(Q40466156)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15669681%20AND%20SRC:MED&resulttype=core&format=json

7 January 2020

title

Correlation between enzyme activity and substrate storage in a cell culture model system for Gaucher disease (English)

1 reference

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7 January 2020

1 reference

3

1 reference

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7 January 2020

author name string

U H Schueler

1

1 reference

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7 January 2020

T Kolter

2

1 reference

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7 January 2020

G C Zirzow

4

1 reference

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7 January 2020

K Sandhoff

5

1 reference

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7 January 2020

R O Brady

6

1 reference

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7 January 2020

publication date

1 January 2004

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15669681%20AND%20SRC:MED&resulttype=core&format=json

Journal of Inherited Metabolic Disease

7 January 2020

published in

1 reference

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7 January 2020

volume

27

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7 January 2020

issue

5

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7 January 2020

page(s)

649-658

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Lysosomal degradation on vesicular membrane surfaces. Enhanced glucosylceramide degradation by lysosomal anionic lipids and activators.

7 January 2020

cites work

1 reference

12 December 2020

Altered ganglioside biosynthesis in mouse cell cultures following transformation with chemical carcinogens and x-irradiation

1 reference

12 December 2020

The Gaucher mouse: additional biochemical alterations

1 reference

12 December 2020

Novel oral treatment of Gaucher's disease with N-butyldeoxynojirimycin (OGT 918) to decrease substrate biosynthesis.

1 reference

12 December 2020

Partial enzyme deficiencies: residual activities and the development of neurological disorders

1 reference

12 December 2020

Macrophages exposed in vitro to conduritol B epoxide resemble Gaucher cells

1 reference

12 December 2020

Gaucher-like changes in human blood-derived macrophages induced by beta-glucocerebrosidase inhibition

1 reference

12 December 2020

METABOLISM OF GLUCOCEREBROSIDES. II. EVIDENCE OF AN ENZYMATIC DEFICIENCY IN GAUCHER'S DISEASE.

1 reference

12 December 2020

The Gaucher mouse: differential action of conduritol B epoxide and reversibility of its effects

1 reference

12 December 2020

Analysis of the lipids of normal and Gaucher bone marrow.

1 reference

12 December 2020

Measurement of protein using bicinchoninic acid

1 reference

12 December 2020

Quantitative correlation between the residual activity of beta-hexosaminidase A and arylsulfatase A and the severity of the resulting lysosomal storage disease

1 reference

12 December 2020

Chemical chaperones increase the cellular activity of N370S beta -glucosidase: a therapeutic strategy for Gaucher disease

1 reference

12 December 2020

47 Enzymic diagnosis of sphingolipidoses

1 reference

12 December 2020

Glycolipids of hamster fibroblasts and derived malignant-transformed cell lines

1 reference

12 December 2020

Quantitative analysis of plasma neutral glycosphingolipids by high performance liquid chromatography of their perbenzoyl derivatives

1 reference

12 December 2020

Inhibitors and stimulators of glucocerebroside metabolism

1 reference

12 December 2020

The uptake of iron by reticulocytes. The influence of purification of the ghosts on iron-containing components in the ghost suspension

1 reference

12 December 2020

Biosynthesis and degradation of mammalian glycosphingolipids

1 reference

12 December 2020

Cellular pathology of lysosomal storage disorders.

1 reference

12 December 2020

Modulation of ganglioside biosynthesis in primary cultured neurons

1 reference

12 December 2020

Glucocerebrosidase deficiency and lysosomal storage of glucocerebroside induced in cultured macrophages

1 reference

12 December 2020

Absence of a specific ganglioside galactosyltransferase in mouse cells transformed by murine sarcoma virus

1 reference

12 December 2020

1 reference

12 December 2020

Enzyme replacement and enhancement therapies: lessons from lysosomal disorders

1 reference

12 December 2020

Gangliosides in DNA virus-transformed and spontaneously transformed tumorigenic mouse cell lines

1 reference

12 December 2020

Replacement therapy for inherited enzyme deficiency. Use of purified glucocerebrosidase in Gaucher's disease.

1 reference

12 December 2020

Recent advances in the biochemistry of sphingolipidoses

1 reference

12 December 2020

Gaucher disease: Perspectives on a prototype lysosomal disease

1 reference

12 December 2020

Gaucher cells in chronic myelocytic leukemia: an acquired abnormality

1 reference

12 December 2020

Topology of glycosphingolipid degradation

1 reference

12 December 2020

The fine structure of the cerebroside occurring in Gaucher's disease

1 reference

12 December 2020

beta-Glucosidase inhibition in murine peritoneal macrophages by conduritol-B-epoxide: an in vitro model of the Gaucher cell

1 reference

12 December 2020

Sphingolipids—Their Metabolic Pathways and the Pathobiochemistry of Neurodegenerative Diseases

1 reference

Crossref

https://api.crossref.org/works/10.1023%2FB%3ABOLI.0000042959.44318.7C

7 January 2021