(Q40593834)

21 September 2017

title

The N-terminal metal-binding site 2 of the Wilson's Disease Protein plays a key role in the transfer of copper from Atox1. (English)

1 reference

21 September 2017

Joel M Walker

1

1 reference

21 September 2017

Dominik Huster

2

1 reference

21 September 2017

Martina Ralle

3

1 reference

21 September 2017

Clinton T Morgan

4

1 reference

21 September 2017

Ninian J Blackburn

5

1 reference

21 September 2017

Svetlana Lutsenko

6

1 reference

21 September 2017

language of work or name

English

0 references

publication date

30 January 2004

1 reference

Journal of Biological Chemistry

21 September 2017

published in

1 reference

21 September 2017

volume

279

1 reference

21 September 2017

issue

15

1 reference

21 September 2017

page(s)

15376-15384

1 reference

Intracellular copper routing: the role of copper chaperones

21 September 2017

cites work

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Metallochaperones, an intracellular shuttle service for metal ions

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Human copper-transporting ATPase ATP7B (the Wilson's disease protein): biochemical properties and regulation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Function and regulation of the mammalian copper-transporting ATPases: insights from biochemical and cell biological approaches

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Undetectable intracellular free copper: the requirement of a copper chaperone for superoxide dismutase

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Identification of the copper chaperone SAH in Ovis aries: expression analysis and in vitro interaction of SAH with ATP7B.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Characterization of the interaction between the Wilson and Menkes disease proteins and the cytoplasmic copper chaperone, HAH1p

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Metallochaperone Atox1 transfers copper to the NH2-terminal domain of the Wilson's disease protein and regulates its catalytic activity

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Metal ion chaperone function of the soluble Cu(I) receptor Atx1.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Interaction of the copper chaperone HAH1 with the Wilson disease protein is essential for copper homeostasis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Structure and metal binding studies of the second copper binding domain of the Menkes ATPase

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Solution structure of the fourth metal-binding domain from the Menkes copper-transporting ATPase

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

N-terminal domains of human copper-transporting adenosine triphosphatases (the Wilson's and Menkes disease proteins) bind copper selectively in vivo and in vitro with stoichiometry of one copper per metal-binding repeat.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

HAH1 is a copper-binding protein with distinct amino acid residues mediating copper homeostasis and antioxidant defense

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

X-ray absorption spectroscopy of the copper chaperone HAH1 reveals a linear two-coordinate Cu(I) center capable of adduct formation with exogenous thiols and phosphines

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Structural basis for copper transfer by the metallochaperone for the Menkes/Wilson disease proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

The distinct roles of the N-terminal copper-binding sites in regulation of catalytic activity of the Wilson's disease protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Tricine-sodium dodecyl sulfate-polyacrylamide gel electrophoresis for the separation of proteins in the range from 1 to 100 kDa

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Real-space multiple-scattering calculation and interpretation of x-ray-absorption near-edge structure

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Functional properties of the copper-transporting ATPase ATP7B (the Wilson's disease protein) expressed in insect cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Site-directed chemical labeling of extracellular loops in a membrane protein. The topology of the Na,K-ATPase alpha-subunit

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

An atypical linear Cu(I)-S2 center constitutes the high-affinity metal-sensing site in the CueR metalloregulatory protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

The Lys1010-Lys1325 fragment of the Wilson's disease protein binds nucleotides and interacts with the N-terminal domain of this protein in a copper-dependent manner

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

MOLMOL: a program for display and analysis of macromolecular structures

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Expression, Purification, and Metal Binding Properties of the N-terminal Domain from the Wilson Disease Putative Copper-transporting ATPase (ATP7B)

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

Copper-Induced Conformational Changes in the N-Terminal Domain of the Wilson Disease Copper-Transporting ATPase†

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M400053200

21 January 2018

Identifiers

DOI

10.1074/JBC.M400053200

1 reference

21 September 2017

1 reference