(Q40768916)

23 September 2017

title

Saposins (sap) A and C activate the degradation of galactosylsphingosine (English)

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23 September 2017

Harzer K

1

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23 September 2017

Hiraiwa M

series ordinal

2

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23 September 2017

Paton BC

series ordinal

3

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23 September 2017

language of work or name

English

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publication date

1 November 2001

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23 September 2017

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23 September 2017

volume

508

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23 September 2017

issue

1

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23 September 2017

page(s)

107-110

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Stimulation of acid ceramidase activity by saposin D.

23 September 2017

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Additional biochemical findings in a patient and fetal sibling with a genetic defect in the sphingolipid activator protein (SAP) precursor, prosaposin. Evidence for a deficiency in SAP-1 and for a normal lysosomal neuraminidase

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Sphingolipid activator protein deficiency in a 16-week-old atypical Gaucher disease patient and his fetal sibling: biochemical signs of combined sphingolipidoses

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Saposins (sap) A and C activate the degradation of galactosylceramide in living cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Saposin A: second cerebrosidase activator protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Globoid cell leukodystrophy: Additional deficiency of psychosine galactosidase

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Hydrolysis of galactosylsphingosine and lactosylsphingosine by beta-galactosidases in human brain and cultured fibroblasts.

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Model SV40-transformed fibroblast lines for metabolic studies of human prosaposin and acid ceramidase deficiencies

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Analysis of the multiple forms of Gaucher spleen sphingolipid activator protein 2.

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Isolation, characterization, and proteolysis of human prosaposin, the precursor of saposins (sphingolipid activator proteins).

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Lactosylceramide galactosidase: Comparison with other sphingolipid hydrolases in developing rat brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Prenatal enzymic diagnosis in 24 pregnancies with risk of Krabbe disease .

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

A protein activator of galactosylceramide beta-galactosidase.

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Twenty five years of the "psychosine hypothesis": a personal perspective of its history and present status

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Infantile and fetal globoid cell leukodystrophy: analysis of galactosylceramide and galactosylsphingosine

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

A mutation in the saposin A domain of the sphingolipid activator protein (prosaposin) gene results in a late-onset, chronic form of globoid cell leukodystrophy in the mouse

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Accumulation of glucosylceramide and glucosylsphingosine (psychosine) in cerebrum and cerebellum in infantile and juvenile Gaucher disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

A novel mutation in the coding region of the prosaposin gene leads to a complete deficiency of prosaposin and saposins, and is associated with a complex sphingolipidosis dominated by lactosylceramide accumulation

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Targeted disruption of the mouse sphingolipid activator protein gene: a complex phenotype, including severe leukodystrophy and wide-spread storage of multiple sphingolipids.

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Sphingolipid activator protein D (sap-D) stimulates the lysosomal degradation of ceramide in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Prosaposin deficiency: further characterization of the sphingolipid activator protein-deficient sibs. Multiple glycolipid elevations (including lactosylceramidosis), partial enzyme deficiencies and ultrastructure of the skin in this generalized sphi

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Late-onset globoid cell leukodystrophy: unusual ultrastructural pathology and subtotal beta-galactocerebrosidase deficiency

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Production and characterization of a monoclonal antibody to human saposin C

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

IMMUNOCHEMICAL STUDIES OF LIPIDS. I. PREPARATION AND IMMUNOLOGICAL PROPERTIES OF SYNTHETIC PSYCHOSINE-PROTEIN ANTIGENS

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

Effect of saposins A and C on the enzymatic hydrolysis of liposomal glucosylceramide

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0014-5793%2801%2903044-7

10.1016/S0014-5793(01)03044-7

7 January 2021

Identifiers

DOI

1 reference

23 September 2017

1 reference