(Q40629149)

22 September 2017

Expression of a human surfactant protein C mutation associated with interstitial lung disease disrupts lung development in transgenic mice (English)

1 reference

22 September 2017

Expression of a Human Surfactant Protein C Mutation Associated with Interstitial Lung Disease Disrupts Lung Development in Transgenic Mice (English)

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

interstitial lung disease

17 March 2024

main subject

1 reference

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

James P. Bridges

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14525980

17 March 2024

Susan E. Wert

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14525980

17 March 2024

Lawrence M. Nogee

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14525980

17 March 2024

Timothy E. Weaver

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14525980

17 March 2024

language of work or name

English

0 references

publication date

2 October 2003

1 reference

full work available at URL

22 September 2017

http://www.jbc.org/content/278/52/52739.full.pdf

file format

Portable Document Format

online access status

open access

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14525980

https://api.elsevier.com/content/article/PII:S0021925820752865?httpAccept=text/xml

17 March 2024

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

https://api.elsevier.com/content/article/PII:S0021925820752865?httpAccept=text/plain

17 March 2024

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

https://syndication.highwire.org/content/doi/10.1074/jbc.M309599200

17 March 2024

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Journal of Biological Chemistry

17 March 2024

published in

1 reference

22 September 2017

278

1 reference

22 September 2017

52

1 reference

22 September 2017

52739-52746

1 reference

Dose-response comparisons of five lung surfactant factor (LSF) preparations in an animal model of adult respiratory distress syndrome (ARDS).

22 September 2017

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Lung function in premature lambs and rabbits treated with a recombinant SP-C surfactant

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Function of surfactant proteins B and C

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

The NMR structure of the pulmonary surfactant-associated polypeptide SP-C in an apolar solvent contains a valyl-rich alpha-helix

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Secretion of surfactant protein C, an integral membrane protein, requires the N-terminal propeptide.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

The pulmonary surfactant protein C (SP-C) precursor is a type II transmembrane protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Biosynthesis of surfactant protein C (SP-C). Sorting of SP-C proprotein involves homomeric association via a signal anchor domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

A mutation in the surfactant protein C gene associated with familial interstitial lung disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Heterozygosity for a surfactant protein C gene mutation associated with usual interstitial pneumonitis and cellular nonspecific interstitial pneumonitis in one kindred

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

High throughput method for creating and screening recombinant adenoviruses.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Thyroid transcription factor-1, hepatocyte nuclear factor-3beta, surfactant protein B, C, and Clara cell secretory protein in developing mouse lung

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Pneumonitis and emphysema in sp-C gene targeted mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Altered stability of pulmonary surfactant in SP-C-deficient mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Structural requirements for intracellular transport of pulmonary surfactant protein B (SP-B).

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

A stress response pathway from the endoplasmic reticulum to the nucleus requires a novel bifunctional protein kinase/endoribonuclease (Ire1p) in mammalian cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Lysosome-related organelles

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Stress signaling from the lumen of the endoplasmic reticulum: coordination of gene transcriptional and translational controls

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Cis-acting sequences from a human surfactant protein gene confer pulmonary-specific gene expression in transgenic mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Transcriptional and translational control in the Mammalian unfolded protein response

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Deletion of exon 4 from human surfactant protein C results in aggresome formation and generation of a dominant negative

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Impairment of the ubiquitin-proteasome system by protein aggregation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M309599200

Lung function in premature rabbits treated with recombinant human surfactant protein-C

21 January 2018

2

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

4

261

L349

Glasser

1991

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Transcriptional elements from the human SP-C gene direct expression in the primordial respiratory epithelium of transgenic mice

17 March 2024

5

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

7

13

L727

Vorbroker

1995

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

8

13

L744

Beers

1995

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

10

277

L1034

Russo

1999

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Mutations in the surfactant protein C gene associated with interstitial lung disease

17 March 2024

16

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

17

278

L933

Glasser

2000

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Ablation of a critical surfactant protein B intramolecular disulfide bond in transgenic mice

17 March 2024

18

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Intracellular pH modulates the activity of chloride channels in isolated lacrimal gland acinar cells

17 March 2024

21

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

24

283

L256

Rice

2002

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

26

277

L1104

Ross

1999

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

30

283

L510

Demayo

2002

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Rescue of SP-B knockout mice with a truncated SP-B proprotein. Function of the C-terminal propeptide

17 March 2024

31

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Bacterial killing is enhanced by expression of lysozyme in the lungs of transgenic mice

17 March 2024

32

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Overexpression of surfactant protein-C mature peptide causes neonatal lethality in transgenic mice

17 March 2024

33

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

Surfactant protein deficiency in familial interstitial lung disease

17 March 2024

36

1 reference

https://api.crossref.org/works/10.1074/JBC.M309599200

17 March 2024

Identifiers

1 reference

release_q44w6c3zabd2bhe37cwhh7prcu

22 September 2017

1 reference

Fatcat

https://api.fatcat.wiki/v0/release/q44w6c3zabd2bhe37cwhh7prcu

mapped directly with Wikidata item

24 November 2022

based on heuristic

1 reference