(Q38354158)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:12773530%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

title

The functional integrity of the serpin domain of C1-inhibitor depends on the unique N-terminal domain, as revealed by a pathological mutant (English)

1 reference

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4 November 2019

4

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4 November 2019

author name string

Ineke G A Bos

1

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4 November 2019

Yvonne T P Lubbers

2

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4 November 2019

Dorina Roem

3

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4 November 2019

C Erik Hack

5

1 reference

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4 November 2019

Eric Eldering

6

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4 November 2019

language of work or name

English

0 references

publication date

27 May 2003

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:12773530%20AND%20SRC:MED&resulttype=core&format=json

Journal of Biological Chemistry

4 November 2019

published in

1 reference

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4 November 2019

volume

278

1 reference

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4 November 2019

issue

32

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4 November 2019

page(s)

29463-29470

1 reference

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A BIOCHEMICAL ABNORMALITY IN HEREDIATRY ANGIONEUROTIC EDEMA: ABSENCE OF SERUM INHIBITOR OF C' 1-ESTERASE.

4 November 2019

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Inactivation of kallikrein in human plasma

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Contribution of Plasma Protease Inhibitors to the Inactivation of Kallikrein in Plasma

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Negatively charged phosphopeptides of nucleolar nonhistone proteins from novikoff hepatoma ascites cells

21 January 2018

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C1 inhibitor and hereditary angioneurotic edema

21 January 2018

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Behavior in vivo of normal and dysfunctional C1 inhibitor in normal subjects and patients with hereditary angioneurotic edema.

21 January 2018

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Crucial residues in the carboxy-terminal end of C1 inhibitor revealed by pathogenic mutants impaired in secretion or function

21 January 2018

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COOH-terminal substitutions in the serpin C1 inhibitor that cause loop overinsertion and subsequent multimerization

21 January 2018

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Structural and functional aspects of C1-inhibitor

21 January 2018

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What do dysfunctional serpins tell us about molecular mobility and disease?

21 January 2018

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Structural basis for serpin inhibitor activity

21 January 2018

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Structure of a serpin-protease complex shows inhibition by deformation

21 January 2018

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Structural change in alpha-chymotrypsin induced by complexation with alpha 1-antichymotrypsin as seen by enhanced sensitivity to proteolysis.

21 January 2018

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Proteolytically cleaved mutant antithrombin-Hamilton has high stability to denaturation characteristic of wild type inhibitor serpins

21 January 2018

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Alpha 1-proteinase inhibitor variant T345R. Influence of P14 residue on substrate and inhibitory pathways

21 January 2018

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Substrate behavior of plasminogen activator inhibitor-1 is not associated with a lack of insertion of the reactive site loop.

21 January 2018

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C1 inhibitor hinge region mutations produce dysfunction by different mechanisms

21 January 2018

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Type II hereditary angioneurotic edema that may result from a single nucleotide change in the codon for alanine-436 in the C1 inhibitor gene

21 January 2018

1 reference

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Structural basis of latency in plasminogen activator inhibitor-1

21 January 2018

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Biological implications of a 3 A structure of dimeric antithrombin

21 January 2018

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Serpinopathies and the conformational dementias

21 January 2018

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Antithrombin-TRI (Ala382 to Thr) causing severe thromboembolic tendency undergoes the S-to-R transition and is associated with a plasma-inactive high-molecular-weight complex of aggregated antithrombin

21 January 2018

1 reference

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alpha 1-Antitrypsin Mmalton (Phe52-deleted) forms loop-sheet polymers in vivo. Evidence for the C sheet mechanism of polymerization.

21 January 2018

1 reference

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Thromboembolic disease due to thermolabile conformational changes of antithrombin Rouen-VI (187 Asn-->Asp)

21 January 2018

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Human C1 inhibitor: primary structure, cDNA cloning, and chromosomal localization

21 January 2018

1 reference

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The use of biotinylated DNA probes in parentage testing: non-isotopic labeling and non-toxic extraction

21 January 2018

1 reference

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Plasma levels of C1- inhibitor complexes and cleaved C1- inhibitor in patients with hereditary angioneurotic edema.

21 January 2018

1 reference

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Complete nucleotide sequence of the gene for human C1 inhibitor with an unusually high density of Alu elements

21 January 2018

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Proteolytic inactivation of plasma C1- inhibitor in sepsis

21 January 2018

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The structural basis for neutrophil inactivation of C1 inhibitor.

21 January 2018

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Limited proteolysis of C1-inhibitor by chymotrypsin-like proteinases

21 January 2018

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C1 inhibitor-C1s complexes are internalized and degraded by the low density lipoprotein receptor-related protein

21 January 2018

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The anticoagulant activation of antithrombin by heparin

21 January 2018

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Detection of C1 inhibitor mutations in patients with hereditary angioedema.

21 January 2018

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Trypsin complexed with alpha 1-proteinase inhibitor has an increased structural flexibility

21 January 2018

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The contribution of the conserved hinge region residues of alpha1-antitrypsin to its reaction with elastase

21 January 2018

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Effect of the Z mutation on the physical and inhibitory properties of alpha 1-antitrypsin

21 January 2018

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Preparation and characterization of latent alpha 1-antitrypsin

21 January 2018

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Conformation of the reactive site loop of alpha 1-proteinase inhibitor probed by limited proteolysis

21 January 2018

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Formation and properties of C1-inhibitor polymers

21 January 2018

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Characterization of C1 inhibitor-Ta. A dysfunctional C1INH with deletion of lysine 251

21 January 2018

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The native metastable fold of C1-inhibitor is stabilized by disulfide bonds

21 January 2018

1 reference

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Recombinant human C1-inhibitor produced in Pichia pastoris has the same inhibitory capacity as plasma C1-inhibitor

21 January 2018

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The potentiation of human C1-inhibitor by dextran sulphate is transient in vivo: studies in a rat model

21 January 2018

1 reference

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Purification and characterization of human C1-esterase inhibitor

21 January 2018

1 reference

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21 January 2018

Identifiers

DOI

10.1074/JBC.M302977200

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:12773530%20AND%20SRC:MED&resulttype=core&format=json

4 November 2019

1 reference