(Q41717827)

7 October 2017

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title

Towards gene therapy of mitochondrial disorders (English)

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7 October 2017

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Collombet JM

1

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PubMed ID

9494968

7 October 2017

Coutelle C

series ordinal

2

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7 October 2017

1 January 1998

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Trends in Molecular Medicine

7 October 2017

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7 October 2017

4

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7 October 2017

1

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7 October 2017

31-38

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An ancestral mitochondrial DNA resembling a eubacterial genome in miniature.

7 October 2017

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

The protein import machinery of the mitochondrial inner membrane

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Sequence and organization of the human mitochondrial genome

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https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Sequence and gene organization of mouse mitochondrial DNA

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https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Transcription and replication of animal mitochondrial DNAs.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Elimination of paternal mitochondrial DNA in intraspecific crosses during early mouse embryogenesis

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

A different genetic code in human mitochondria

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https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Normal oxidative damage to mitochondrial and nuclear DNA is extensive

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Mitotic segregation of mitochondrial DNAs in human cell hybrids and expression of chloramphenicol resistance.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Diseases of the mitochondrial DNA.

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https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Mitochondrial genetics: a paradigm for aging and degenerative diseases?

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Mutation of a nuclear succinate dehydrogenase gene results in mitochondrial respiratory chain deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

An autosomal locus predisposing to deletions of mitochondrial DNA

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Spontaneous Kearns-Sayre/chronic external ophthalmoplegia plus syndrome associated with a mitochondrial DNA deletion: a slip-replication model and metabolic therapy

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Families of mtDNA re-arrangements can be detected in patients with mtDNA deletions: duplications may be a transient intermediate form.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Liver transplantation for ornithine transcarbamylase deficiency in a girl

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Cardiac transplantation in an incomplete Kearns-Sayre syndrome with mitochondrial DNA deletion.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Abnormal ornithine carbamoyltransferase in mice having the sparse-fur mutation

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

A new allele of the sparse fur gene in the mouse

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Evaluation of the transfer and expression in mice of an enzyme-encoding gene using a human adenovirus vector

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Prolonged metabolic correction in adult ornithine transcarbamylase-deficient mice with adenoviral vectors

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Retroviral-mediated gene transfer of human ornithine transcarbamylase into primary hepatocytes of spf and spf-ash mice

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Synthesis of a modified gene encoding human ornithine transcarbamylase for expression in mammalian mitochondrial and universal translation systems: a novel approach towards correction of a genetic defect

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Assembly of functional proton-translocating ATPase complex in yeast mitochondria with cytoplasmically synthesized subunit 8, a polypeptide normally encoded within the organelle

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Mitochondrially-imported cytoplasmic tRNA(Lys)(CUU) of Saccharomyces cerevisiae: in vivo and in vitro targetting systems.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Mouse RNAase MRP RNA is encoded by a nuclear gene and contains a decamer sequence complementary to a conserved region of mitochondrial RNA substrate.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Evidence against a mitochondrial location of the 7-2/MRP RNA in mammalian cells

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Interaction of intravenously injected liposomes with mouse liver mitochondria. A fluorescence and electron microscopy study

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Organelle transformation: shoot first, ask questions later

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

DNA-protein conjugates can enter mitochondria via the protein import pathway.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Transfection of mitochondria: strategy towards a gene therapy of mitochondrial DNA diseases

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Selective inhibition of mutant human mitochondrial DNA replication in vitro by peptide nucleic acids

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Introduction of plasmid DNA into isolated mitochondria by electroporation. A novel approach toward gene correction for mitochondrial disorders

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Modification of the mouse mitochondrial genome by insertion of an exogenous gene

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Human cells lacking mtDNA: repopulation with exogenous mitochondria by complementation

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Mitochondrial transformation of mammalian cells.

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

The mature form of imported mitochondrial proteins undergoes conformational changes upon binding to isolated mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

Gene therapy of mitochondrial diseases using human cytoplasts

1 reference

https://api.crossref.org/works/10.1016%2FS1357-4310%2897%2980543-6

7 January 2021

10.1016/S1357-4310(97)80543-6

Identifiers

DOI

1 reference

7 October 2017

1 reference

PubMed ID

9494968