(Q43638688)

25 November 2017

Partial restoration of defective chloride conductance in DeltaF508 CF mice by trimethylamine oxide (English)

1 reference

25 November 2017

3

1 reference

25 November 2017

Fischer H

1

1 reference

25 November 2017

Fukuda N

2

1 reference

25 November 2017

Illek B

4

1 reference

25 November 2017

Sartori C

5

1 reference

25 November 2017

Matthay MA

6

1 reference

25 November 2017

1 July 2001

1 reference

American Journal of Physiology - Lung Cellular and Molecular Physiology

25 November 2017

1 reference

25 November 2017

281

1 reference

25 November 2017

1

1 reference

25 November 2017

L52-7

1 reference

Development of substituted Benzo[c]quinolizinium compounds as novel activators of the cystic fibrosis chloride channel.

25 November 2017

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Chemical chaperones correct the mutant phenotype of the delta F508 cystic fibrosis transmembrane conductance regulator protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Molecular chaperones and the centrosome. A role for HSP 73 in centrosomal repair following heat shock treatment

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Immediate early gene and HSP70 expression in hyperosmotic stress in MDCK cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Ion-transporting activity in the murine colonic epithelium of normal animals and animals with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Chloride Conductance Expressed by ΔF508 and Other Mutant CFTRs In Xenopus Oocytes

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Mechanism of protein stabilization by glycerol: preferential hydration in glycerol-water mixtures

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Thermodynamic and kinetic examination of protein stabilization by glycerol

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Maturation and function of cystic fibrosis transmembrane conductance regulator variants bearing mutations in putative nucleotide-binding domains 1 and 2

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Intestinal physiology and pathology in gene-targeted mouse models of cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Anomalies in ion transport in CF mouse tracheal epithelium

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Delta F508-CFTR channels: kinetics, activation by forskolin, and potentiation by xanthines

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Alternate stimulation of apical CFTR by genistein in epithelia

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

cAMP and genistein stimulate HCO3- conductance through CFTR in human airway epithelia

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Defective function of the cystic fibrosis-causing missense mutation G551D is recovered by genistein

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Expression of normal and cystic fibrosis phenotypes by continuous airway epithelial cell lines

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Multiple proteolytic systems, including the proteasome, contribute to CFTR processing.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Efficiency of gene transfer for restoration of normal airway epithelial function in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Correction of the apical membrane chloride permeability defect in polarized cystic fibrosis airway epithelia following retroviral-mediated gene transfer

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Mechanism of glibenclamide inhibition of cystic fibrosis transmembrane conductance regulator Cl- channels expressed in a murine cell line

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

An animal model for cystic fibrosis made by gene targeting

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Degradation of CFTR by the ubiquitin-proteasome pathway

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Influence of molecular and chemical chaperones on protein folding

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

A mouse model for the delta F508 allele of cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.2001.281.1.L52

10.1152/AJPLUNG.2001.281.1.L52

21 January 2018

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0 references

1 reference