(Q40398397)

20 September 2017

1 reference

title

Gene therapy for the respiratory manifestations of cystic fibrosis (English)

1 reference

20 September 2017

0 references

0 references

Korst RJ

1

1 reference

20 September 2017

McElvaney NG

2

1 reference

20 September 2017

Chu CS

3

1 reference

20 September 2017

Rosenfeld MA

4

1 reference

20 September 2017

Mastrangeli A

5

1 reference

20 September 2017

Hay J

6

1 reference

20 September 2017

Brody SL

7

1 reference

20 September 2017

Eissa NT

8

1 reference

20 September 2017

Danel C

9

1 reference

20 September 2017

Jaffe HA

10

1 reference

20 September 2017

language of work or name

English

0 references

publication date

1 March 1995

1 reference

American Journal of Respiratory and Critical Care Medicine

20 September 2017

1 reference

20 September 2017

151

1 reference

20 September 2017

3 Pt 2

1 reference

20 September 2017

S75-87

1 reference

The lung in cystic fibrosis. A quantitative study including prevalence of pathologic findings among different age groups

20 September 2017

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Cystic fibrosis. 2. Lung injury in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Pseudomonas colonization in cystic fibrosis. A study of 160 patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Neutrophil elastase and cathepsin G stimulate secretion from cultured bovine airway gland serous cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Identification of the cystic fibrosis gene: genetic analysis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Identification of the cystic fibrosis gene: chromosome walking and jumping

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Demonstration That CFTR Is a Chloride Channel by Alteration of Its Anion Selectivity

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Generation of cAMP-Activated Chloride Currents by Expression of CFTR

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR)

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Correction of the cystic fibrosis defect in vitro by retrovirus-mediated gene transfer

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Cl- channels in CF: lack of activation by protein kinase C and cAMP-dependent protein kinase

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Cystic fibrosis: molecular biology and therapeutic implications

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Cystic fibrosis transmembrane conductance regulator: a chloride channel with novel regulation

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Genomic DNA sequence of the cystic fibrosis transmembrane conductance regulator (CFTR) gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

The relation between genotype and phenotype in cystic fibrosis--analysis of the most common mutation (delta F508).

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Severe deficiency of cystic fibrosis transmembrane conductance regulator messenger RNA carrying nonsense mutations R553X and W1316X in respiratory epithelial cells of patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Structural model of ATP-binding proteins associated with cystic fibrosis, multidrug resistance and bacterial transport

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Immunocytochemical localization of the cystic fibrosis gene product CFTR

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Localization of cystic fibrosis transmembrane conductance regulator in chloride secretory epithelia

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Localization of the cystic fibrosis transmembrane conductance regulator in pancreas

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Defective acidification of intracellular organelles in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Regulation of plasma membrane recycling by CFTR.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Chloride Conductance Expressed by ΔF508 and Other Mutant CFTRs In Xenopus Oocytes

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Maturation and function of cystic fibrosis transmembrane conductance regulator variants bearing mutations in putative nucleotide-binding domains 1 and 2

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Expression of the cystic fibrosis transmembrane conductance regulator gene in the respiratory tract of normal individuals and individuals with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Airway mucosal bioelectric potential difference in cystic fibrosis after lung transplantation.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Persistence of abnormal chloride conductance regulation in transformed cystic fibrosis epithelia.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Activation of chloride channels in normal and cystic fibrosis airway epithelial cells by multifunctional calcium/calmodulin-dependent protein kinase

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

A Cystic Fibrosis Bronchial Epithelial Cell Line: Immortalization by Adeno-12-SV40 Infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

In vivo transfer of the human cystic fibrosis transmembrane conductance regulator gene to the airway epithelium

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Expression of the human cystic fibrosis transmembrane conductance regulator gene in the mouse lung after in vivo intratracheal plasmid-mediated gene transfer

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Direct in vivo gene transfer to airway epithelium employing adenovirus-polylysine-DNA complexes.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Aerosol gene delivery in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

In vivo transfection of murine lungs with a functioning prokaryotic gene using a liposome vehicle.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

High-efficiency gene transfer mediated by adenovirus coupled to DNA-polylysine complexes

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Adenovirus-mediated transfer of a recombinant alpha 1-antitrypsin gene to the lung epithelium in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Image reconstruction reveals the complex molecular organization of adenovirus

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Adenoviruses in the immunocompromised host

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

The virus watch program: a continuing surveillance of viral infections in metropolitan New York families. VI. Observations of adenovirus infections: virus excretion patterns, antibody response, efficiency of surveillance, patterns of infections, and

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Immunization by selective infection with type 4 adenovirus grown in human diploid tissue culture. II. specific protective effect against epidemic disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Immunization with live type 4 adenovirus: determination of infectious virus dose and protective effect of enteric infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Experimental respiratory infection with type 4 adenovirus vaccine in volunteers: clinical and immunological responses

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Characteristics of a human cell line transformed by DNA from human adenovirus type 5

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Diversity of airway epithelial cell targets for in vivo recombinant adenovirus-mediated gene transfer

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Cyclic AMP-dependent protein kinase opens chloride channels in normal but not cystic fibrosis airway epithelium

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Regulation of chloride channels by protein kinase C in normal and cystic fibrosis airway epithelia

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM%2F151.3_PT_2.S75

10.1164/AJRCCM/151.3_PT_2.S75

21 January 2018

Identifiers

DOI

1 reference

20 September 2017

1 reference