(Q41647589)

6 October 2017

1 reference

title

Molecular defects in genetic diseases of peroxisomes (English)

1 reference

6 October 2017

Y Fujiki

1

1 reference

6 October 2017

1 October 1997

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Biochimica et Biophysica Acta

6 October 2017

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6 October 2017

1361

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6 October 2017

235-250

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6 October 2017

3

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Peroxisomes (microbodies and related particles)

6 October 2017

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Transcription regulation of peroxisomal fatty acyl-CoA oxidase and enoyl-CoA hydratase/3-hydroxyacyl-CoA dehydrogenase in rat liver by peroxisome proliferators

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Activation of a member of the steroid hormone receptor superfamily by peroxisome proliferators

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Control of the peroxisomal β-oxidation pathway by a novel family of nuclear hormone receptors

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Differential expression and activation of a family of murine peroxisome proliferator-activated receptors

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The PPARalpha-leukotriene B4 pathway to inflammation control.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

15-Deoxy-delta 12, 14-prostaglandin J2 is a ligand for the adipocyte determination factor PPAR gamma

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

A prostaglandin J2 metabolite binds peroxisome proliferator-activated receptor gamma and promotes adipocyte differentiation

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisomes of alkane-grown yeast: fundamental and practical aspects

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisomal beta-oxidation system of Candida tropicalis. Purification of a multifunctional protein possessing enoyl-CoA hydratase, 3-hydroxyacyl-CoA dehydrogenase and 3-hydroxyacyl-CoA epimerase activities.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Development of the yeast Pichia pastoris as a model organism for a genetic and molecular analysis of peroxisome assembly

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

An efficient screen for peroxisome-deficient mutants of Pichia pastoris

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisomal disorders. Neurodevelopmental and biochemical aspects

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Protein import into peroxisomes and biogenesis of the organelle

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Disorders of peroxisome biogenesis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Approaches to studies on peroxisome biogenesis and human peroxisome-deficient disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Biogenesis of peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Topogenesis of peroxisomal proteins

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Import of proteins into peroxisomes and other microbodies

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Translocation of acyl-CoA oxidase into peroxisomes requires ATP hydrolysis but not a membrane potential

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Cytosol-dependent peroxisomal protein import in a permeabilized cell system

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Import of firefly luciferase into peroxisomes of permeabilized Chinese hamster ovary cells: a model system to study peroxisomal protein import in vitro

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Proton ionophores prevent assembly of a peroxisomal protein

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Involvement of 70-kD heat-shock proteins in peroxisomal import

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisome targeting signal of rat liver acyl-coenzyme A oxidase resides at the carboxy terminus

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Import of stably folded proteins into peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

An oligomeric protein is imported into peroxisomes in vivo

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Saccharomyces cerevisiae peroxisomal thiolase is imported as a dimer.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

A conserved tripeptide sorts proteins to peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Targeting efficiencies of various permutations of the consensus C-terminal tripeptide peroxisomal targeting signal

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Glycosome assembly in trypanosomes: variations in the acceptable degeneracy of a COOH-terminal microbody targeting signal

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

In vivo import of firefly luciferase into the glycosomes of Trypanosoma brucei and mutational analysis of the C-terminal targeting signal

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Targeting of human catalase to peroxisomes is dependent upon a novel COOH-terminal peroxisomal targeting sequence

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Synthesis of 3-ketoacyl-CoA thiolase of rat liver peroxisomes on free polyribosomes as a larger precursor. Induction of thiolase mRNA activity by clofibrate

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Nucleotide sequence of human peroxisomal 3-oxoacyl-CoA thiolase

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Molecular cloning and deduced amino acid sequence of nonspecific lipid transfer protein (sterol carrier protein 2) of rat liver: a higher molecular mass (60 kDa) protein contains the primary sequence of nonspecific lipid transfer protein as its C-te

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Identification of the cDNA clone which encodes the 58-kDa protein containing the amino acid sequence of rat liver non-specific lipid-transfer protein (sterol-carrier protein 2). Homology with rat peroxisomal and mitochondrial 3-oxoacyl-CoA thiolases

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Cloning and expression of a cDNA encoding human sterol carrier protein 2

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Mutational analysis of the N-terminal topogenic signal of watermelon glyoxysomal malate dehydrogenase using the heterologous host Hansenula polymorpha

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The methylotrophic yeast Hansenula polymorpha contains an inducible import pathway for peroxisomal matrix proteins with an N-terminal targeting signal (PTS2 proteins).

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Amino-terminal presequence of the precursor of peroxisomal 3-ketoacyl-CoA thiolase is a cleavable signal peptide for peroxisomal targeting.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The peroxisomal targeting signal of 3-oxoacyl-CoA thiolase from Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Acyl-CoA oxidase contains two targeting sequences each of which can mediate protein import into peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Two independent peroxisomal targeting signals in catalase A of Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The sorting sequence of the peroxisomal integral membrane protein PMP47 is contained within a short hydrophilic loop

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

A 42K outer-membrane protein is a component of the yeast mitochondrial protein import site

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

MOM19, an import receptor for mitochondrial precursor proteins

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Identification of a receptor for protein import into chloroplasts and its localization to envelope contact zones.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

A unified nomenclature for peroxisome biogenesis factors

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The pas8 mutant of Pichia pastoris exhibits the peroxisomal protein import deficiencies of Zellweger syndrome cells--the PAS8 protein binds to the COOH-terminal tripeptide peroxisomal targeting signal, and is a member of the TPR protein family

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

PAS10 is a tetratricopeptide-repeat protein that is essential for the import of most matrix proteins into peroxisomes of Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The Hansenula polymorpha PER3 gene is essential for the import of PTS1 proteins into the peroxisomal matrix.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The PAH2 gene is required for peroxisome assembly in the methylotrophic yeast Hansenula polymorpha and encodes a member of the tetratricopeptide repeat family of proteins

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Pay32p of the yeast Yarrowia lipolytica is an intraperoxisomal component of the matrix protein translocation machinery

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The TPR snap helix: a novel protein repeat motif from mitosis to transcription

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Mutations in the PTS1 receptor gene, PXR1, define complementation group 2 of the peroxisome biogenesis disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Human peroxisomal targeting signal-1 receptor restores peroxisomal protein import in cells from patients with fatal peroxisomal disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Identification and characterization of the putative human peroxisomal C-terminal targeting signal import receptor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Multiple PEX genes are required for proper subcellular distribution and stability of Pex5p, the PTS1 receptor: evidence that PTS1 protein import is mediated by a cycling receptor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

PAS7 encodes a novel yeast member of the WD-40 protein family essential for import of 3-oxoacyl-CoA thiolase, a PTS2-containing protein, into peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

PEB1 (PAS7) in Saccharomyces cerevisiae encodes a hydrophilic, intra-peroxisomal protein that is a member of the WD repeat family and is essential for the import of thiolase into peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peb1p (Pas7p) is an intraperoxisomal receptor for the NH2-terminal, type 2, peroxisomal targeting sequence of thiolase: Peb1p itself is targeted to peroxisomes by an NH2-terminal peptide.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The import receptor for the peroxisomal targeting signal 2 (PTS2) in Saccharomyces cerevisiae is encoded by the PAS7 gene.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Pex13p is an SH3 protein of the peroxisome membrane and a docking factor for the predominantly cytoplasmic PTs1 receptor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The SH3 domain of the Saccharomyces cerevisiae peroxisomal membrane protein Pex13p functions as a docking site for Pex5p, a mobile receptor for the import PTS1-containing proteins.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Identification of Pex13p a peroxisomal membrane receptor for the PTS1 recognition factor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

How proteins penetrate peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Phenotype of patients with peroxisomal disorders subdivided into sixteen complementation groups

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Complementation study of peroxisome-deficient disorders by immunofluorescence staining and characterization of fused cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Animal cell mutants represent two complementation groups of peroxisome-defective Zellweger syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisomal assembly defects: clinical, pathologic, and biochemical findings in two patients in a newly identified complementation group.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Intracellular protein trafficking defects in human disease

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Isolation of animal cell mutants deficient in plasmalogen biosynthesis and peroxisome assembly

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Isolation and characterization of Chinese hamster ovary cell mutants defective in assembly of peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The targeting and assembly of peroxisomal proteins: some old rules do not apply

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Proteins involved in peroxisome biogenesis and functioning.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

A rapid selection for animal cell mutants with defective peroxisomes.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Isolation of a new peroxisome-deficient CHO cell mutant defective in peroxisome targeting signal-1 receptor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Isolation and characterization of peroxisome-deficient Chinese hamster ovary cell mutants representing human complementation group III.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Polypeptide and phospholipid composition of the membrane of rat liver peroxisomes: comparison with endoplasmic reticulum and mitochondrial membranes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisome assembly mutations in humans: structural heterogeneity in Zellweger syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Presence of cytoplasmic factors functional in peroxisomal protein import implicates organelle-associated defects in several human peroxisomal disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

A human gene responsible for Zellweger syndrome that affects peroxisome assembly

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Restoration by a 35K membrane protein of peroxisome assembly in a peroxisome-deficient mammalian cell mutant

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisome assembly factor 1: nonsense mutation in a peroxisome-deficient Chinese hamster ovary cell mutant and deletion analysis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Does this have a familiar RING?

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The Pichia pastoris PER6 gene product is a peroxisomal integral membrane protein essential for peroxisome biogenesis and has sequence similarity to the Zellweger syndrome protein PAF-1.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

A nonmammalian homolog of the PAF1 gene (Zellweger syndrome) discovered as a gene involved in caryogamy in the fungus Podospora anserina

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Mutations in the PAY5 gene of the yeast Yarrowia lipolytica cause the accumulation of multiple subpopulations of peroxisomes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The Hansenula polymorpha PER8 gene encodes a novel peroxisomal integral membrane protein involved in proliferation

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Formation of the peroxisome lumen is abolished by loss of Pichia pastoris Pas7p, a zinc-binding integral membrane protein of the peroxisome

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisome assembly factor-2, a putative ATPase cloned by functional complementation on a peroxisome-deficient mammalian cell mutant

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Two complementary approaches to study peroxisome biogenesis in Saccharomyces cerevisiae: forward and reversed genetics

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

PAS1, a yeast gene required for peroxisome biogenesis, encodes a member of a novel family of putative ATPases

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Role of the PAS1 gene of Pichia pastoris in peroxisome biogenesis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Sequence of the PAS8 gene, the product of which is essential for biogenesis of peroxisomes in Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Cloning and characterization of PAS5: a gene required for peroxisome biogenesis in the methylotrophic yeast Pichia pastoris

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The peroxisome biogenesis disorder group 4 gene, PXAAA1, encodes a cytoplasmic ATPase required for stability of the PTS1 receptor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Differential protein import deficiencies in human peroxisome assembly disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Correction by gene expression of biochemical abnormalities in fibroblasts from Zellweger patients

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Prenatal diagnosis of Zellweger syndrome using DNA analysis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Assignment of the human peroxisome assembly factor-1 gene (PXMP3) responsible for Zellweger syndrome to chromosome 8q21.1 by fluorescence in situ hybridization

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Mutations in the 70K peroxisomal membrane protein gene in Zellweger syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Putative X-linked adrenoleukodystrophy gene shares unexpected homology with ABC transporters

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The gene responsible for adrenoleukodystrophy encodes a peroxisomal membrane protein

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Structural model of ATP-binding proteins associated with cystic fibrosis, multidrug resistance and bacterial transport

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Retroviral-mediated gene transfer corrects very-long-chain fatty acid metabolism in adrenoleukodystrophy fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Adrenoleukodystrophy: the restoration of peroxisomal beta-oxidation by transfection of normal cDNA

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisomal alanine:glyoxylate aminotransferase deficiency in primary hyperoxaluria type I

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

An enzyme trafficking defect in two patients with primary hyperoxaluria type 1: peroxisomal alanine/glyoxylate aminotransferase rerouted to mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Identification of mutations associated with peroxisome-to-mitochondrion mistargeting of alanine/glyoxylate aminotransferase in primary hyperoxaluria type 1

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Inhibition of alanine:glyoxylate aminotransferase 1 dimerization is a prerequisite for its peroxisome-to-mitochondrion mistargeting in primary hyperoxaluria type 1.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

ATP-dependent degradation of a mutant serine: pyruvate/alanine:glyoxylate aminotransferase in a primary hyperoxaluria type 1 case

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Peroxisomal bifunctional enzyme deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Human peroxisomal 3-oxoacyl-coenzyme A thiolase deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Human dihydroxyacetonephosphate acyltransferase deficiency: a new peroxisomal disorder

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Human alkyldihydroxyacetonephosphate synthase deficiency: a new peroxisomal disorder

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Studies on the metabolic error in Refsum's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Phytol metabolites are circulating dietary factors that activate the nuclear receptor RXR

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Two cases of acatalasia in Switzerland

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Isolation and characterization of the human catalase gene

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Molecular analysis of human acatalasemia. Identification of a splicing mutation

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Characterization of peroxisome-deficient mutants of Hansenula polymorpha

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Common principles of protein translocation across membranes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Pex14p, a peroxisomal membrane protein binding both receptors of the two PTS-dependent import pathways

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

The Hansenula polymorpha PEX14 gene encodes a novel peroxisomal membrane protein essential for peroxisome biogenesis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Human PEX7 encodes the peroxisomal PTS2 receptor and is responsible for rhizomelic chondrodysplasia punctata

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Rhizomelic chondrodysplasia punctata is a peroxisomal protein targeting disease caused by a non-functional PTS2 receptor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Rhizomelic chondrodysplasia punctata is caused by deficiency of human PEX7, a homologue of the yeast PTS2 receptor

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

Isolation of the human PEX12 gene, mutated in group 3 of the peroxisome biogenesis disorders

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2897%2900051-3

7 January 2021

10.1016/S0925-4439(97)00051-3

Identifiers

DOI

1 reference

6 October 2017

1 reference

PubMed ID

9375798