(Q42794848)

English

Metabolism of saturated and polyunsaturated very-long-chain fatty acids in fibroblasts from patients with defects in peroxisomal beta-oxidation

scientific article published on August 1990

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scholarly article

1 reference

Europe PubMed Central

7 November 2017

Metabolism of saturated and polyunsaturated very-long-chain fatty acids in fibroblasts from patients with defects in peroxisomal beta-oxidation (English)

1 reference

Europe PubMed Central

7 November 2017

0 references

author name string

Street JM

1

1 reference

Europe PubMed Central

7 November 2017

Singh H

2

1 reference

Europe PubMed Central

7 November 2017

Poulos A

3

1 reference

Europe PubMed Central

7 November 2017

language of work or name

0 references

publication date

1 August 1990

1 reference

Europe PubMed Central

7 November 2017

number of pages

7

1 reference

based on heuristic

inferred from page(s)

Biochemical Journal

1 reference

Europe PubMed Central

7 November 2017

269

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Europe PubMed Central

7 November 2017

671-677

1 reference

Europe PubMed Central

7 November 2017

3

1 reference

Europe PubMed Central

7 November 2017

A RAPID METHOD OF TOTAL LIPID EXTRACTION AND PURIFICATION

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

A simple method for the isolation and purification of total lipides from animal tissues

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Adrenoleukodystrophy: increased plasma content of saturated very long chain fatty acids

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Adrenoleukodystrophy: survey of 303 cases: biochemistry, diagnosis, and therapy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Peroxisomal alanine:glyoxylate aminotransferase deficiency in primary hyperoxaluria type I

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Peroxisomal lignoceroyl-CoA ligase deficiency in childhood adrenoleukodystrophy and adrenomyeloneuropathy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Peroxisomal disorders in neurology

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Mitochondrial and peroxisomal oxidation of arachidonic and eicosapentaenoic acid studied in isolated liver cells.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

A new peroxisomal disorder with enlarged peroxisomes and a specific deficiency of acyl-CoA oxidase (pseudo-neonatal adrenoleukodystrophy)

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Human peroxisomal 3-oxoacyl-coenzyme A thiolase deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Pseudo-Zellweger syndrome: deficiencies in several peroxisomal oxidative activities.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Lipid metabolism in Zellweger's syndrome

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Metabolism of saturated and polyunsaturated fatty acids by normal and Zellweger syndrome skin fibroblasts

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Beta-oxidation of very-long-chain fatty acids and their coenzyme A derivatives by human skin fibroblasts

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Fatty acid abnormality in adrenoleukodystrophy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

A rapid and sensitive method for the quantitation of microgram quantities of protein utilizing the principle of protein-dye binding

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

27 May 2018

Deficient activities and proteins of peroxisomal beta-oxidation enzymes in infants with Zellweger syndrome.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

16 August 2018

Cerebro-hepato-renal (Zellweger) syndrome, adrenoleukodystrophy, and Refsum's disease: plasma changes and skin fibroblast phytanic acid oxidase

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=1131640

16 August 2018

Flux of palmitate through the peroxisomal and mitochondrial beta-oxidation systems in isolated rat hepatocytes

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Accumulation and defective beta-oxidation of very long chain fatty acids in Zellweger's syndrome, adrenoleukodystrophy and Refsum's disease variants

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

A comparative study of stearic and lignoceric acid oxidation by human skin fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Direct demonstration that the deficient oxidation of very long chain fatty acids in X-linked adrenoleukodystrophy is due to an impaired ability of peroxisomes to activate very long chain fatty acids

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Plasma polyenoic very-long-chain fatty acids in peroxisomal disease: biochemical discrimination of Zellweger's syndrome from other phenotypes

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Adrenoleukodystrophy. The chain shortening of erucic acid (22:1(n-9)) and adrenic acid (22:4(n-6)) is deficient in neonatal adrenoleukodystrophy and normal in X-linked adrenoleukodistrophy skin fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Adrenoleukodystrophy. Report of two cases with relapsing and remitting courses

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Adrenoleukodystrophy: Elevated C26 fatty acid in cultured skin fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Characterization of water-soluble products of palmitic acid beta-oxidation by a rat brain preparation

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Diagnosis of Refsum's disease using [1-14C]phytanic acid as substrate

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Assay for polyunsaturated fatty acids by argentation--thin-layer chromatography using commercial thin-layer plates

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Fatty acid elongation activity in fibroblasts from patients with adrenoleukodystrophy (ALD)

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peroxisomal beta-oxidation enzyme proteins in the Zellweger syndrome

1 reference

https://pubmed.ncbi.nlm.nih.gov/2117919

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1042/BJ2690671

1 reference

Europe PubMed Central

7 November 2017

1 reference

Europe PubMed Central

7 November 2017

1 reference

Europe PubMed Central

7 November 2017

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0 references

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