(Q37957815)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

title

Exploring frataxin function (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

Diego F Gómez-Casati

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

author name string

Maria V Busi

series ordinal

1

1 reference

25 August 2017

Diego F Gomez-Casati

series ordinal

2

1 reference

25 August 2017

17 November 2011

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

volume

64

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

issue

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

16 January 2020

page(s)

56-63

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22095894%20AND%20SRC:MED&resulttype=core&format=json

Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

16 January 2020

cites work

1 reference

Studies of human, mouse and yeast homologues indicate a mitochondrial function for frataxin

21 January 2018

1 reference

Inactivation of the Friedreich ataxia mouse gene leads to early embryonic lethality without iron accumulation

21 January 2018

1 reference

Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin

21 January 2018

1 reference

Reduced expression of frataxin extends the lifespan of Caenorhabditis elegans

21 January 2018

1 reference

RNAi-mediated suppression of the mitochondrial iron chaperone, frataxin, in Drosophila.

21 January 2018

1 reference

Functional and molecular characterization of the frataxin homolog from Arabidopsis thaliana.

21 January 2018

1 reference

Frataxin activates mitochondrial energy conversion and oxidative phosphorylation

21 January 2018

1 reference

Inhibition of Fe-S cluster biosynthesis decreases mitochondrial iron export: evidence that Yfh1p affects Fe-S cluster synthesis

21 January 2018

1 reference

The yeast frataxin homolog Yfh1p plays a specific role in the maturation of cellular Fe/S proteins

21 January 2018

1 reference

Yeast Frataxin Sequentially Chaperones and Stores Iron by Coupling Protein Assembly with Iron Oxidation

21 January 2018

1 reference

Frataxin acts as an iron chaperone protein to modulate mitochondrial aconitase activity

21 January 2018

1 reference

Iron use for haeme synthesis is under control of the yeast frataxin homologue (Yfh1).

21 January 2018

1 reference

Mitochondrial iron detoxification is a primary function of frataxin that limits oxidative damage and preserves cell longevity

21 January 2018

1 reference

Assembly of human frataxin is a mechanism for detoxifying redox-active iron

21 January 2018

1 reference

The ferroxidase activity of yeast frataxin

21 January 2018

1 reference

Nitric oxide and frataxin: two players contributing to maintain cellular iron homeostasis

21 January 2018

1 reference

Crystal structure of Escherichia coli CyaY protein reveals a previously unidentified fold for the evolutionarily conserved frataxin family

21 January 2018

1 reference

Crystal structure of human frataxin

21 January 2018

1 reference

Towards a structural understanding of Friedreich's ataxia: the solution structure of frataxin

21 January 2018

1 reference

Yeast frataxin solution structure, iron binding, and ferrochelatase interaction.

21 January 2018

1 reference

Iron-dependent self-assembly of recombinant yeast frataxin: implications for Friedreich ataxia

21 January 2018

1 reference

Assembly and iron-binding properties of human frataxin, the protein deficient in Friedreich ataxia

21 January 2018

1 reference

Iron-induced oligomerization of yeast frataxin homologue Yfh1 is dispensable in vivo

21 January 2018

1 reference

Maturation of iron-sulfur proteins in eukaryotes: mechanisms, connected processes, and diseases

21 January 2018

1 reference

Structure, function, and formation of biological iron-sulfur clusters

21 January 2018

1 reference

Ancient and essential: the assembly of iron-sulfur clusters in plants

21 January 2018

1 reference

Formation and insertion of the nitrogenase iron-molybdenum cofactor

21 January 2018

1 reference

Maturation of nitrogenase: a biochemical puzzle

21 January 2018

1 reference

A third bacterial system for the assembly of iron-sulfur clusters with homologs in archaea and plastids.

21 January 2018

1 reference

Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits

21 January 2018

1 reference

Causative role of oxidative stress in a Drosophila model of Friedreich ataxia.

21 January 2018

1 reference

Idebenone delays the onset of cardiac functional alteration without correction of Fe-S enzymes deficit in a mouse model for Friedreich ataxia

21 January 2018

1 reference

Mitochondrial frataxin interacts with ISD11 of the NFS1/ISCU complex and multiple mitochondrial chaperones.

21 January 2018

1 reference

Frataxin interacts functionally with mitochondrial electron transport chain proteins

21 January 2018

1 reference

An interaction between frataxin and Isu1/Nfs1 that is crucial for Fe/S cluster synthesis on Isu1.

21 January 2018

1 reference

Iron-sulfur cluster biosynthesis: characterization of Escherichia coli CYaY as an iron donor for the assembly of [2Fe-2S] clusters in the scaffold IscU.

21 January 2018

1 reference

Structure of the hydrophilic domain of respiratory complex I from Thermus thermophilus

21 January 2018

1 reference

Structural Basis for the Mechanism of Respiratory Complex I

21 January 2018

1 reference

A structural approach to understanding the iron-binding properties of phylogenetically different frataxins.

21 January 2018

1 reference

Frataxin-mediated iron delivery to ferrochelatase in the final step of heme biosynthesis

21 January 2018

1 reference

Candida albicans lacking the frataxin homologue: a relevant yeast model for studying the role of frataxin.

21 January 2018

1 reference

Decreased expression of genes involved in sulfur amino acid metabolism in frataxin-deficient cells.

21 January 2018

1 reference

Salmonella enterica strains lacking the frataxin homolog CyaY show defects in Fe-S cluster metabolism in vivo

21 January 2018

1 reference

Multicellular models of Friedreich ataxia.

21 January 2018

1 reference

Erythroid differentiation and protoporphyrin IX down-regulate frataxin expression in Friend cells: characterization of frataxin expression compared to molecules involved in iron metabolism and hemoglobinization

21 January 2018

1 reference

Deletion of the mitochondrial carrier genes MRS3 and MRS4 suppresses mitochondrial iron accumulation in a yeast frataxin-deficient strain

21 January 2018

1 reference

Frataxin, iron-sulfur clusters, heme, ROS, and aging.

21 January 2018

1 reference

Hemin rescues adrenodoxin, heme a and cytochrome oxidase activity in frataxin-deficient oligodendroglioma cells

21 January 2018

1 reference

Biochemistry of Nitric Oxide and Its Redox-Activated Forms

21 January 2018

1 reference

Nitric oxide and mechanisms of redox signaling

21 January 2018

1 reference

Nitric oxide: the versatility of an extensive signal molecule.

21 January 2018

1 reference

Nitric oxide and iron in plants: an emerging and converging story

21 January 2018

1 reference

Iron and iron-responsive proteins in the cardiomyopathy of Friedreich's ataxia

21 January 2018

1 reference

Expression and one-step purification of recombinant Arabidopsis thaliana frataxin homolog (AtFH).

21 January 2018

1 reference

The phylogenetic distribution of frataxin indicates a role in iron-sulfur cluster protein assembly

21 January 2018

1 reference

Friedreich's ataxia protein: phylogenetic evidence for mitochondrial dysfunction

21 January 2018

1 reference

Solution Structure of the Bacterial Frataxin Ortholog, CyaY

21 January 2018

1 reference