(Q42603418)

3 November 2017

title

Hyperactive behaviour in the mouse model of mucopolysaccharidosis IIIB in the open field and home cage environments (English)

1 reference

3 November 2017

A Langford-Smith

1

1 reference

3 November 2017

M Malinowska

2

1 reference

3 November 2017

K J Langford-Smith

3

1 reference

3 November 2017

G Wegrzyn

4

1 reference

3 November 2017

S Jones

5

1 reference

3 November 2017

R Wynn

6

1 reference

3 November 2017

J E Wraith

7

1 reference

3 November 2017

F L Wilkinson

8

1 reference

3 November 2017

B W Bigger

9

1 reference

3 November 2017

language of work or name

English

0 references

publication date

29 June 2011

1 reference

Genes, Brain and Behavior

3 November 2017

published in

1 reference

3 November 2017

volume

10

1 reference

3 November 2017

issue

6

1 reference

3 November 2017

page(s)

673-682

1 reference

Circadian rhythm and suprachiasmatic nucleus alterations in the mouse model of mucopolysaccharidosis IIIB.

3 November 2017

cites work

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Management of mucopolysaccharidosis type III.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Neurochemistry of the mucopolysaccharidoses: brain glycosaminoglycans, lipids and lysosomal enzymes in mucopolysaccharidosis type III B (alpha-N-acetylglucosaminidase deficiency)

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Improved behavior and neuropathology in the mouse model of Sanfilippo type IIIB disease after adeno-associated virus-mediated gene transfer in the striatum.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Sleep disturbance in mucopolysaccharidosis type III (Sanfilippo syndrome): a survey of managing clinicians

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Sleep disturbance in Sanfilippo syndrome: a parental questionnaire study

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Significantly increased lifespan and improved behavioral performances by rAAV gene delivery in adult mucopolysaccharidosis IIIB mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Restoration of central nervous system alpha-N-acetylglucosaminidase activity and therapeutic benefits in mucopolysaccharidosis IIIB mice by a single intracisternal recombinant adeno-associated viral type 2 vector delivery

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Development of sensory, motor and behavioral deficits in the murine model of Sanfilippo syndrome type B

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Therapeutic efficacy of bone marrow transplant, intracranial AAV-mediated gene therapy, or both in the mouse model of MPS IIIB

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Development of motor deficits in a murine model of mucopolysaccharidosis type IIIA (MPS-IIIA).

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Heparin cofactor II-thrombin complex and dermatan sulphate:chondroitin sulphate ratio are biomarkers of short- and long-term treatment effects in mucopolysaccharide diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Mouse model of Sanfilippo syndrome type B produced by targeted disruption of the gene encoding alpha-N-acetylglucosaminidase

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Genistein reduces lysosomal storage in peripheral tissues of mucopolysaccharide IIIB mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Genistein improves neuropathology and corrects behaviour in a mouse model of neurodegenerative metabolic disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Differential subcellular localization of cholesterol, gangliosides, and glycosaminoglycans in murine models of mucopolysaccharide storage disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Is Sanfilippo type B in your mind when you see adults with mental retardation and behavioral problems?

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Sanfilippo syndrome: profound deficiency of alpha-acetylglucosaminidase activity in organs and skin fibroblasts from type-B patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Activated microglia in cortex of mouse models of mucopolysaccharidoses I and IIIB

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Thigmotaxis as an index of anxiety in mice. Influence of dopaminergic transmissions

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Sanfilippo syndrome: a mini-review

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

Short-term enzyme replacement in the murine model of Sanfilippo syndrome type B.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

The molecular basis of Sanfilippo syndrome type B

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1601-183X.2011.00706.X

10.1111/J.1601-183X.2011.00706.X

21 January 2018

Identifiers

DOI

1 reference

3 November 2017

1 reference