosuccinate synthetase deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Continuous renal replacement therapy and plasma exchange in newborns and infants

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Comparison of solute clearance in three modes of continuous renal replacement therapy

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Efficacy of L-ornithine L-aspartate in acute liver failure: a double-blind, randomized, placebo-controlled study

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Mechanisms of cognitive alterations in hyperammonemia and hepatic encephalopathy: therapeutical implications.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Liver transplantation for inherited metabolic disorders of the liver.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Liver transplantation for the treatment of urea cycle disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

The role of liver transplantation in urea cycle disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Long-term correction of urea cycle disorders

21 January 2018

2 references

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

21 January 2018

12 December 2020

One liver for four children: first clinical series of liver cell transplantation for severe neonatal urea cycle defects

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Intellectual, adaptive, and behavioral functioning in children with urea cycle disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Nitrogen sparing therapy revisited 2009.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Estimation of the total number of disease-causing mutations in ornithine transcarbamylase (OTC) deficiency. Value of the OTC structure in predicting a mutation pathogenic potential

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00467-011-1838-5

Cognitive development in children with inborn errors of urea synthesis

21 January 2018

1 reference

12 December 2020

Late clinical presentation of partial carbamyl phosphate synthetase I deficiency

1 reference

12 December 2020

Phenylacetate and benzoate clearance in a hyperammonemic infant on sequential hemodialysis and hemofiltration

1 reference

12 December 2020

Effect of hyperammonemia on insulin-mediated glucose uptake in rats

1 reference

12 December 2020

1 reference

12 December 2020

Treatment of hyperammonemic coma caused by inborn errors of urea synthesis

1 reference

12 December 2020

Acute hemodialysis of infants weighing less than five kilograms

1 reference

12 December 2020

Carbamazepine-associated asterixis and hyperammonemia

1 reference

12 December 2020

Urea cycle disorders: diagnosis, pathophysiology, and therapy.

1 reference

12 December 2020

Clinical consequences of urea cycle enzyme deficiencies and potential links to arginine and nitric oxide metabolism

1 reference

12 December 2020

Valproate-induced inhibition of urea synthesis

1 reference

12 December 2020

Brain MR imaging in neonatal hyperammonemic encephalopathy resulting from proximal urea cycle disorders.

1 reference

12 December 2020

Biochemistry and physiology of brain ammonia

1 reference

12 December 2020

Hyperammonaemic encephalopathy associated with rituximab-containing chemotherapy

1 reference

12 December 2020

Hyperammonaemia in a child with distal renal tubular acidosis

1 reference

12 December 2020

Ammonia clearance by peritoneal dialysis and continuous arteriovenous hemodiafiltration

1 reference

12 December 2020

Dialysis in neonates with inborn errors of metabolism

1 reference

12 December 2020

Quinolinic acid in children with congenital hyperammonemia

1 reference

12 December 2020

Peritoneal dialysis in the treatment of metabolic crises caused by inherited disorders of organic and amino acid metabolism

1 reference

12 December 2020

Generalized convulsion resulted in hyperammonemia during treatment with tranexamic acid for hemoptysis

1 reference

12 December 2020

Ammonium-induced impairment of axonal growth is prevented through glial creatine.

1 reference

12 December 2020

Respiratory fuels and nitrogen metabolism in vivo in small intestine of fed rats. Quantitative importance of glutamine, glutamate, and aspartate

1 reference

12 December 2020

Increase of Tryptophan and 5-Hydroxyindole Acetic Acid in the Brain of Ornithine Carbamoyltransferase Deficient Sparse-Fur Mice

1 reference

12 December 2020

Ammonia encephalopathy secondary to urinary tract infection with Proteus mirabilis

1 reference

12 December 2020

Valproate-induced hyperammonemic encephalopathy

1 reference

12 December 2020

Evidence for cholinergic neuronal loss in brain in congenital ornithine transcarbamylase deficiency

1 reference

12 December 2020

Continuous venovenous haemofiltration in the acute treatment of inborn errors of metabolism

1 reference

12 December 2020

Comparison of exchange transfusion, peritoneal dialysis, and hemodialysis for the treatment of hyperammonemia in an anuric newborn infant

1 reference

12 December 2020

Hyperammonemic encephalopathy in multiple myeloma

1 reference

12 December 2020

10.1007/S00467-011-1838-5

Identifiers

DOI

1 reference

24 August 2017

1 reference