(Q43450051)

English

Peroxisomal integral membrane proteins in livers of patients with Zellweger syndrome, infantile Refsum's disease and X-linked adrenoleukodystrophy

scientific article published in January 1988

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scholarly article

1 reference

Europe PubMed Central

23 November 2017

Peroxisomal integral membrane proteins in livers of patients with Zellweger syndrome, infantile Refsum's disease and X-linked adrenoleukodystrophy (English)

1 reference

Europe PubMed Central

23 November 2017

membrane proteins

1 reference

based on heuristic

inferred from title

Zellweger syndrome

1 reference

based on heuristic

inferred from title

author name string

G M Small

1

1 reference

Europe PubMed Central

23 November 2017

M J Santos

2

1 reference

Europe PubMed Central

23 November 2017

T Imanaka

3

1 reference

Europe PubMed Central

23 November 2017

A Poulos

4

1 reference

Europe PubMed Central

23 November 2017

D M Danks

5

1 reference

Europe PubMed Central

23 November 2017

H W Moser

6

1 reference

Europe PubMed Central

23 November 2017

P B Lazarow

7

1 reference

Europe PubMed Central

23 November 2017

language of work or name

1 reference

based on heuristic

inferred from title

publication date

1 January 1988

1 reference

Europe PubMed Central

23 November 2017

Journal of Inherited Metabolic Disease

1 reference

Europe PubMed Central

23 November 2017

11

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Europe PubMed Central

23 November 2017

358-371

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Europe PubMed Central

23 November 2017

4

1 reference

Europe PubMed Central

23 November 2017

https://scigraph.springernature.com/pub.10.1007/bf01800425

0 references

How proteins get into microbodies (peroxisomes, glyoxysomes, glycosomes).

1 reference

https://api.crossref.org/works/10.1007%2FBF01800425

21 January 2018

Detection of a homologous series of C26-C38 polyenoic fatty acids in the brain of patients without peroxisomes (Zellweger's syndrome).

1 reference

https://api.crossref.org/works/10.1007%2FBF01800425

21 January 2018

Lignoceroyl-CoASH ligase: enzyme defect in fatty acid beta-oxidation system in X-linked childhood adrenoleukodystrophy

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Improved isolation and purification of rat liver peroxisomes by combined rate zonal and equilibrium density centrifugation

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peroxisomal beta-oxidation enzyme proteins in adrenoleukodystrophy: distinction between X-linked adrenoleukodystrophy and neonatal adrenoleukodystrophy

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Refsum's disease, adrenoleucodystrophy, and the Zellweger syndrome

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Hepatic peroxisomes are deficient in infantile refsum disease: a cytochemical study of 4 cases

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Infantile Refsum's disease: biochemical findings suggesting multiple peroxisomal dysfunction.

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peroxisomal defects in neonatal-onset and X-linked adrenoleukodystrophies

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Immunoblotting of hydrophobic integral membrane proteins

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identification of 3 alpha,7 alpha,12 alpha-trihydroxy-5 beta-cholestan-26-oic acid, an intermediate in cholic acid synthesis, in the plasma of patients with infantile Refsum's disease

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cerebro-hepato-renal syndrome of Zellweger. A report of eight cases with comments upon the incidence, the liver lesion, and a fault in pipecolic acid metabolism

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Translocation of acyl-CoA oxidase into peroxisomes requires ATP hydrolysis but not a membrane potential

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Biogenesis of peroxisomes

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Permeability of the peroxisomal membrane to cofactors of beta-oxidation. Evidence for the presence of a pore-forming protein

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Zellweger syndrome: biochemical and morphological studies on two patients treated with clofibrate

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Isolation of intracellular membranes by means of sodium carbonate treatment: application to endoplasmic reticulum

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Cerebro-hepato-renal (Zellweger) syndrome, adrenoleukodystrophy, and Refsum's disease: plasma changes and skin fibroblast phytanic acid oxidase

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Deficiency of acyl-CoA: dihydroxyacetone phosphate acyltransferase in patients with Zellweger (cerebro-hepato-renal) syndrome.

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The large-scale separation of peroxisomes, mitochondria, and lysosomes from the livers of rats injected with triton WR-1339. Improved isolation procedures, automated analysis, biochemical and morphological properties of fractions

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Adrenoleukodystrophy: survey of 303 cases: biochemistry, diagnosis, and therapy

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Synthesis of a major integral membrane polypeptide of rat liver peroxisomes on free polysomes

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Presence of the peroxisomal 22-kDa integral membrane protein in the liver of a person lacking recognizable peroxisomes (Zellweger syndrome)

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Deficiency of enzymes catalyzing the biosynthesis of glycerol-ether lipids in Zellweger syndrome. A new category of metabolic disease involving the absence of peroxisomes.

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peroxisomal organization in normal and cerebrohepatorenal (Zellweger) syndrome fibroblasts

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Infantile phytanic acid storage disease, a possible variant of Refsum's disease: three cases, including ultrastructural studies of the liver.

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Ultrastructure of the Liver in the Cerebrohepatorenal Syndrome of Zellweger

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Activity of peroxisomal enzymes and intracellular distribution of catalase in Zellweger syndrome.

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Purification of membrane polypeptides of rat liver peroxisomes

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peroxisomal and mitochondrial defects in the cerebro-hepato-renal syndrome.

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Polypeptide and phospholipid composition of the membrane of rat liver peroxisomes: comparison with endoplasmic reticulum and mitochondrial membranes

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peroxisomal beta-oxidation enzyme proteins in the Zellweger syndrome

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The peroxisomal disorders

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Protein measurement with the Folin phenol reagent

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The cerebrohepatorenal syndrome of Zellweger, morphologic and metabolic aspects

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Peroxisomal disorders: a newly recognised group of genetic diseases

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Dysmorphic syndrome with phytanic acid oxidase deficiency, abnormal very long chain fatty acids, and pipecolic acidemia: studies in four children

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Plasma and skin fibroblast C26 fatty acids in infantile Refsum's disease

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Biosynthesis of peroxisomal membrane polypeptides in infants with Zellweger syndrome.

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

“Western Blotting”: Electrophoretic transfer of proteins from sodium dodecyl sulfate-polyacrylamide gels to unmodified nitrocellulose and radiographic detection with antibody and radioiodinated protein A

1 reference

https://pubmed.ncbi.nlm.nih.gov/2468817

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1007/BF01800425

1 reference

Europe PubMed Central

23 November 2017

Dimensions Publication ID

0 references

1 reference

Europe PubMed Central

23 November 2017

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