(Q42585910)

3 November 2017

Inhibition by the branched-chain 2-oxo acids of the 2-oxoglutarate dehydrogenase complex in developing rat and human brain (English)

1 reference

3 November 2017

Patel MS

1

1 reference

PMCID

1168468

3 November 2017

language of work or name

English

0 references

publication date

1 October 1974

1 reference

3 November 2017

1 reference

3 November 2017

144

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3 November 2017

91-97

1 reference

3 November 2017

1

1 reference

Protein measurement with the Folin phenol reagent

3 November 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Studies in maple syrup urine disease

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

A new syndrome: progressive familial infantile cerebral dysfunction associated with an unusual urinary substance.

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Further Observations on the Biochemical Lesion in Maple Syrup Urine Disease

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Maple syrup disease. Effects of dietary therapy on cerebral lipids.

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Serotonin Depletion by Dietary Leucine

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Branched-chain aminotransferase in brain tissue

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

The inhibition of pyruvate decarboxylation in rat brain by α-ketoisocaproic acid

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Ketone bodies as precursors of sterols and fatty acids in the developing rat.

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Effect of the branched-chain alpha-keto acids on pyruvate metabolism by homogenates of human brain

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

The effect of phenylpyruvate on pyruvate metabolism in rat brain

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Development of mitochondrial pyruvate metabolism in rat brain.

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

The metabolism of rat brain mitochondria. Preparation and characterization.

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Kinetic properties of the partially purified pyruvate dehydrogenase complex of ox brain

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

CEREBRAL LIPIDS IN MAPLE SYRUP DISEASE.

28 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Influence of alpha-ketoacids on the respiration of brain in vitro.

16 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Maple syrup urine disease; an inborn error of the metabolism of valine, leucine, and isoleucine associated with gross mental deficiency.

16 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Brain lipids, proteolipids, and free amino acids in maple syrup urine disease

16 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Maple syrup urine disease metabolites studies in cerebellum cultures.

16 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Free amino acids of fetal brain. Influence of the branched chain amino acids.

16 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Development of myelin in inherited disorders of amino acid metabolism.

16 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

Inhibition of brain protein synthesis: an approach to the biochemical basis of neurological dysfunction in the amino-acidurias

16 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1168468

The inhibition of malate, tricarboxylate and oxoglutarate entry into mitochondria by 2-n-butylmalonate

16 August 2018

1 reference

12 December 2020

Mammalian alpha-keto acid dehydrogenase complexes. IV. Substrate specificities and kinetic properties of the pig heart pyruvate and 2-oxyoglutarate dehydrogenase complexes

1 reference

12 December 2020

Maple syrup urine disease

1 reference

12 December 2020

Maple syrup disease; isolation and identification of organic acids in the urine

1 reference

12 December 2020

Maple syrup urine disease

1 reference

12 December 2020

Kinetic studies of rat liver glutamicalanine transaminase

1 reference

12 December 2020

MAPLE SYRUP URINE DISEASE, WITH PARTICULAR REFERENCE TO DIETOTHERAPY

1 reference

12 December 2020

FAMILY SCREENING STUDIES IN MAPLE SYRUP URINE DISEASE (BRANCHED-CHAIN KETOACIDURIA)

1 reference

12 December 2020

Studies on the mutual influences of substrates on bovine -keto acid metabolism

1 reference

12 December 2020

Identifiers

DOI

10.1042/BJ1440091

1 reference

3 November 2017

1 reference

3 November 2017

1 reference

PMCID

1168468