(Q41033062)

25 September 2017

title

Pristanic acid beta-oxidation in peroxisomal disorders: studies in cultured human fibroblasts (English)

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25 September 2017

N M Verhoeven

1

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25 September 2017

D S Schor

2

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25 September 2017

C R Roe

3

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25 September 2017

R J Wanders

4

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25 September 2017

C Jakobs

5

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25 September 2017

publication date

1 April 1998

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Biochimica et Biophysica Acta

25 September 2017

number of pages

6

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based on heuristic

inferred from page(s)

published in

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25 September 2017

volume

1391

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25 September 2017

issue

3

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25 September 2017

page(s)

351-356

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Beta oxidation of fatty acids

25 September 2017

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Further characterization of the peroxisomal 3-hydroxyacyl-CoA dehydrogenases from rat liver. Relationship between the different dehydrogenases and evidence that fatty acids and the C27 bile acids di- and tri-hydroxycoprostanic acids are metabolized

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Physiological role of D-3-hydroxyacyl-CoA dehydratase/D-3-hydroxyacyl-CoA dehydrogenase bifunctional protein

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Peroxisomal multifunctional enzyme of beta-oxidation metabolizing D-3-hydroxyacyl-CoA esters in rat liver: molecular cloning, expression and characterization

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

The presence of a new 3-oxoacyl-CoA thiolase in rat liver peroxisomes

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Sterol carrier protein X (SCPx) is a peroxisomal branched-chain beta-ketothiolase specifically reacting with 3-oxo-pristanoyl-CoA: a new, unique role for SCPx in branched-chain fatty acid metabolism in peroxisomes

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

The cerebrohepatorenal (Zellweger) syndrome. Increased levels and impaired degradation of very-long-chain fatty acids and their use in prenatal diagnosis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Complementation analysis of patients with intact peroxisomes and impaired peroxisomal beta-oxidation

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Novel subtype of peroxisomal acyl-CoA oxidase deficiency and bifunctional enzyme deficiency with detectable enzyme protein: identification by means of complementation analysis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Complementation analysis of fibroblasts from peroxisomal fatty acid oxidation deficient patients shows high frequency of bifunctional enzyme deficiency plus intragenic complementation: unequivocal evidence for differential defects in the same enzyme

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Peroxisomal bifunctional enzyme deficiency

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Bile acid analyses in "pseudo-Zellweger" syndrome; clues to the defect in peroxisomal beta-oxidation

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

A bifunctional protein with deficient enzymic activity: identification of a new peroxisomal disorder using novel methods to measure the peroxisomal beta-oxidation enzyme activities

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Bifunctional enzyme deficiency: identification of a new type of peroxisomal disorder in a patient with an impairment in peroxisomal beta-oxidation of unknown aetiology by means of complementation analysis

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

Pre- and postnatal diagnosis of peroxisomal disorders using stable-isotope dilution gas chromatography--mass spectrometry

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FS0005-2760%2898%2900019-8

10.1016/S0005-2760(98)00019-8

7 January 2021

Identifiers

DOI

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25 September 2017

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