(Q37976595)

26 August 2017

title

Creatine and guanidinoacetate transport at blood-brain and blood-cerebrospinal fluid barriers (English)

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26 August 2017

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ChEBI release 2020-05-28

Olivier Braissant

1

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26 August 2017

publication date

18 January 2012

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Journal of Inherited Metabolic Disease

26 August 2017

published in

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26 August 2017

volume

35

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26 August 2017

issue

4

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26 August 2017

page(s)

655-664

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https://scigraph.springernature.com/pub.10.1007/s10545-011-9433-2

26 August 2017

exact match

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cites work

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AGAT, GAMT and SLC6A8 distribution in the central nervous system, in relation to creatine deficiency syndromes: a review

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21 January 2018

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21 January 2018

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21 January 2018

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In situ hybridization analysis of CHOT1, a creatine transporter, in the rat central nervous system.

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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Intracerebroventricular administration of creatine protects against damage by global cerebral ischemia in rat.

21 January 2018

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The creatine transporter mediates the uptake of creatine by brain tissue, but not the uptake of two creatine-derived compounds.

21 January 2018

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Immunohistochemical localisation of the creatine transporter in the rat brain.

21 January 2018

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Two novel mutations in SLC6A8 cause creatine transporter defect and distinctive X-linked mental retardation in two unrelated Dutch families.

21 January 2018

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Blood-to-retina transport of creatine via creatine transporter (CRT) at the rat inner blood-retinal barrier

21 January 2018

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Evidence for creatine biosynthesis in Müller glia

21 January 2018

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Engaging neuroscience to advance translational research in brain barrier biology.

21 January 2018

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https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

The blood-brain barrier creatine transporter is a major pathway for supplying creatine to the brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Kinetics of creatine in blood and brain after intraperitoneal injection in the rat.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Protective effects of some creatine derivatives in brain tissue anoxia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

In vivo neuroprotection by a creatine-derived compound: phosphocreatine-Mg-complex acetate.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

X-Linked creatine transporter deficiency in two patients with severe mental retardation and autism.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

X-linked creatine-transporter gene (SLC6A8) defect: a new creatine-deficiency syndrome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

The putative rat choline transporter CHOT1 transports creatine and is highly expressed in neural and muscle-rich tissues

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Severely altered guanidino compound levels, disturbed body weight homeostasis and impaired fertility in a mouse model of guanidinoacetate N-methyltransferase (GAMT) deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Creatine deficiency syndrome caused by guanidinoacetate methyltransferase deficiency: diagnostic tools for a new inborn error of metabolism.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Lack of creatine in muscle and brain in an adult with GAMT deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Presymptomatic treatment of neonatal guanidinoacetate methyltransferase deficiency.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

1H MR spectroscopy of the brain in Cr transporter defect

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Nature and consequences of mammalian brain and CSF efflux transporters: four decades of progress

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Creatine replacement therapy in guanidinoacetate methyltransferase deficiency, a novel inborn error of metabolism.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Transport characteristics of guanidino compounds at the blood-brain barrier and blood-cerebrospinal fluid barrier: relevance to neural disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Distinct cellular expressions of creatine synthetic enzyme GAMT and creatine kinases uCK-Mi and CK-B suggest a novel neuron-glial relationship for brain energy homeostasis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Expression and possible role of creatine transporter in the brain and at the blood-cerebrospinal fluid barrier as a transporting protein of guanidinoacetate, an endogenous convulsant

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

The blood-brain barrier transport and cerebral distribution of guanidinoacetate in rats: involvement of creatine and taurine transporters

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Evolutionary evidence of the effect of rare variants on disease etiology

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Spatiotemporal expression of the creatine metabolism related genes agat, gamt and ct1 during zebrafish embryogenesis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Choroid plexus: biology and pathology

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Astrocyte heterogeneity: an underappreciated topic in neurobiology

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Materno-fetal transport of creatine in the rat

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

Creatine deficiency in the brain: a new, treatable inborn error of metabolism

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10545-011-9433-2

The neuroprotective role of creatine.

21 January 2018

1 reference

12 December 2020

Dietary supplement creatine protects against traumatic brain injury

1 reference

12 December 2020

Blood-brain barrier permeability of glucose and ketone bodies during short-term starvation in humans.

1 reference

12 December 2020

The Blood–Brain Barrier Creatine Transporter is a Major Pathway for Supplying Creatine to the Brain

1 reference

12 December 2020

Therapeutic trial of arginine restriction in creatine deficiency syndrome

1 reference

12 December 2020

Creatine and creatinine metabolism

1 reference

12 December 2020

Ammonium-induced impairment of axonal growth is prevented through glial creatine.

1 reference

12 December 2020

Pre-symptomatic treatment of creatine biosynthesis defects

1 reference

12 December 2020

Clinical features and X-inactivation in females heterozygous for creatine transporter defect.

1 reference

12 December 2020

Increase of total creatine in human brain after oral supplementation of creatine-monohydrate

1 reference

12 December 2020

Expression and function of AGAT, GAMT and CT1 in the mammalian brain

1 reference

12 December 2020

Treatment by oral creatine, L-arginine and L-glycine in six severely affected patients with creatine transporter defect.

1 reference

12 December 2020

Searching for a therapy of creatine transporter deficiency: some effects of creatine ethyl ester in brain slices in vitro.

1 reference

12 December 2020

Long-term follow-up and treatment in nine boys with X-linked creatine transporter defect

1 reference

12 December 2020

Cerebral creatine deficiency syndromes: clinical aspects, treatment and pathophysiology.

1 reference

12 December 2020

10.1007/S10545-011-9433-2

Identifiers

DOI

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26 August 2017

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